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2. A case with central and peripheral hypomyelination with hypogonadotropic hypogonadism and hypodontia (4H syndrome) plus cataract. Sato I; Onuma A; Goto N; Sakai F; Fujiwara I; Uematsu M; Osaka H; Okahashi S; Nonaka I; Tanaka S; Haginoya K J Neurol Sci; 2011 Jan; 300(1-2):179-81. PubMed ID: 20884016 [TBL] [Abstract][Full Text] [Related]
3. [Central hypomyelination, hypogonadotrophic hypogonadism and hypodontia: a new leukodystrophy]. Vázquez-López M; Ruiz-Martín Y; de Castro-Castro P; Garzo-Fernández C; Martín-del Valle F; Márquez-de la Plata L Rev Neurol; 2008 Aug 16-31; 47(4):204-8. PubMed ID: 18671210 [TBL] [Abstract][Full Text] [Related]
4. Hypomyelination, Hypodontia, Hypogonadotropic Hypogonadism (4H) Syndrome With Vertebral Anomalies: A Novel Association. Muthusamy K; Sudhakar SV; Yoganathan S; Thomas MM; Alexander M J Child Neurol; 2015 Jun; 30(7):937-41. PubMed ID: 25213661 [TBL] [Abstract][Full Text] [Related]
5. An Indian boy with a novel leukodystrophy: 4H syndrome. Jauhari P; Sahu JK; Singhi P; Dayal D; Khandelwal N J Child Neurol; 2014 Jan; 29(1):135-8. PubMed ID: 23307887 [TBL] [Abstract][Full Text] [Related]
6. New case of 4H syndrome and a review of the literature. Orcesi S; Tonduti D; Uggetti C; Larizza D; Fazzi E; Balottin U Pediatr Neurol; 2010 May; 42(5):359-64. PubMed ID: 20399393 [TBL] [Abstract][Full Text] [Related]
7. Leukoencephalopathy with ataxia, hypodontia, and hypomyelination. Wolf NI; Harting I; Boltshauser E; Wiegand G; Koch MJ; Schmitt-Mechelke T; Martin E; Zschocke J; Uhlenberg B; Hoffmann GF; Weber L; Ebinger F; Rating D Neurology; 2005 Apr; 64(8):1461-4. PubMed ID: 15851747 [TBL] [Abstract][Full Text] [Related]
8. 4H Leukodystrophy: A Brain Magnetic Resonance Imaging Scoring System. Vrij-van den Bos S; Hol JA; La Piana R; Harting I; Vanderver A; Barkhof F; Cayami F; van Wieringen WN; Pouwels PJW; van der Knaap MS; Bernard G; Wolf NI Neuropediatrics; 2017 Jun; 48(3):152-160. PubMed ID: 28561206 [TBL] [Abstract][Full Text] [Related]
9. [Cerebellar ataxia with hypogonadotropic hypogonadism and mental disturbance]. Johkura K; Yamaguchi S; Matsumoto M; Nagatomo H; Hasegawa O; Kuroiwa Y No To Shinkei; 1994 May; 46(5):493-6. PubMed ID: 8060689 [TBL] [Abstract][Full Text] [Related]
10. Peripheral and central hypomyelination with hypogonadotropic hypogonadism and hypodontia. Timmons M; Tsokos M; Asab MA; Seminara SB; Zirzow GC; Kaneski CR; Heiss JD; van der Knaap MS; Vanier MT; Schiffmann R; Wong K Neurology; 2006 Dec; 67(11):2066-9. PubMed ID: 17159124 [TBL] [Abstract][Full Text] [Related]
11. Longitudinal follow up of a boy affected by Pol III-related leukodystrophy: a detailed phenotype description. Battini R; Bertelloni S; Astrea G; Casarano M; Travaglini L; Baroncelli G; Pasquariello R; Bertini E; Cioni G BMC Med Genet; 2015 Jul; 16():53. PubMed ID: 26204956 [TBL] [Abstract][Full Text] [Related]
12. A novel homozygous mutation in POLR3A gene causing 4H syndrome: a case report. Tewari VV; Mehta R; Sreedhar CM; Tewari K; Mohammad A; Gupta N; Gulati S; Kabra M BMC Pediatr; 2018 Apr; 18(1):126. PubMed ID: 29618326 [TBL] [Abstract][Full Text] [Related]
13. Childhood ataxia with cerebral hypomyelination (CACH) syndrome: a study of three siblings. Vaidya SR; Desai SB; Khadilkar SV; Mehta NA Neurol India; 2004 Sep; 52(3):372-4. PubMed ID: 15472431 [TBL] [Abstract][Full Text] [Related]
14. Diffuse central hypomyelination presenting as 4H syndrome caused by compound heterozygous mutations in POLR3A encoding the catalytic subunit of polymerase III. Terao Y; Saitsu H; Segawa M; Kondo Y; Sakamoto K; Matsumoto N; Tsuji S; Nomura Y J Neurol Sci; 2012 Sep; 320(1-2):102-5. PubMed ID: 22819058 [TBL] [Abstract][Full Text] [Related]
15. More than hypomyelination in Pol-III disorder. Vanderver A; Tonduti D; Bernard G; Lai J; Rossi C; Carosso G; Quezado M; Wong K; Schiffmann R J Neuropathol Exp Neurol; 2013 Jan; 72(1):67-75. PubMed ID: 23242285 [TBL] [Abstract][Full Text] [Related]
16. Prothrombin G20210A mutation, hypogonadotropic hypogonadism, and generalized vitiligo-related ischemic stroke in a young adult. Varoglu AO; Kocatürk I; Tatar A Int J Neurosci; 2010 Jun; 120(6):451-3. PubMed ID: 20504218 [TBL] [Abstract][Full Text] [Related]
17. 4H syndrome with late-onset growth hormone deficiency caused by POLR3A mutations. Potic A; Brais B; Choquet K; Schiffmann R; Bernard G Arch Neurol; 2012 Jul; 69(7):920-3. PubMed ID: 22451160 [TBL] [Abstract][Full Text] [Related]
18. Ataxia With Hypodontia: A Unique Leukodystrophy. Currie AD; Karmarkar SA Pediatr Neurol; 2018 Mar; 80():94-95. PubMed ID: 29429779 [No Abstract] [Full Text] [Related]
19. [Significance of neuroimaging in the diagnosis of Boucher-Neuhauser syndrome]. Santos AV; Saraiva PF; Breia PN Acta Med Port; 2003; 16(3):193-5. PubMed ID: 12868401 [TBL] [Abstract][Full Text] [Related]
20. [Kallmann syndrome--a form of hypogonadotropic hypogonadism]. Hefner J; Csef H; Seufert J Dtsch Med Wochenschr; 2009 May; 134(22):1157-60. PubMed ID: 19603380 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]