These tools will no longer be maintained as of December 31, 2024. Archived website can be found here. PubMed4Hh GitHub repository can be found here. Contact NLM Customer Service if you have questions.
25. PRRT2 gene variant in a child with dysmorphic features, congenital microcephaly, and severe epileptic seizures: genotype-phenotype correlation? Pavone P; Corsello G; Cho SY; Pappalardo XG; Ruggieri M; Marino SD; Jin DK; Marino S; Falsaperla R Ital J Pediatr; 2019 Dec; 45(1):159. PubMed ID: 31801583 [TBL] [Abstract][Full Text] [Related]
26. Wolcott-Rallison syndrome is the most common genetic cause of permanent neonatal diabetes in consanguineous families. Rubio-Cabezas O; Patch AM; Minton JA; Flanagan SE; Edghill EL; Hussain K; Balafrej A; Deeb A; Buchanan CR; Jefferson IG; Mutair A; ; Hattersley AT; Ellard S J Clin Endocrinol Metab; 2009 Nov; 94(11):4162-70. PubMed ID: 19837917 [TBL] [Abstract][Full Text] [Related]
27. A neuropathological study of novel RTTN gene mutations causing a familial microcephaly with simplified gyral pattern. Chartier S; Alby C; Boutaud L; Thomas S; Elkhartoufi N; Martinovic J; Kaplan J; Benachi A; Lacombe D; Sonigo P; Drunat S; Vekemans M; Agenor J; Encha Razavi F; Attie-Bitach T Birth Defects Res; 2018 Apr; 110(7):598-602. PubMed ID: 29356416 [TBL] [Abstract][Full Text] [Related]
28. Loss of NARS1 impairs progenitor proliferation in cortical brain organoids and leads to microcephaly. Wang L; Li Z; Sievert D; Smith DEC; Mendes MI; Chen DY; Stanley V; Ghosh S; Wang Y; Kara M; Aslanger AD; Rosti RO; Houlden H; Salomons GS; Gleeson JG Nat Commun; 2020 Aug; 11(1):4038. PubMed ID: 32788587 [TBL] [Abstract][Full Text] [Related]
29. Autosomal-Recessive Mutations in AP3B2, Adaptor-Related Protein Complex 3 Beta 2 Subunit, Cause an Early-Onset Epileptic Encephalopathy with Optic Atrophy. Assoum M; Philippe C; Isidor B; Perrin L; Makrythanasis P; Sondheimer N; Paris C; Douglas J; Lesca G; Antonarakis S; Hamamy H; Jouan T; Duffourd Y; Auvin S; Saunier A; Begtrup A; Nowak C; Chatron N; Ville D; Mireskandari K; Milani P; Jonveaux P; Lemeur G; Milh M; Amamoto M; Kato M; Nakashima M; Miyake N; Matsumoto N; Masri A; Thauvin-Robinet C; Rivière JB; Faivre L; Thevenon J Am J Hum Genet; 2016 Dec; 99(6):1368-1376. PubMed ID: 27889060 [TBL] [Abstract][Full Text] [Related]
30. A Genotype-First Approach for Clinical and Genetic Evaluation of Wolcott-Rallison Syndrome in a Large Cohort of Iranian Children With Neonatal Diabetes. Abbasi F; Habibi M; Enayati S; Bitarafan F; Razzaghy-Azar M; Sotodeh A; Omran SP; Maroofian R; Amoli MM Can J Diabetes; 2018 Jun; 42(3):272-275. PubMed ID: 28843469 [TBL] [Abstract][Full Text] [Related]
31. DPM2-CDG: a muscular dystrophy-dystroglycanopathy syndrome with severe epilepsy. Barone R; Aiello C; Race V; Morava E; Foulquier F; Riemersma M; Passarelli C; Concolino D; Carella M; Santorelli F; Vleugels W; Mercuri E; Garozzo D; Sturiale L; Messina S; Jaeken J; Fiumara A; Wevers RA; Bertini E; Matthijs G; Lefeber DJ Ann Neurol; 2012 Oct; 72(4):550-8. PubMed ID: 23109149 [TBL] [Abstract][Full Text] [Related]
32. Delineating SPTAN1 associated phenotypes: from isolated epilepsy to encephalopathy with progressive brain atrophy. Syrbe S; Harms FL; Parrini E; Montomoli M; Mütze U; Helbig KL; Polster T; Albrecht B; Bernbeck U; van Binsbergen E; Biskup S; Burglen L; Denecke J; Heron B; Heyne HO; Hoffmann GF; Hornemann F; Matsushige T; Matsuura R; Kato M; Korenke GC; Kuechler A; Lämmer C; Merkenschlager A; Mignot C; Ruf S; Nakashima M; Saitsu H; Stamberger H; Pisano T; Tohyama J; Weckhuysen S; Werckx W; Wickert J; Mari F; Verbeek NE; Møller RS; Koeleman B; Matsumoto N; Dobyns WB; Battaglia D; Lemke JR; Kutsche K; Guerrini R Brain; 2017 Sep; 140(9):2322-2336. PubMed ID: 29050398 [TBL] [Abstract][Full Text] [Related]
33. EIF2AK3 mutations in South Indian children with permanent neonatal diabetes mellitus associated with Wolcott-Rallison syndrome. Jahnavi S; Poovazhagi V; Kanthimathi S; Gayathri V; Mohan V; Radha V Pediatr Diabetes; 2014 Jun; 15(4):313-8. PubMed ID: 24168455 [TBL] [Abstract][Full Text] [Related]
34. Cloning and characterization of a novel endoplasmic reticulum localized G-patch domain protein, IER3IP1. Yiu WH; Poon JW; Tsui SK; Fung KP; Waye MM Gene; 2004 Aug; 337():37-44. PubMed ID: 15276200 [TBL] [Abstract][Full Text] [Related]
36. A complex microcephaly syndrome in a Pakistani family associated with a novel missense mutation in RBBP8 and a heterozygous deletion in NRXN1. Agha Z; Iqbal Z; Azam M; Siddique M; Willemsen MH; Kleefstra T; Zweier C; de Leeuw N; Qamar R; van Bokhoven H Gene; 2014 Mar; 538(1):30-5. PubMed ID: 24440292 [TBL] [Abstract][Full Text] [Related]
37. RRP7A links primary microcephaly to dysfunction of ribosome biogenesis, resorption of primary cilia, and neurogenesis. Farooq M; Lindbæk L; Krogh N; Doganli C; Keller C; Mönnich M; Gonçalves AB; Sakthivel S; Mang Y; Fatima A; Andersen VS; Hussain MS; Eiberg H; Hansen L; Kjaer KW; Gopalakrishnan J; Pedersen LB; Møllgård K; Nielsen H; Baig SM; Tommerup N; Christensen ST; Larsen LA Nat Commun; 2020 Nov; 11(1):5816. PubMed ID: 33199730 [TBL] [Abstract][Full Text] [Related]
38. Functional characterization of biallelic RTTN variants identified in an infant with microcephaly, simplified gyral pattern, pontocerebellar hypoplasia, and seizures. Wambach JA; Wegner DJ; Yang P; Shinawi M; Baldridge D; Betleja E; Shimony JS; Spencer D; Hackett BP; Andrews MV; Ferkol T; Dutcher SK; Mahjoub MR; Cole FS Pediatr Res; 2018 Sep; 84(3):435-441. PubMed ID: 29967526 [TBL] [Abstract][Full Text] [Related]
39. Two novel EIF2S3 mutations associated with syndromic intellectual disability with severe microcephaly, growth retardation, and epilepsy. Moortgat S; Désir J; Benoit V; Boulanger S; Pendeville H; Nassogne MC; Lederer D; Maystadt I Am J Med Genet A; 2016 Nov; 170(11):2927-2933. PubMed ID: 27333055 [TBL] [Abstract][Full Text] [Related]