365 related articles for article (PubMed ID: 21169527)
1. Gene therapy rescues cone structure and function in the 3-month-old rd12 mouse: a model for midcourse RPE65 leber congenital amaurosis.
Li X; Li W; Dai X; Kong F; Zheng Q; Zhou X; Lü F; Chang B; Rohrer B; Hauswirth WW; Qu J; Pang JJ
Invest Ophthalmol Vis Sci; 2011 Jan; 52(1):7-15. PubMed ID: 21169527
[TBL] [Abstract][Full Text] [Related]
2. Intraperitoneal chromophore injections delay early-onset and rapid retinal cone degeneration in a mouse model of Leber congenital amaurosis.
Dai X; Jin X; Ye Q; Huang H; Duo L; Lu C; Bao J; Chen H
Exp Eye Res; 2021 Nov; 212():108776. PubMed ID: 34582935
[TBL] [Abstract][Full Text] [Related]
3. Gene therapy following subretinal AAV5 vector delivery is not affected by a previous intravitreal AAV5 vector administration in the partner eye.
Li W; Kong F; Li X; Dai X; Liu X; Zheng Q; Wu R; Zhou X; Lü F; Chang B; Li Q; Hauswirth WW; Qu J; Pang JJ
Mol Vis; 2009; 15():267-75. PubMed ID: 19190735
[TBL] [Abstract][Full Text] [Related]
4. Lentiviral gene transfer of RPE65 rescues survival and function of cones in a mouse model of Leber congenital amaurosis.
Bemelmans AP; Kostic C; Crippa SV; Hauswirth WW; Lem J; Munier FL; Seeliger MW; Wenzel A; Arsenijevic Y
PLoS Med; 2006 Oct; 3(10):e347. PubMed ID: 17032058
[TBL] [Abstract][Full Text] [Related]
5. Differential proteomics and functional research following gene therapy in a mouse model of Leber congenital amaurosis.
Zheng Q; Ren Y; Tzekov R; Zhang Y; Chen B; Hou J; Zhao C; Zhu J; Zhang Y; Dai X; Ma S; Li J; Pang J; Qu J; Li W
PLoS One; 2012; 7(8):e44855. PubMed ID: 22953002
[TBL] [Abstract][Full Text] [Related]
6. Light prevents exogenous 11-cis retinal from maintaining cone photoreceptors in chromophore-deficient mice.
Fan J; Crouch RK; Kono M
Invest Ophthalmol Vis Sci; 2011 Apr; 52(5):2412-6. PubMed ID: 21228385
[TBL] [Abstract][Full Text] [Related]
7. Self-complementary AAV-mediated gene therapy restores cone function and prevents cone degeneration in two models of Rpe65 deficiency.
Pang J; Boye SE; Lei B; Boye SL; Everhart D; Ryals R; Umino Y; Rohrer B; Alexander J; Li J; Dai X; Li Q; Chang B; Barlow R; Hauswirth WW
Gene Ther; 2010 Jul; 17(7):815-26. PubMed ID: 20237510
[TBL] [Abstract][Full Text] [Related]
8. Retinal degeneration 12 (rd12): a new, spontaneously arising mouse model for human Leber congenital amaurosis (LCA).
Pang JJ; Chang B; Hawes NL; Hurd RE; Davisson MT; Li J; Noorwez SM; Malhotra R; McDowell JH; Kaushal S; Hauswirth WW; Nusinowitz S; Thompson DA; Heckenlively JR
Mol Vis; 2005 Feb; 11():152-62. PubMed ID: 15765048
[TBL] [Abstract][Full Text] [Related]
9. Pharmacological Amelioration of Cone Survival and Vision in a Mouse Model for Leber Congenital Amaurosis.
Li S; Samardzija M; Yang Z; Grimm C; Jin M
J Neurosci; 2016 May; 36(21):5808-19. PubMed ID: 27225770
[TBL] [Abstract][Full Text] [Related]
10. Inverse correlation between fatty acid transport protein 4 and vision in Leber congenital amaurosis associated with RPE65 mutation.
Li S; Gordon WC; Bazan NG; Jin M
Proc Natl Acad Sci U S A; 2020 Dec; 117(50):32114-32123. PubMed ID: 33257550
[TBL] [Abstract][Full Text] [Related]
11. Long-term restoration of rod and cone vision by single dose rAAV-mediated gene transfer to the retina in a canine model of childhood blindness.
Acland GM; Aguirre GD; Bennett J; Aleman TS; Cideciyan AV; Bennicelli J; Dejneka NS; Pearce-Kelling SE; Maguire AM; Palczewski K; Hauswirth WW; Jacobson SG
Mol Ther; 2005 Dec; 12(6):1072-82. PubMed ID: 16226919
[TBL] [Abstract][Full Text] [Related]
12. Cone outer segment morphology and cone function in the Rpe65-/- Nrl-/- mouse retina are amenable to retinoid replacement.
Kunchithapautham K; Coughlin B; Crouch RK; Rohrer B
Invest Ophthalmol Vis Sci; 2009 Oct; 50(10):4858-64. PubMed ID: 19407011
[TBL] [Abstract][Full Text] [Related]
13. Gene therapy restores vision-dependent behavior as well as retinal structure and function in a mouse model of RPE65 Leber congenital amaurosis.
Pang JJ; Chang B; Kumar A; Nusinowitz S; Noorwez SM; Li J; Rani A; Foster TC; Chiodo VA; Doyle T; Li H; Malhotra R; Teusner JT; McDowell JH; Min SH; Li Q; Kaushal S; Hauswirth WW
Mol Ther; 2006 Mar; 13(3):565-72. PubMed ID: 16223604
[TBL] [Abstract][Full Text] [Related]
14. RPE65 is present in human green/red cones and promotes photopigment regeneration in an in vitro cone cell model.
Tang PH; Buhusi MC; Ma JX; Crouch RK
J Neurosci; 2011 Dec; 31(50):18618-26. PubMed ID: 22171060
[TBL] [Abstract][Full Text] [Related]
15. Protection of cone photoreceptor M-opsin degradation with 9-cis-β-carotene-rich alga Dunaliella bardawil in Rpe65(-/-) mouse retinal explant culture.
Ozaki T; Nakazawa M; Kudo T; Hirano S; Suzuki K; Ishiguro S
Curr Eye Res; 2014 Dec; 39(12):1221-31. PubMed ID: 25006880
[TBL] [Abstract][Full Text] [Related]
16. Pathophysilogical mechanism and treatment strategies for Leber congenital amaurosis.
Fu Y; Zhang T
Adv Exp Med Biol; 2014; 801():791-6. PubMed ID: 24664772
[TBL] [Abstract][Full Text] [Related]
17. Overexpression of Type 3 Iodothyronine Deiodinase Reduces Cone Death in the Leber Congenital Amaurosis Model Mice.
Yang F; Ma H; Boye SL; Hauswirth WW; Ding XQ
Adv Exp Med Biol; 2018; 1074():125-131. PubMed ID: 29721936
[TBL] [Abstract][Full Text] [Related]
18. Rpe65-/- and Lrat-/- mice: comparable models of leber congenital amaurosis.
Fan J; Rohrer B; Frederick JM; Baehr W; Crouch RK
Invest Ophthalmol Vis Sci; 2008 Jun; 49(6):2384-9. PubMed ID: 18296659
[TBL] [Abstract][Full Text] [Related]
19. Bax-induced apoptosis in Leber's congenital amaurosis: a dual role in rod and cone degeneration.
Hamann S; Schorderet DF; Cottet S
PLoS One; 2009 Aug; 4(8):e6616. PubMed ID: 19672311
[TBL] [Abstract][Full Text] [Related]
20. Deletion of M-Opsin Prevents M Cone Degeneration in a Mouse Model of Leber Congenital Amaurosis.
Xu H; Enemchukwu N; Zhong X; Zhang O; Fu Y
Am J Pathol; 2020 May; 190(5):1059-1067. PubMed ID: 32084365
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]
