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2. Downregulation of glial genes involved in synaptic function mitigates Huntington's disease pathogenesis. Onur TS; Laitman A; Zhao H; Keyho R; Kim H; Wang J; Mair M; Wang H; Li L; Perez A; de Haro M; Wan YW; Allen G; Lu B; Al-Ramahi I; Liu Z; Botas J Elife; 2021 Apr; 10():. PubMed ID: 33871358 [TBL] [Abstract][Full Text] [Related]
4. Inactivation of Drosophila Apaf-1 related killer suppresses formation of polyglutamine aggregates and blocks polyglutamine pathogenesis. Sang TK; Li C; Liu W; Rodriguez A; Abrams JM; Zipursky SL; Jackson GR Hum Mol Genet; 2005 Feb; 14(3):357-72. PubMed ID: 15590702 [TBL] [Abstract][Full Text] [Related]
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9. CA150 expression delays striatal cell death in overexpression and knock-in conditions for mutant huntingtin neurotoxicity. Arango M; Holbert S; Zala D; Brouillet E; Pearson J; Régulier E; Thakur AK; Aebischer P; Wetzel R; Déglon N; Néri C J Neurosci; 2006 Apr; 26(17):4649-59. PubMed ID: 16641246 [TBL] [Abstract][Full Text] [Related]
12. Interaction of the nuclear matrix protein NAKAP with HypA and huntingtin: implications for nuclear toxicity in Huntington's disease pathogenesis. Sayer JA; Manczak M; Akileswaran L; Reddy PH; Coghlan VM Neuromolecular Med; 2005; 7(4):297-310. PubMed ID: 16391387 [TBL] [Abstract][Full Text] [Related]
13. Copper enhances aggregational toxicity of mutant huntingtin in a Drosophila model of Huntington's Disease. Lobato AG; Ortiz-Vega N; Zhu Y; Neupane D; Meier KK; Zhai RG Biochim Biophys Acta Mol Basis Dis; 2024 Jan; 1870(1):166928. PubMed ID: 38660915 [TBL] [Abstract][Full Text] [Related]
14. Full length mutant huntingtin is required for altered Ca2+ signaling and apoptosis of striatal neurons in the YAC mouse model of Huntington's disease. Zhang H; Li Q; Graham RK; Slow E; Hayden MR; Bezprozvanny I Neurobiol Dis; 2008 Jul; 31(1):80-8. PubMed ID: 18502655 [TBL] [Abstract][Full Text] [Related]
15. Mutant huntingtin and glycogen synthase kinase 3-beta accumulate in neuronal lipid rafts of a presymptomatic knock-in mouse model of Huntington's disease. Valencia A; Reeves PB; Sapp E; Li X; Alexander J; Kegel KB; Chase K; Aronin N; DiFiglia M J Neurosci Res; 2010 Jan; 88(1):179-90. PubMed ID: 19642201 [TBL] [Abstract][Full Text] [Related]
16. Huntington's disease: from huntingtin function and dysfunction to therapeutic strategies. Borrell-Pagès M; Zala D; Humbert S; Saudou F Cell Mol Life Sci; 2006 Nov; 63(22):2642-60. PubMed ID: 17041811 [TBL] [Abstract][Full Text] [Related]
17. Huntington disease arises from a combinatory toxicity of polyglutamine and copper binding. Xiao G; Fan Q; Wang X; Zhou B Proc Natl Acad Sci U S A; 2013 Sep; 110(37):14995-5000. PubMed ID: 23980182 [TBL] [Abstract][Full Text] [Related]
18. Sp1 and TAFII130 transcriptional activity disrupted in early Huntington's disease. Dunah AW; Jeong H; Griffin A; Kim YM; Standaert DG; Hersch SM; Mouradian MM; Young AB; Tanese N; Krainc D Science; 2002 Jun; 296(5576):2238-43. PubMed ID: 11988536 [TBL] [Abstract][Full Text] [Related]