309 related articles for article (PubMed ID: 21543800)
1. Proteostasis: a new therapeutic paradigm for pulmonary disease.
Bouchecareilh M; Balch WE
Proc Am Thorac Soc; 2011 May; 8(2):189-95. PubMed ID: 21543800
[TBL] [Abstract][Full Text] [Related]
2. Alpha 1-Antitrypsin Deficiency: A Disorder of Proteostasis-Mediated Protein Folding and Trafficking Pathways.
Karatas E; Bouchecareilh M
Int J Mol Sci; 2020 Feb; 21(4):. PubMed ID: 32098273
[TBL] [Abstract][Full Text] [Related]
3. Histone deacetylase inhibitor (HDACi) suberoylanilide hydroxamic acid (SAHA)-mediated correction of α1-antitrypsin deficiency.
Bouchecareilh M; Hutt DM; Szajner P; Flotte TR; Balch WE
J Biol Chem; 2012 Nov; 287(45):38265-78. PubMed ID: 22995909
[TBL] [Abstract][Full Text] [Related]
4. Proteostasis strategies for restoring alpha1-antitrypsin deficiency.
Bouchecareilh M; Conkright JJ; Balch WE
Proc Am Thorac Soc; 2010 Nov; 7(6):415-22. PubMed ID: 21030523
[TBL] [Abstract][Full Text] [Related]
5. Proteostasis, an emerging therapeutic paradigm for managing inflammatory airway stress disease.
Bouchecareilh M; Balch WE
Curr Mol Med; 2012 Aug; 12(7):815-26. PubMed ID: 22697348
[TBL] [Abstract][Full Text] [Related]
6. [Alpha-1 antitrypsin deficiency: A model of alteration of protein homeostasis or proteostasis].
Vignaud H; Cullin C; Bouchecareilh M
Rev Mal Respir; 2015 Dec; 32(10):1059-71. PubMed ID: 26386628
[TBL] [Abstract][Full Text] [Related]
7. Alpha1-antitrypsin deficiency: biological answers to clinical questions.
Coakley RJ; Taggart C; O'Neill S; McElvaney NG
Am J Med Sci; 2001 Jan; 321(1):33-41. PubMed ID: 11202478
[TBL] [Abstract][Full Text] [Related]
8. Proteostasis impairment in protein-misfolding and -aggregation diseases.
Hipp MS; Park SH; Hartl FU
Trends Cell Biol; 2014 Sep; 24(9):506-14. PubMed ID: 24946960
[TBL] [Abstract][Full Text] [Related]
9. [Alpha-1-antitrypsin deficiency].
Bouchecareilh M
Med Sci (Paris); 2014 Oct; 30(10):889-95. PubMed ID: 25311024
[TBL] [Abstract][Full Text] [Related]
10. Underlying mechanisms and chemical/biochemical therapeutic approaches to ameliorate protein misfolding neurodegenerative diseases.
Hekmatimoghaddam S; Zare-Khormizi MR; Pourrajab F
Biofactors; 2017 Nov; 43(6):737-759. PubMed ID: 26899445
[TBL] [Abstract][Full Text] [Related]
11. The proteostasis boundary in misfolding diseases of membrane traffic.
Hutt DM; Powers ET; Balch WE
FEBS Lett; 2009 Aug; 583(16):2639-46. PubMed ID: 19708088
[TBL] [Abstract][Full Text] [Related]
12. Lack of effect of oral 4-phenylbutyrate on serum alpha-1-antitrypsin in patients with alpha-1-antitrypsin deficiency: a preliminary study.
Teckman JH
J Pediatr Gastroenterol Nutr; 2004 Jul; 39(1):34-7. PubMed ID: 15187777
[TBL] [Abstract][Full Text] [Related]
13. Modeling general proteostasis: proteome balance in health and disease.
Roth DM; Balch WE
Curr Opin Cell Biol; 2011 Apr; 23(2):126-34. PubMed ID: 21131189
[TBL] [Abstract][Full Text] [Related]
14. Chemical Biology Framework to Illuminate Proteostasis.
Sebastian RM; Shoulders MD
Annu Rev Biochem; 2020 Jun; 89():529-555. PubMed ID: 32097570
[TBL] [Abstract][Full Text] [Related]
15. Emergent properties of proteostasis in managing cystic fibrosis.
Balch WE; Roth DM; Hutt DM
Cold Spring Harb Perspect Biol; 2011 Feb; 3(2):. PubMed ID: 21421917
[TBL] [Abstract][Full Text] [Related]
16. Intrapleural administration of an AAVrh.10 vector coding for human α1-antitrypsin for the treatment of α1-antitrypsin deficiency.
Chiuchiolo MJ; Kaminsky SM; Sondhi D; Hackett NR; Rosenberg JB; Frenk EZ; Hwang Y; Van de Graaf BG; Hutt JA; Wang G; Benson J; Crystal RG
Hum Gene Ther Clin Dev; 2013 Dec; 24(4):161-73. PubMed ID: 24191907
[TBL] [Abstract][Full Text] [Related]
17. Biological and chemical approaches to diseases of proteostasis deficiency.
Powers ET; Morimoto RI; Dillin A; Kelly JW; Balch WE
Annu Rev Biochem; 2009; 78():959-91. PubMed ID: 19298183
[TBL] [Abstract][Full Text] [Related]
18. Endoplasmic reticulum polymers impair luminal protein mobility and sensitize to cellular stress in alpha1-antitrypsin deficiency.
Ordóñez A; Snapp EL; Tan L; Miranda E; Marciniak SJ; Lomas DA
Hepatology; 2013 May; 57(5):2049-60. PubMed ID: 23197448
[TBL] [Abstract][Full Text] [Related]
19. Tracing genetic diversity captures the molecular basis of misfolding disease.
Zhao P; Wang C; Sun S; Wang X; Balch WE
Nat Commun; 2024 Apr; 15(1):3333. PubMed ID: 38637533
[TBL] [Abstract][Full Text] [Related]
20. [Alpha-1 antitrypsin deficiency 50 years later].
Mornex JF
Bull Acad Natl Med; 2014; 198(4-5):757-66. PubMed ID: 26753407
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]