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12. The iminosugar isofagomine increases the activity of N370S mutant acid beta-glucosidase in Gaucher fibroblasts by several mechanisms. Steet RA; Chung S; Wustman B; Powe A; Do H; Kornfeld SA Proc Natl Acad Sci U S A; 2006 Sep; 103(37):13813-8. PubMed ID: 16945909 [TBL] [Abstract][Full Text] [Related]
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