196 related articles for article (PubMed ID: 21584652)
1. Variably protease-sensitive prionopathy: a novel disease of the prion protein.
Gambetti P; Puoti G; Zou WQ
J Mol Neurosci; 2011 Nov; 45(3):422-4. PubMed ID: 21584652
[TBL] [Abstract][Full Text] [Related]
2. Variably protease-sensitive prionopathy.
Notari S; Appleby BS; Gambetti P
Handb Clin Neurol; 2018; 153():175-190. PubMed ID: 29887135
[TBL] [Abstract][Full Text] [Related]
3. Variably protease-sensitive prionopathy: a new sporadic disease of the prion protein.
Zou WQ; Puoti G; Xiao X; Yuan J; Qing L; Cali I; Shimoji M; Langeveld JP; Castellani R; Notari S; Crain B; Schmidt RE; Geschwind M; Dearmond SJ; Cairns NJ; Dickson D; Honig L; Torres JM; Mastrianni J; Capellari S; Giaccone G; Belay ED; Schonberger LB; Cohen M; Perry G; Kong Q; Parchi P; Tagliavini F; Gambetti P
Ann Neurol; 2010 Aug; 68(2):162-72. PubMed ID: 20695009
[TBL] [Abstract][Full Text] [Related]
4. The prion protein protease sensitivity, stability and seeding activity in variably protease sensitive prionopathy brain tissue suggests molecular overlaps with sporadic Creutzfeldt-Jakob disease.
Peden AH; Sarode DP; Mulholland CR; Barria MA; Ritchie DL; Ironside JW; Head MW
Acta Neuropathol Commun; 2014 Oct; 2():152. PubMed ID: 25331173
[TBL] [Abstract][Full Text] [Related]
5. Human prion diseases in the Netherlands (1998-2009): clinical, genetic and molecular aspects.
Jansen C; Parchi P; Capellari S; Ibrahim-Verbaas CA; Schuur M; Strammiello R; Corrado P; Bishop MT; van Gool WA; Verbeek MM; Baas F; van Saane W; Spliet WG; Jansen GH; van Duijn CM; Rozemuller AJ
PLoS One; 2012; 7(4):e36333. PubMed ID: 22558438
[TBL] [Abstract][Full Text] [Related]
6. Variably protease-sensitive prionopathy with methionine homozygosity at codon 129 in the prion protein gene.
Clemmensen FK; Areskeviciute A; Lund EL; Roos P
BMJ Case Rep; 2024 Feb; 17(2):. PubMed ID: 38388201
[TBL] [Abstract][Full Text] [Related]
7. Variably protease-sensitive prionopathy, a unique prion variant with inefficient transmission properties.
Diack AB; Ritchie DL; Peden AH; Brown D; Boyle A; Morabito L; Maclennan D; Burgoyne P; Jansen C; Knight RS; Piccardo P; Ironside JW; Manson JC
Emerg Infect Dis; 2014 Dec; 20(12):1969-79. PubMed ID: 25418327
[TBL] [Abstract][Full Text] [Related]
8. In Vitro Seeding Activity of Glycoform-Deficient Prions from Variably Protease-Sensitive Prionopathy and Familial CJD Associated with PrP
Wang Z; Yuan J; Shen P; Abskharon R; Lang Y; Dang J; Adornato A; Xu L; Chen J; Feng J; Moudjou M; Kitamoto T; Lee HG; Kim YS; Langeveld J; Appleby B; Ma J; Kong Q; Petersen RB; Zou WQ; Cui L
Mol Neurobiol; 2019 Aug; 56(8):5456-5469. PubMed ID: 30612334
[TBL] [Abstract][Full Text] [Related]
9. Transmission characteristics of variably protease-sensitive prionopathy.
Notari S; Xiao X; Espinosa JC; Cohen Y; Qing L; Aguilar-Calvo P; Kofskey D; Cali I; Cracco L; Kong Q; Torres JM; Zou W; Gambetti P
Emerg Infect Dis; 2014 Dec; 20(12):2006-14. PubMed ID: 25418590
[TBL] [Abstract][Full Text] [Related]
10. A novel form of human disease with a protease-sensitive prion protein and heterozygosity methionine/valine at codon 129: Case report.
Rodríguez-Martínez AB; Garrido JM; Zarranz JJ; Arteagoitia JM; de Pancorbo MM; Atarés B; Bilbao MJ; Ferrer I; Juste RA
BMC Neurol; 2010 Oct; 10():99. PubMed ID: 20973975
[TBL] [Abstract][Full Text] [Related]
11. Glycoform-selective prion formation in sporadic and familial forms of prion disease.
Xiao X; Yuan J; Haïk S; Cali I; Zhan Y; Moudjou M; Li B; Laplanche JL; Laude H; Langeveld J; Gambetti P; Kitamoto T; Kong Q; Brandel JP; Cobb BA; Petersen RB; Zou WQ
PLoS One; 2013; 8(3):e58786. PubMed ID: 23527023
[TBL] [Abstract][Full Text] [Related]
12. Variably protease-sensitive prionopathy mimicking frontotemporal dementia.
Aizpurua M; Selvackadunco S; Yull H; Kipps CM; Ironside JW; Bodi I
Neuropathology; 2019 Apr; 39(2):135-140. PubMed ID: 30847986
[TBL] [Abstract][Full Text] [Related]
13. Variable Protease-Sensitive Prionopathy Transmission to Bank Voles.
Nonno R; Notari S; Di Bari MA; Cali I; Pirisinu L; d'Agostino C; Cracco L; Kofskey D; Vanni I; Lavrich J; Parchi P; Agrimi U; Gambetti P
Emerg Infect Dis; 2019 Jan; 25(1):73-81. PubMed ID: 30561322
[TBL] [Abstract][Full Text] [Related]
14. Variably protease-sensitive prionopathy in the UK: a retrospective review 1991-2008.
Head MW; Yull HM; Ritchie DL; Langeveld JP; Fletcher NA; Knight RS; Ironside JW
Brain; 2013 Apr; 136(Pt 4):1102-15. PubMed ID: 23550113
[TBL] [Abstract][Full Text] [Related]
15. An autopsy case of variably protease-sensitive prionopathy with Met/Met homogeneity at codon 129.
Uchino A; Saito Y; Oonuma S; Murayama S; Yagishita S; Kitamoto T; Hasegawa K
Neuropathology; 2023 Dec; 43(6):486-495. PubMed ID: 37253452
[TBL] [Abstract][Full Text] [Related]
16. Prions in variably protease-sensitive prionopathy: an update.
Zou WQ; Gambetti P; Xiao X; Yuan J; Langeveld J; Pirisinu L
Pathogens; 2013 Jul; 2(3):457-71. PubMed ID: 25437202
[TBL] [Abstract][Full Text] [Related]
17. Absence of spontaneous disease and comparative prion susceptibility of transgenic mice expressing mutant human prion proteins.
Asante EA; Gowland I; Grimshaw A; Linehan JM; Smidak M; Houghton R; Osiguwa O; Tomlinson A; Joiner S; Brandner S; Wadsworth JDF; Collinge J
J Gen Virol; 2009 Mar; 90(Pt 3):546-558. PubMed ID: 19218199
[TBL] [Abstract][Full Text] [Related]
18. Further Characterization of Glycoform-Selective Prions of Variably Protease-Sensitive Prionopathy.
Zhang W; Xiao X; Ding M; Yuan J; Foutz A; Moudjou M; Kitamoto T; Langeveld JPM; Cui L; Zou WQ
Pathogens; 2021 Apr; 10(5):. PubMed ID: 33922765
[TBL] [Abstract][Full Text] [Related]
19. Association of prion protein genotype and scrapie prion protein type with cellular prion protein charge isoform profiles in cerebrospinal fluid of humans with sporadic or familial prion diseases.
Schmitz M; Lüllmann K; Zafar S; Ebert E; Wohlhage M; Oikonomou P; Schlomm M; Mitrova E; Beekes M; Zerr I
Neurobiol Aging; 2014 May; 35(5):1177-88. PubMed ID: 24360565
[TBL] [Abstract][Full Text] [Related]
20. A novel human disease with abnormal prion protein sensitive to protease.
Gambetti P; Dong Z; Yuan J; Xiao X; Zheng M; Alshekhlee A; Castellani R; Cohen M; Barria MA; Gonzalez-Romero D; Belay ED; Schonberger LB; Marder K; Harris C; Burke JR; Montine T; Wisniewski T; Dickson DW; Soto C; Hulette CM; Mastrianni JA; Kong Q; Zou WQ
Ann Neurol; 2008 Jun; 63(6):697-708. PubMed ID: 18571782
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]
