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9. Patterns of CAG repeat instability in the central nervous system and periphery in Huntington's disease and in spinocerebellar ataxia type 1. Mouro Pinto R; Arning L; Giordano JV; Razghandi P; Andrew MA; Gillis T; Correia K; Mysore JS; Grote Urtubey DM; Parwez CR; von Hein SM; Clark HB; Nguyen HP; Förster E; Beller A; Jayadaev S; Keene CD; Bird TD; Lucente D; Vonsattel JP; Orr H; Saft C; Petrasch-Parwez E; Wheeler VC Hum Mol Genet; 2020 Aug; 29(15):2551-2567. PubMed ID: 32761094 [TBL] [Abstract][Full Text] [Related]
10. Msh2 acts in medium-spiny striatal neurons as an enhancer of CAG instability and mutant huntingtin phenotypes in Huntington's disease knock-in mice. Kovalenko M; Dragileva E; St Claire J; Gillis T; Guide JR; New J; Dong H; Kucherlapati R; Kucherlapati MH; Ehrlich ME; Lee JM; Wheeler VC PLoS One; 2012; 7(9):e44273. PubMed ID: 22970194 [TBL] [Abstract][Full Text] [Related]
11. Promotion of somatic CAG repeat expansion by Fan1 knock-out in Huntington's disease knock-in mice is blocked by Mlh1 knock-out. Loupe JM; Pinto RM; Kim KH; Gillis T; Mysore JS; Andrew MA; Kovalenko M; Murtha R; Seong I; Gusella JF; Kwak S; Howland D; Lee R; Lee JM; Wheeler VC; MacDonald ME Hum Mol Genet; 2020 Nov; 29(18):3044-3053. PubMed ID: 32876667 [TBL] [Abstract][Full Text] [Related]
12. Instability of highly expanded CAG repeats in mice transgenic for the Huntington's disease mutation. Mangiarini L; Sathasivam K; Mahal A; Mott R; Seller M; Bates GP Nat Genet; 1997 Feb; 15(2):197-200. PubMed ID: 9020849 [TBL] [Abstract][Full Text] [Related]
13. Lack of huntingtin promotes neural stem cells differentiation into glial cells while neurons expressing huntingtin with expanded polyglutamine tracts undergo cell death. Conforti P; Camnasio S; Mutti C; Valenza M; Thompson M; Fossale E; Zeitlin S; MacDonald ME; Zuccato C; Cattaneo E Neurobiol Dis; 2013 Feb; 50():160-70. PubMed ID: 23089356 [TBL] [Abstract][Full Text] [Related]
14. A novel approach to investigate tissue-specific trinucleotide repeat instability. Lee JM; Zhang J; Su AI; Walker JR; Wiltshire T; Kang K; Dragileva E; Gillis T; Lopez ET; Boily MJ; Cyr M; Kohane I; Gusella JF; MacDonald ME; Wheeler VC BMC Syst Biol; 2010 Mar; 4():29. PubMed ID: 20302627 [TBL] [Abstract][Full Text] [Related]
15. Partial resistance to malonate-induced striatal cell death in transgenic mouse models of Huntington's disease is dependent on age and CAG repeat length. Hansson O; Castilho RF; Korhonen L; Lindholm D; Bates GP; Brundin P J Neurochem; 2001 Aug; 78(4):694-703. PubMed ID: 11520890 [TBL] [Abstract][Full Text] [Related]