234 related articles for article (PubMed ID: 21156023)
1. Fatty acid omega-oxidation as a rescue pathway for fatty acid oxidation disorders in humans.
Wanders RJ; Komen J; Kemp S
FEBS J; 2011 Jan; 278(2):182-94. PubMed ID: 21156023
[TBL] [Abstract][Full Text] [Related]
2. Phytanic acid and very long chain fatty acids in genetic peroxisomal disorders.
Molzer B; Kainz-Korschinsky M; Sundt-Heller R; Bernheimer H
J Clin Chem Clin Biochem; 1989 May; 27(5):309-14. PubMed ID: 2474624
[TBL] [Abstract][Full Text] [Related]
3. [X-linked adrenoleukodystrophy and other peroxisomal diseases caused by a failing peroxisomal beta-oxidation system: clinical expression, diagnosis and treatment].
Wanders RJ; Barth PG; Schutgens RB; Van den Bosch H; Tager JM; Stroink H; Przyrembel H; Heymans HS
Tijdschr Kindergeneeskd; 1989 Oct; 57(5):186-97. PubMed ID: 2683204
[TBL] [Abstract][Full Text] [Related]
4. In vivo stable isotope studies in three patients affected with mitochondrial fatty acid oxidation disorders: limited diagnostic use of 1-13C fatty acid breath test using bolus technique.
Jakobs C; Kneer J; Martin D; Boulloche J; Brivet M; Poll-The BT; Saudubray JM
Eur J Pediatr; 1997 Aug; 156 Suppl 1():S78-82. PubMed ID: 9266222
[TBL] [Abstract][Full Text] [Related]
5. Intestinal pseudo-obstruction as a manifestation of impaired mitochondrial fatty acid oxidation.
Gilbert J; Ibdah JA
Med Hypotheses; 2005; 64(3):586-9. PubMed ID: 15617873
[TBL] [Abstract][Full Text] [Related]
6. New genetic defects in mitochondrial fatty acid oxidation and carnitine deficiency.
Stanley CA
Adv Pediatr; 1987; 34():59-88. PubMed ID: 3318304
[TBL] [Abstract][Full Text] [Related]
7. Peroxisomal fatty acid beta-oxidation in relation to the accumulation of very long chain fatty acids in cultured skin fibroblasts from patients with Zellweger syndrome and other peroxisomal disorders.
Wanders RJ; van Roermund CW; van Wijland MJ; Schutgens RB; Heikoop J; van den Bosch H; Schram AW; Tager JM
J Clin Invest; 1987 Dec; 80(6):1778-83. PubMed ID: 3680527
[TBL] [Abstract][Full Text] [Related]
8. Fatty acid oxidation disorders: maternal health and neonatal outcomes.
Rector RS; Ibdah JA
Semin Fetal Neonatal Med; 2010 Jun; 15(3):122-8. PubMed ID: 19926542
[TBL] [Abstract][Full Text] [Related]
9. Mutation analysis in mitochondrial fatty acid oxidation defects: Exemplified by acyl-CoA dehydrogenase deficiencies, with special focus on genotype-phenotype relationship.
Gregersen N; Andresen BS; Corydon MJ; Corydon TJ; Olsen RK; Bolund L; Bross P
Hum Mutat; 2001 Sep; 18(3):169-89. PubMed ID: 11524729
[TBL] [Abstract][Full Text] [Related]
10. Mitochondrial fatty-acid oxidation disorders.
Kompare M; Rizzo WB
Semin Pediatr Neurol; 2008 Sep; 15(3):140-9. PubMed ID: 18708005
[TBL] [Abstract][Full Text] [Related]
11. Regulation of mitochondrial fatty acid β-oxidation in human: what can we learn from inborn fatty acid β-oxidation deficiencies?
Bastin J
Biochimie; 2014 Jan; 96():113-20. PubMed ID: 23764392
[TBL] [Abstract][Full Text] [Related]
12. Modeling disorders of fatty acid metabolism in the mouse.
Goetzman ES
Prog Mol Biol Transl Sci; 2011; 100():389-417. PubMed ID: 21377632
[TBL] [Abstract][Full Text] [Related]
13. Fatty acid oxidation disorders.
Rinaldo P; Matern D; Bennett MJ
Annu Rev Physiol; 2002; 64():477-502. PubMed ID: 11826276
[TBL] [Abstract][Full Text] [Related]
14. Characterization of phytanic acid omega-hydroxylation in human liver microsomes.
Komen JC; Duran M; Wanders RJ
Mol Genet Metab; 2005 Jul; 85(3):190-5. PubMed ID: 15979030
[TBL] [Abstract][Full Text] [Related]
15. [The contribution of peroxisomes to lipid metabolism].
Kramar R
J Clin Chem Clin Biochem; 1986 Feb; 24(2):109-18. PubMed ID: 3711795
[TBL] [Abstract][Full Text] [Related]
16. Inherited disorders of fatty alcohol metabolism.
Rizzo WB
Mol Genet Metab; 1998 Oct; 65(2):63-73. PubMed ID: 9787098
[TBL] [Abstract][Full Text] [Related]
17. Inhibition of fatty acid synthase-dependent neoplastic lipogenesis as the mechanism of gamma-linolenic acid-induced toxicity to tumor cells: an extension to Nwankwo's hypothesis.
Menendez JA; Colomer R; Lupu R
Med Hypotheses; 2005; 64(2):337-41. PubMed ID: 15607568
[TBL] [Abstract][Full Text] [Related]
18. [From gene to disease; X-linked adrenoleukodystrophy].
Engelen M; Kemp S; van Geel BM
Ned Tijdschr Geneeskd; 2008 Apr; 152(14):804-8. PubMed ID: 18491823
[TBL] [Abstract][Full Text] [Related]
19. Cytochrome P450 metabolizing fatty acids in living organisms.
Pinot F
FEBS J; 2011 Jan; 278(2):181. PubMed ID: 21205193
[No Abstract] [Full Text] [Related]
20. Heat stress deteriorates mitochondrial beta-oxidation of long-chain fatty acids in cultured fibroblasts with fatty acid beta-oxidation disorders.
Li H; Fukuda S; Hasegawa Y; Purevsuren J; Kobayashi H; Mushimoto Y; Yamaguchi S
J Chromatogr B Analyt Technol Biomed Life Sci; 2010 Jun; 878(20):1669-72. PubMed ID: 20207594
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]