533 related articles for article (PubMed ID: 21867484)
1. Tetrahydrobiopterin: biochemistry and pathophysiology.
Werner ER; Blau N; Thöny B
Biochem J; 2011 Sep; 438(3):397-414. PubMed ID: 21867484
[TBL] [Abstract][Full Text] [Related]
2. Tetrahydrobiopterin biosynthesis, regeneration and functions.
Thöny B; Auerbach G; Blau N
Biochem J; 2000 Apr; 347 Pt 1(Pt 1):1-16. PubMed ID: 10727395
[TBL] [Abstract][Full Text] [Related]
3. Sapropterin dihydrochloride, 6-R-L-erythro-5,6,7,8-tetrahydrobiopterin, in the treatment of phenylketonuria.
Michals-Matalon K
Expert Opin Investig Drugs; 2008 Feb; 17(2):245-51. PubMed ID: 18230057
[TBL] [Abstract][Full Text] [Related]
4. Nitric oxide synthase inhibition and oxidative stress in cardiovascular diseases: possible therapeutic targets?
Rochette L; Lorin J; Zeller M; Guilland JC; Lorgis L; Cottin Y; Vergely C
Pharmacol Ther; 2013 Dec; 140(3):239-57. PubMed ID: 23859953
[TBL] [Abstract][Full Text] [Related]
5. Mutations in the BH4-metabolizing genes GTP cyclohydrolase I, 6-pyruvoyl-tetrahydropterin synthase, sepiapterin reductase, carbinolamine-4a-dehydratase, and dihydropteridine reductase.
Thöny B; Blau N
Hum Mutat; 2006 Sep; 27(9):870-8. PubMed ID: 16917893
[TBL] [Abstract][Full Text] [Related]
6. Tetrahydrobiopterin protects phenylalanine hydroxylase activity in vivo: implications for tetrahydrobiopterin-responsive hyperphenylalaninemia.
Thöny B; Ding Z; Martínez A
FEBS Lett; 2004 Nov; 577(3):507-11. PubMed ID: 15556637
[TBL] [Abstract][Full Text] [Related]
7. The activity of wild-type and mutant phenylalanine hydroxylase and its regulation by phenylalanine and tetrahydrobiopterin at physiological and pathological concentrations: an isothermal titration calorimetry study.
Pey AL; Martinez A
Mol Genet Metab; 2005 Dec; 86 Suppl 1():S43-53. PubMed ID: 15936235
[TBL] [Abstract][Full Text] [Related]
8. Tetrahydrobiopterin deficiencies without hyperphenylalaninemia: diagnosis and genetics of dopa-responsive dystonia and sepiapterin reductase deficiency.
Blau N; Bonafé L; Thöny B
Mol Genet Metab; 2001; 74(1-2):172-85. PubMed ID: 11592814
[TBL] [Abstract][Full Text] [Related]
9. Molecular and enzymatic characterization of two enzymes BmPCD and BmDHPR involving in the regeneration pathway of tetrahydrobiopterin from the silkworm Bombyx mori.
Li W; Gong M; Shu R; Li X; Gao J; Meng Y
Comp Biochem Physiol B Biochem Mol Biol; 2015 Aug; 186():20-7. PubMed ID: 25899859
[TBL] [Abstract][Full Text] [Related]
10. Regulation of tetrahydrobiopterin synthesis and bioavailability in endothelial cells.
Shi W; Meininger CJ; Haynes TE; Hatakeyama K; Wu G
Cell Biochem Biophys; 2004; 41(3):415-34. PubMed ID: 15509890
[TBL] [Abstract][Full Text] [Related]
11. Nitric oxide and vascular insulin resistance.
Wu G; Meininger CJ
Biofactors; 2009; 35(1):21-7. PubMed ID: 19319842
[TBL] [Abstract][Full Text] [Related]
12. Disorders of biopterin metabolism.
Longo N
J Inherit Metab Dis; 2009 Jun; 32(3):333-42. PubMed ID: 19234759
[TBL] [Abstract][Full Text] [Related]
13. Metabolism of tetrahydrobiopterin: its relevance in monoaminergic neurons and neurological disorders.
Ichinose H; Nomura T; Sumi-Ichinose C
Chem Rec; 2008; 8(6):378-85. PubMed ID: 19107867
[TBL] [Abstract][Full Text] [Related]
14. Disorders of tetrahydrobiopterin metabolism and their treatment.
Shintaku H
Curr Drug Metab; 2002 Apr; 3(2):123-31. PubMed ID: 12003346
[TBL] [Abstract][Full Text] [Related]
15. Unresponsiveness to tetrahydrobiopterin of phenylalanine hydroxylase deficiency.
Ponzone A; Porta F; Mussa A; Alluto A; Ferraris S; Spada M
Metabolism; 2010 May; 59(5):645-52. PubMed ID: 19913839
[TBL] [Abstract][Full Text] [Related]
16. Contrasting effects of N5-substituted tetrahydrobiopterin derivatives on phenylalanine hydroxylase, dihydropteridine reductase and nitric oxide synthase.
Werner ER; Habisch HJ; Gorren AC; Schmidt K; Canevari L; Werner-Felmayer G; Mayer B
Biochem J; 2000 Jun; 348 Pt 3(Pt 3):579-83. PubMed ID: 10839989
[TBL] [Abstract][Full Text] [Related]
17. [Biopterin and child neurologic disease].
Shintaku H
No To Hattatsu; 2009 Jan; 41(1):5-10. PubMed ID: 19172809
[TBL] [Abstract][Full Text] [Related]
18. Tetrahydrobiopterin and cardiovascular disease.
Moens AL; Kass DA
Arterioscler Thromb Vasc Biol; 2006 Nov; 26(11):2439-44. PubMed ID: 16946131
[TBL] [Abstract][Full Text] [Related]
19. Therapeutic potential of tetrahydrobiopterin for treating vascular and cardiac disease.
Moens AL; Kass DA
J Cardiovasc Pharmacol; 2007 Sep; 50(3):238-46. PubMed ID: 17878750
[TBL] [Abstract][Full Text] [Related]
20. Increase in tetrahydrobiopterin concentration with aging in the cerebral cortex of the senescence-accelerated mouse prone 10 strain caused by abnormal regulation of tetrahydrobiopterin biosynthesis.
Miyajima M; Minoshima M; Tanaka M; Nishimura R; Hishioka N; Numata T; Hosokawa T; Kurasaki M; Saito T
Biogerontology; 2013 Oct; 14(5):491-501. PubMed ID: 23933678
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]