279 related articles for article (PubMed ID: 21030523)
1. Proteostasis strategies for restoring alpha1-antitrypsin deficiency.
Bouchecareilh M; Conkright JJ; Balch WE
Proc Am Thorac Soc; 2010 Nov; 7(6):415-22. PubMed ID: 21030523
[TBL] [Abstract][Full Text] [Related]
2. Alpha 1-Antitrypsin Deficiency: A Disorder of Proteostasis-Mediated Protein Folding and Trafficking Pathways.
Karatas E; Bouchecareilh M
Int J Mol Sci; 2020 Feb; 21(4):. PubMed ID: 32098273
[TBL] [Abstract][Full Text] [Related]
3. Histone deacetylase inhibitor (HDACi) suberoylanilide hydroxamic acid (SAHA)-mediated correction of α1-antitrypsin deficiency.
Bouchecareilh M; Hutt DM; Szajner P; Flotte TR; Balch WE
J Biol Chem; 2012 Nov; 287(45):38265-78. PubMed ID: 22995909
[TBL] [Abstract][Full Text] [Related]
4. The proteostasis boundary in misfolding diseases of membrane traffic.
Hutt DM; Powers ET; Balch WE
FEBS Lett; 2009 Aug; 583(16):2639-46. PubMed ID: 19708088
[TBL] [Abstract][Full Text] [Related]
5. Multiple Genes Core to ERAD, Macroautophagy and Lysosomal Degradation Pathways Participate in the Proteostasis Response in α1-Antitrypsin Deficiency.
Li J; Moretti F; Hidvegi T; Sviben S; Fitzpatrick JAJ; Sundaramoorthi H; Pak SC; Silverman GA; Knapp B; Filipuzzi I; Alford J; Reece-Hoyes J; Nigsch F; Murphy LO; Nyfeler B; Perlmutter DH
Cell Mol Gastroenterol Hepatol; 2024; 17(6):1007-1024. PubMed ID: 38336172
[TBL] [Abstract][Full Text] [Related]
6. Proteostasis: a new therapeutic paradigm for pulmonary disease.
Bouchecareilh M; Balch WE
Proc Am Thorac Soc; 2011 May; 8(2):189-95. PubMed ID: 21543800
[TBL] [Abstract][Full Text] [Related]
7. Endoplasmic reticulum proteostasis impairment in aging.
Martínez G; Duran-Aniotz C; Cabral-Miranda F; Vivar JP; Hetz C
Aging Cell; 2017 Aug; 16(4):615-623. PubMed ID: 28436203
[TBL] [Abstract][Full Text] [Related]
8. Proteostasis: bad news and good news from the endoplasmic reticulum.
Noack J; Brambilla Pisoni G; Molinari M
Swiss Med Wkly; 2014; 144():w14001. PubMed ID: 25144910
[TBL] [Abstract][Full Text] [Related]
9. Chemical and biological approaches for adapting proteostasis to ameliorate protein misfolding and aggregation diseases: progress and prognosis.
Lindquist SL; Kelly JW
Cold Spring Harb Perspect Biol; 2011 Dec; 3(12):. PubMed ID: 21900404
[TBL] [Abstract][Full Text] [Related]
10. A C. elegans model of human α1-antitrypsin deficiency links components of the RNAi pathway to misfolded protein turnover.
Long OS; Benson JA; Kwak JH; Luke CJ; Gosai SJ; O'Reilly LP; Wang Y; Li J; Vetica AC; Miedel MT; Stolz DB; Watkins SC; Züchner S; Perlmutter DH; Silverman GA; Pak SC
Hum Mol Genet; 2014 Oct; 23(19):5109-22. PubMed ID: 24838286
[TBL] [Abstract][Full Text] [Related]
11. Accumulation of mutant alpha1-antitrypsin Z in the endoplasmic reticulum activates caspases-4 and -12, NFkappaB, and BAP31 but not the unfolded protein response.
Hidvegi T; Schmidt BZ; Hale P; Perlmutter DH
J Biol Chem; 2005 Nov; 280(47):39002-15. PubMed ID: 16183649
[TBL] [Abstract][Full Text] [Related]
12. Protecting the future: balancing proteostasis for reproduction.
Sala AJ; Morimoto RI
Trends Cell Biol; 2022 Mar; 32(3):202-215. PubMed ID: 34654604
[TBL] [Abstract][Full Text] [Related]
13. The Autophagy Pathway: A Critical Route in the Disposal of Alpha 1-Antitrypsin Aggregates That Holds Many Mysteries.
Leon C; Bouchecareilh M
Int J Mol Sci; 2021 Feb; 22(4):. PubMed ID: 33668611
[TBL] [Abstract][Full Text] [Related]
14. Endoplasmic reticulum polymers impair luminal protein mobility and sensitize to cellular stress in alpha1-antitrypsin deficiency.
Ordóñez A; Snapp EL; Tan L; Miranda E; Marciniak SJ; Lomas DA
Hepatology; 2013 May; 57(5):2049-60. PubMed ID: 23197448
[TBL] [Abstract][Full Text] [Related]
15. Quality control of mislocalized and orphan proteins.
Kong KE; Coelho JPL; Feige MJ; Khmelinskii A
Exp Cell Res; 2021 Jun; 403(2):112617. PubMed ID: 33930402
[TBL] [Abstract][Full Text] [Related]
16. Underlying mechanisms and chemical/biochemical therapeutic approaches to ameliorate protein misfolding neurodegenerative diseases.
Hekmatimoghaddam S; Zare-Khormizi MR; Pourrajab F
Biofactors; 2017 Nov; 43(6):737-759. PubMed ID: 26899445
[TBL] [Abstract][Full Text] [Related]
17. Modeling general proteostasis: proteome balance in health and disease.
Roth DM; Balch WE
Curr Opin Cell Biol; 2011 Apr; 23(2):126-34. PubMed ID: 21131189
[TBL] [Abstract][Full Text] [Related]
18. Stress-responsive regulation of extracellular proteostasis.
Mesgarzadeh JS; Buxbaum JN; Wiseman RL
J Cell Biol; 2022 Apr; 221(4):. PubMed ID: 35191945
[TBL] [Abstract][Full Text] [Related]
19. Proteostasis impairment in protein-misfolding and -aggregation diseases.
Hipp MS; Park SH; Hartl FU
Trends Cell Biol; 2014 Sep; 24(9):506-14. PubMed ID: 24946960
[TBL] [Abstract][Full Text] [Related]
20. Glycoprotein folding and quality-control mechanisms in protein-folding diseases.
Ferris SP; Kodali VK; Kaufman RJ
Dis Model Mech; 2014 Mar; 7(3):331-41. PubMed ID: 24609034
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]
