199 related articles for article (PubMed ID: 20498480)
1. Tissue and cellular expression patterns of porcine CFTR: similarities to and differences from human CFTR.
Plog S; Mundhenk L; Bothe MK; Klymiuk N; Gruber AD
J Histochem Cytochem; 2010 Sep; 58(9):785-97. PubMed ID: 20498480
[TBL] [Abstract][Full Text] [Related]
2. Intestinal CFTR expression alleviates meconium ileus in cystic fibrosis pigs.
Stoltz DA; Rokhlina T; Ernst SE; Pezzulo AA; Ostedgaard LS; Karp PH; Samuel MS; Reznikov LR; Rector MV; Gansemer ND; Bouzek DC; Abou Alaiwa MH; Hoegger MJ; Ludwig PS; Taft PJ; Wallen TJ; Wohlford-Lenane C; McMenimen JD; Chen JH; Bogan KL; Adam RJ; Hornick EE; Nelson GA; Hoffman EA; Chang EH; Zabner J; McCray PB; Prather RS; Meyerholz DK; Welsh MJ
J Clin Invest; 2013 Jun; 123(6):2685-93. PubMed ID: 23676501
[TBL] [Abstract][Full Text] [Related]
3. Cystic fibrosis F508del patients have apically localized CFTR in a reduced number of airway cells.
Penque D; Mendes F; Beck S; Farinha C; Pacheco P; Nogueira P; Lavinha J; Malhó R; Amaral MD
Lab Invest; 2000 Jun; 80(6):857-68. PubMed ID: 10879737
[TBL] [Abstract][Full Text] [Related]
4. Cystic fibrosis transmembrane conductance regulator-dependent regulation of epithelial inducible nitric oxide synthase expression.
Steagall WK; Elmer HL; Brady KG; Kelley TJ
Am J Respir Cell Mol Biol; 2000 Jan; 22(1):45-50. PubMed ID: 10615064
[TBL] [Abstract][Full Text] [Related]
5. Comparative processing and function of human and ferret cystic fibrosis transmembrane conductance regulator.
Fisher JT; Liu X; Yan Z; Luo M; Zhang Y; Zhou W; Lee BJ; Song Y; Guo C; Wang Y; Lukacs GL; Engelhardt JF
J Biol Chem; 2012 Jun; 287(26):21673-85. PubMed ID: 22570484
[TBL] [Abstract][Full Text] [Related]
6. Lack of correlation between CFTR expression, CFTR Cl- currents, amiloride-sensitive Na+ conductance, and cystic fibrosis phenotype.
Beck S; Kühr J; Schütz VV; Seydewitz HH; Brandis M; Greger R; Kunzelmann K
Pediatr Pulmonol; 1999 Apr; 27(4):251-9. PubMed ID: 10230924
[TBL] [Abstract][Full Text] [Related]
7. Human-specific cystic fibrosis transmembrane conductance regulator antibodies detect in vivo gene transfer to ovine airways.
Davidson H; McLachlan G; Wilson A; Boyd AC; Doherty A; MacGregor G; Davies L; Painter HA; Coles R; Hyde SC; Gill DR; Amaral MD; Collie DD; Porteous DJ; Penque D
Am J Respir Cell Mol Biol; 2006 Jul; 35(1):72-83. PubMed ID: 16498081
[TBL] [Abstract][Full Text] [Related]
8. Naturally Occurring Deletion Mutants of the Pig-Specific, Intestinal Crypt Epithelial Cell Protein CLCA4b without Apparent Phenotype.
Plog S; Klymiuk N; Binder S; Van Hook MJ; Thoreson WB; Gruber AD; Mundhenk L
PLoS One; 2015; 10(10):e0140050. PubMed ID: 26474299
[TBL] [Abstract][Full Text] [Related]
9. Aminoglycoside suppression of a premature stop mutation in a Cftr-/- mouse carrying a human CFTR-G542X transgene.
Du M; Jones JR; Lanier J; Keeling KM; Lindsey JR; Tousson A; Bebök Z; Whitsett JA; Dey CR; Colledge WH; Evans MJ; Sorscher EJ; Bedwell DM
J Mol Med (Berl); 2002 Sep; 80(9):595-604. PubMed ID: 12226741
[TBL] [Abstract][Full Text] [Related]
10.
Zhou ZP; Yang LL; Cao H; Chen ZR; Zhang Y; Wen XY; Hu J
Hum Gene Ther; 2019 Sep; 30(9):1101-1116. PubMed ID: 31099266
[TBL] [Abstract][Full Text] [Related]
11. Cystic fibrosis transmembrane conductance regulator-mRNA delivery: a novel alternative for cystic fibrosis gene therapy.
Bangel-Ruland N; Tomczak K; Fernández Fernández E; Leier G; Leciejewski B; Rudolph C; Rosenecker J; Weber WM
J Gene Med; 2013; 15(11-12):414-26. PubMed ID: 24123772
[TBL] [Abstract][Full Text] [Related]
12. Porcine nasal epithelial cultures for studies of cystic fibrosis sinusitis.
Dean N; Ranganath NK; Jones B; Zhang S; Skinner D; Rowe SM; Sorscher EJ; Woodworth BA
Int Forum Allergy Rhinol; 2014 Jul; 4(7):565-70. PubMed ID: 24733748
[TBL] [Abstract][Full Text] [Related]
13. Molecular and functional characterization of the cystic fibrosis transmembrane conductance regulator from the Australian common brushtail possum, Trichosurus vulpecula.
Demmers KJ; Carter D; Fan S; Mao P; Maqbool NJ; McLeod BJ; Bartolo R; Butt AG
J Comp Physiol B; 2010 Apr; 180(4):545-61. PubMed ID: 20012660
[TBL] [Abstract][Full Text] [Related]
14. Sequential targeting of CFTR by BAC vectors generates a novel pig model of cystic fibrosis.
Klymiuk N; Mundhenk L; Kraehe K; Wuensch A; Plog S; Emrich D; Langenmayer MC; Stehr M; Holzinger A; Kröner C; Richter A; Kessler B; Kurome M; Eddicks M; Nagashima H; Heinritzi K; Gruber AD; Wolf E
J Mol Med (Berl); 2012 May; 90(5):597-608. PubMed ID: 22170306
[TBL] [Abstract][Full Text] [Related]
15. Murine mCLCA6 is an integral apical membrane protein of non-goblet cell enterocytes and co-localizes with the cystic fibrosis transmembrane conductance regulator.
Bothe MK; Braun J; Mundhenk L; Gruber AD
J Histochem Cytochem; 2008 May; 56(5):495-509. PubMed ID: 18285349
[TBL] [Abstract][Full Text] [Related]
16. Activation of cAMP-dependent C1- currents in guinea-pig paneth cells without relevant evidence for CFTR expression.
Tsumura T; Hazama A; Miyoshi T; Ueda S; Okada Y
J Physiol; 1998 Nov; 512 ( Pt 3)(Pt 3):765-77. PubMed ID: 9769420
[TBL] [Abstract][Full Text] [Related]
17. Presence of CFTR in the conjunctival epithelium.
Turner HC; Bernstein A; Candia OA
Curr Eye Res; 2002 Mar; 24(3):182-7. PubMed ID: 12221525
[TBL] [Abstract][Full Text] [Related]
18. Spliceosome-mediated RNA trans-splicing with recombinant adeno-associated virus partially restores cystic fibrosis transmembrane conductance regulator function to polarized human cystic fibrosis airway epithelial cells.
Liu X; Luo M; Zhang LN; Yan Z; Zak R; Ding W; Mansfield SG; Mitchell LG; Engelhardt JF
Hum Gene Ther; 2005 Sep; 16(9):1116-23. PubMed ID: 16149910
[TBL] [Abstract][Full Text] [Related]
19. Optimization of hCFTR lung expression in mice using DNA nanoparticles.
Padegimas L; Kowalczyk TH; Adams S; Gedeon CR; Oette SM; Dines K; Hyatt SL; Sesenoglu-Laird O; Tyr O; Moen RC; Cooper MJ
Mol Ther; 2012 Jan; 20(1):63-72. PubMed ID: 21952168
[TBL] [Abstract][Full Text] [Related]
20. Induction of CFTR gene expression by 1,25(OH)
DiFranco KM; Mulligan JK; Sumal AS; Diamond G
J Steroid Biochem Mol Biol; 2017 Oct; 173():323-332. PubMed ID: 28130182
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]
