These tools will no longer be maintained as of December 31, 2024. Archived website can be found here. PubMed4Hh GitHub repository can be found here. Contact NLM Customer Service if you have questions.


BIOMARKERS

Molecular Biopsy of Human Tumors

- a resource for Precision Medicine *

160 related articles for article (PubMed ID: 20637096)

  • 1. Mucopolysaccharidosis IIIB, a lysosomal storage disease, triggers a pathogenic CNS autoimmune response.
    Killedar S; Dirosario J; Divers E; Popovich PG; McCarty DM; Fu H
    J Neuroinflammation; 2010 Jul; 7():39. PubMed ID: 20637096
    [TBL] [Abstract][Full Text] [Related]  

  • 2. Innate and adaptive immune activation in the brain of MPS IIIB mouse model.
    DiRosario J; Divers E; Wang C; Etter J; Charrier A; Jukkola P; Auer H; Best V; Newsom DL; McCarty DM; Fu H
    J Neurosci Res; 2009 Mar; 87(4):978-90. PubMed ID: 18951493
    [TBL] [Abstract][Full Text] [Related]  

  • 3. Accelerated clinical disease and pathology in mucopolysaccharidosis type IIIB and GalNAc transferase double knockout mice.
    Mohammed EE; Snella EM; Rutz-Mendicino MM; Echevarria FD; Awedikian R; Whitley EM; Ellinwood NM
    Mol Genet Metab; 2012 Sep; 107(1-2):129-35. PubMed ID: 22867887
    [TBL] [Abstract][Full Text] [Related]  

  • 4. Amyloidosis, synucleinopathy, and prion encephalopathy in a neuropathic lysosomal storage disease: the CNS-biomarker potential of peripheral blood.
    Naughton BJ; Duncan FJ; Murrey D; Ware T; Meadows A; McCarty DM; Fu H
    PLoS One; 2013; 8(11):e80142. PubMed ID: 24278249
    [TBL] [Abstract][Full Text] [Related]  

  • 5. Development of sensory, motor and behavioral deficits in the murine model of Sanfilippo syndrome type B.
    Heldermon CD; Hennig AK; Ohlemiller KK; Ogilvie JM; Herzog ED; Breidenbach A; Vogler C; Wozniak DF; Sands MS
    PLoS One; 2007 Aug; 2(8):e772. PubMed ID: 17712420
    [TBL] [Abstract][Full Text] [Related]  

  • 6. Restoration of central nervous system alpha-N-acetylglucosaminidase activity and therapeutic benefits in mucopolysaccharidosis IIIB mice by a single intracisternal recombinant adeno-associated viral type 2 vector delivery.
    Fu H; DiRosario J; Kang L; Muenzer J; McCarty DM
    J Gene Med; 2010 Jul; 12(7):624-33. PubMed ID: 20603889
    [TBL] [Abstract][Full Text] [Related]  

  • 7. Peripheral nervous system neuropathology and progressive sensory impairments in a mouse model of Mucopolysaccharidosis IIIB.
    Fu H; Bartz JD; Stephens RL; McCarty DM
    PLoS One; 2012; 7(9):e45992. PubMed ID: 23049915
    [TBL] [Abstract][Full Text] [Related]  

  • 8. Differential distribution of heparan sulfate glycoforms and elevated expression of heparan sulfate biosynthetic enzyme genes in the brain of mucopolysaccharidosis IIIB mice.
    McCarty DM; DiRosario J; Gulaid K; Killedar S; Oosterhof A; van Kuppevelt TH; Martin PT; Fu H
    Metab Brain Dis; 2011 Mar; 26(1):9-19. PubMed ID: 21225451
    [TBL] [Abstract][Full Text] [Related]  

  • 9. Electrophysiological and Histological Characterization of Rod-Cone Retinal Degeneration and Microglia Activation in a Mouse Model of Mucopolysaccharidosis Type IIIB.
    Tse DY; Lotfi P; Simons DL; Sardiello M; Wu SM
    Sci Rep; 2015 Nov; 5():17143. PubMed ID: 26607664
    [TBL] [Abstract][Full Text] [Related]  

  • 10. Neuropathology in mouse models of mucopolysaccharidosis type I, IIIA and IIIB.
    Wilkinson FL; Holley RJ; Langford-Smith KJ; Badrinath S; Liao A; Langford-Smith A; Cooper JD; Jones SA; Wraith JE; Wynn RF; Merry CL; Bigger BW
    PLoS One; 2012; 7(4):e35787. PubMed ID: 22558223
    [TBL] [Abstract][Full Text] [Related]  

  • 11. Neurological correction of lysosomal storage in a mucopolysaccharidosis IIIB mouse model by adeno-associated virus-mediated gene delivery.
    Fu H; Samulski RJ; McCown TJ; Picornell YJ; Fletcher D; Muenzer J
    Mol Ther; 2002 Jan; 5(1):42-9. PubMed ID: 11786044
    [TBL] [Abstract][Full Text] [Related]  

  • 12. Characterization of early markers of disease in the mouse model of mucopolysaccharidosis IIIB.
    McCullough KB; Titus A; Reardon K; Conyers S; Dougherty JD; Ge X; Garbow JR; Dickson P; Yuede CM; Maloney SE
    J Neurodev Disord; 2024 Apr; 16(1):16. PubMed ID: 38632525
    [TBL] [Abstract][Full Text] [Related]  

  • 13. Macrophage enzyme and reduced inflammation drive brain correction of mucopolysaccharidosis IIIB by stem cell gene therapy.
    Holley RJ; Ellison SM; Fil D; O'Leary C; McDermott J; Senthivel N; Langford-Smith AWW; Wilkinson FL; D'Souza Z; Parker H; Liao A; Rowlston S; Gleitz HFE; Kan SH; Dickson PI; Bigger BW
    Brain; 2018 Jan; 141(1):99-116. PubMed ID: 29186350
    [TBL] [Abstract][Full Text] [Related]  

  • 14. A model of mucopolysaccharidosis IIIB (Sanfilippo syndrome type IIIB): N-acetyl-alpha-D-glucosaminidase deficiency in Schipperke dogs.
    Ellinwood NM; Wang P; Skeen T; Sharp NJ; Cesta M; Decker S; Edwards NJ; Bublot I; Thompson JN; Bush W; Hardam E; Haskins ME; Giger U
    J Inherit Metab Dis; 2003; 26(5):489-504. PubMed ID: 14518829
    [TBL] [Abstract][Full Text] [Related]  

  • 15. Trehalose reduces retinal degeneration, neuroinflammation and storage burden caused by a lysosomal hydrolase deficiency.
    Lotfi P; Tse DY; Di Ronza A; Seymour ML; Martano G; Cooper JD; Pereira FA; Passafaro M; Wu SM; Sardiello M
    Autophagy; 2018; 14(8):1419-1434. PubMed ID: 29916295
    [TBL] [Abstract][Full Text] [Related]  

  • 16. Mucopolysaccharidosis IIIB confers enhanced neonatal intracranial transduction by AAV8 but not by 5, 9 or rh10.
    Gilkes JA; Bloom MD; Heldermon CD
    Gene Ther; 2016 Mar; 23(3):263-71. PubMed ID: 26674264
    [TBL] [Abstract][Full Text] [Related]  

  • 17. Mannitol-facilitated CNS entry of rAAV2 vector significantly delayed the neurological disease progression in MPS IIIB mice.
    McCarty DM; DiRosario J; Gulaid K; Muenzer J; Fu H
    Gene Ther; 2009 Nov; 16(11):1340-52. PubMed ID: 19587708
    [TBL] [Abstract][Full Text] [Related]  

  • 18. Significantly increased lifespan and improved behavioral performances by rAAV gene delivery in adult mucopolysaccharidosis IIIB mice.
    Fu H; Kang L; Jennings JS; Moy SS; Perez A; Dirosario J; McCarty DM; Muenzer J
    Gene Ther; 2007 Jul; 14(14):1065-77. PubMed ID: 17460717
    [TBL] [Abstract][Full Text] [Related]  

  • 19. Proteomic Analysis of Mucopolysaccharidosis IIIB Mouse Brain.
    De Pasquale V; Costanzo M; Siciliano RA; Mazzeo MF; Pistorio V; Bianchi L; Marchese E; Ruoppolo M; Pavone LM; Caterino M
    Biomolecules; 2020 Feb; 10(3):. PubMed ID: 32111039
    [TBL] [Abstract][Full Text] [Related]  

  • 20. Genistein reduces lysosomal storage in peripheral tissues of mucopolysaccharide IIIB mice.
    Malinowska M; Wilkinson FL; Bennett W; Langford-Smith KJ; O'Leary HA; Jakobkiewicz-Banecka J; Wynn R; Wraith JE; Wegrzyn G; Bigger BW
    Mol Genet Metab; 2009 Nov; 98(3):235-42. PubMed ID: 19632871
    [TBL] [Abstract][Full Text] [Related]  

    [Next]    [New Search]
    of 8.