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5. Tibial muscular dystrophy is a titinopathy caused by mutations in TTN, the gene encoding the giant skeletal-muscle protein titin. Hackman P; Vihola A; Haravuori H; Marchand S; Sarparanta J; De Seze J; Labeit S; Witt C; Peltonen L; Richard I; Udd B Am J Hum Genet; 2002 Sep; 71(3):492-500. PubMed ID: 12145747 [TBL] [Abstract][Full Text] [Related]
6. Removal of the calpain 3 protease reverses the myopathology in a mouse model for titinopathies. Charton K; Danièle N; Vihola A; Roudaut C; Gicquel E; Monjaret F; Tarrade A; Sarparanta J; Udd B; Richard I Hum Mol Genet; 2010 Dec; 19(23):4608-24. PubMed ID: 20855473 [TBL] [Abstract][Full Text] [Related]
7. Limb-girdle muscular dystrophy type 2A resulting from homozygous G2338C transversion mutation in the calpain-3 gene. Peddareddygari LR; Surgan V; Grewal RP J Clin Neuromuscul Dis; 2010 Dec; 12(2):62-5. PubMed ID: 21386772 [TBL] [Abstract][Full Text] [Related]
8. Translocation of molecular chaperones to the titin springs is common in skeletal myopathy patients and affects sarcomere function. Unger A; Beckendorf L; Böhme P; Kley R; von Frieling-Salewsky M; Lochmüller H; Schröder R; Fürst DO; Vorgerd M; Linke WA Acta Neuropathol Commun; 2017 Sep; 5(1):72. PubMed ID: 28915917 [TBL] [Abstract][Full Text] [Related]
9. Identification of a Novel Mutation in the Titin Gene in a Chinese Family with Limb-Girdle Muscular Dystrophy 2J. Zheng W; Chen H; Deng X; Yuan L; Yang Y; Song Z; Yang Z; Wu Y; Deng H Mol Neurobiol; 2016 Oct; 53(8):5097-102. PubMed ID: 26392295 [TBL] [Abstract][Full Text] [Related]
11. Secondary calpain3 deficiency in 2q-linked muscular dystrophy: titin is the candidate gene. Haravuori H; Vihola A; Straub V; Auranen M; Richard I; Marchand S; Voit T; Labeit S; Somer H; Peltonen L; Beckmann JS; Udd B Neurology; 2001 Apr; 56(7):869-77. PubMed ID: 11294923 [TBL] [Abstract][Full Text] [Related]
12. Novel Homozygous Missense Mutation in CAPN3 Gene Detected in a Saudi Arabian Family With Limb-Girdle Muscular Dystrophy Type 2A. Al-Harbi TM; Abdulmanaʼ SO; Dridi W J Clin Neuromuscul Dis; 2016 Dec; 18(2):89-91. PubMed ID: 27861222 [TBL] [Abstract][Full Text] [Related]
13. Limb girdle muscular dystrophy in a sibling pair with a homozygous Ser606Leu mutation in the alternatively spliced IS2 region of calpain 3. Jenne DE; Kley RA; Vorgerd M; Schröder JM; Weis J; Reimann H; Albrecht B; Nürnberg P; Thiele H; Müller CR; Meng G; Witt CC; Labeit S Biol Chem; 2005 Jan; 386(1):61-7. PubMed ID: 15843148 [TBL] [Abstract][Full Text] [Related]
14. Mdm muscular dystrophy: interactions with calpain 3 and a novel functional role for titin's N2A domain. Huebsch KA; Kudryashova E; Wooley CM; Sher RB; Seburn KL; Spencer MJ; Cox GA Hum Mol Genet; 2005 Oct; 14(19):2801-11. PubMed ID: 16115818 [TBL] [Abstract][Full Text] [Related]
15. Atypical phenotypes in titinopathies explained by second titin mutations. Evilä A; Vihola A; Sarparanta J; Raheem O; Palmio J; Sandell S; Eymard B; Illa I; Rojas-Garcia R; Hankiewicz K; Negrão L; Löppönen T; Nokelainen P; Kärppä M; Penttilä S; Screen M; Suominen T; Richard I; Hackman P; Udd B Ann Neurol; 2014 Feb; 75(2):230-40. PubMed ID: 24395473 [TBL] [Abstract][Full Text] [Related]
16. A novel mutation in the myotilin gene (MYOT) causes a severe form of limb girdle muscular dystrophy 1A (LGMD1A). Reilich P; Krause S; Schramm N; Klutzny U; Bulst S; Zehetmayer B; Schneiderat P; Walter MC; Schoser B; Lochmüller H J Neurol; 2011 Aug; 258(8):1437-44. PubMed ID: 21336781 [TBL] [Abstract][Full Text] [Related]
17. Limb-girdle muscular dystrophies: heterogeneity of clinical phenotypes and pathogenetic mechanisms. Angelini C Acta Myol; 2004 Dec; 23(3):130-6. PubMed ID: 15938568 [TBL] [Abstract][Full Text] [Related]
18. Homozygous missense variant in the TTN gene causing autosomal recessive limb-girdle muscular dystrophy type 10. Khan A; Wang R; Han S; Umair M; Abbas S; Khan MI; Alshabeeb MA; Alfadhel M; Zhang X BMC Med Genet; 2019 Oct; 20(1):166. PubMed ID: 31664938 [TBL] [Abstract][Full Text] [Related]
19. Interactions with M-band titin and calpain 3 link myospryn (CMYA5) to tibial and limb-girdle muscular dystrophies. Sarparanta J; Blandin G; Charton K; Vihola A; Marchand S; Milic A; Hackman P; Ehler E; Richard I; Udd B J Biol Chem; 2010 Sep; 285(39):30304-15. PubMed ID: 20634290 [TBL] [Abstract][Full Text] [Related]
20. Myotilinopathy in a family with late onset myopathy. Pénisson-Besnier I; Talvinen K; Dumez C; Vihola A; Dubas F; Fardeau M; Hackman P; Carpen O; Udd B Neuromuscul Disord; 2006 Jul; 16(7):427-31. PubMed ID: 16793270 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]