278 related articles for article (PubMed ID: 22012983)
1. Effect of bezafibrate treatment on late-onset mitochondrial myopathy in mice.
Yatsuga S; Suomalainen A
Hum Mol Genet; 2012 Feb; 21(3):526-35. PubMed ID: 22012983
[TBL] [Abstract][Full Text] [Related]
2. Ketogenic diet slows down mitochondrial myopathy progression in mice.
Ahola-Erkkilä S; Carroll CJ; Peltola-Mjösund K; Tulkki V; Mattila I; Seppänen-Laakso T; Oresic M; Tyynismaa H; Suomalainen A
Hum Mol Genet; 2010 May; 19(10):1974-84. PubMed ID: 20167576
[TBL] [Abstract][Full Text] [Related]
3. Mitochondrial myopathy induces a starvation-like response.
Tyynismaa H; Carroll CJ; Raimundo N; Ahola-Erkkilä S; Wenz T; Ruhanen H; Guse K; Hemminki A; Peltola-Mjøsund KE; Tulkki V; Oresic M; Moraes CT; Pietiläinen K; Hovatta I; Suomalainen A
Hum Mol Genet; 2010 Oct; 19(20):3948-58. PubMed ID: 20656789
[TBL] [Abstract][Full Text] [Related]
4. Activation of the PPAR/PGC-1alpha pathway prevents a bioenergetic deficit and effectively improves a mitochondrial myopathy phenotype.
Wenz T; Diaz F; Spiegelman BM; Moraes CT
Cell Metab; 2008 Sep; 8(3):249-56. PubMed ID: 18762025
[TBL] [Abstract][Full Text] [Related]
5. Activation of peroxisome proliferator-activated receptor pathway stimulates the mitochondrial respiratory chain and can correct deficiencies in patients' cells lacking its components.
Bastin J; Aubey F; Rötig A; Munnich A; Djouadi F
J Clin Endocrinol Metab; 2008 Apr; 93(4):1433-41. PubMed ID: 18211970
[TBL] [Abstract][Full Text] [Related]
6. Mutant mitochondrial helicase Twinkle causes multiple mtDNA deletions and a late-onset mitochondrial disease in mice.
Tyynismaa H; Mjosund KP; Wanrooij S; Lappalainen I; Ylikallio E; Jalanko A; Spelbrink JN; Paetau A; Suomalainen A
Proc Natl Acad Sci U S A; 2005 Dec; 102(49):17687-92. PubMed ID: 16301523
[TBL] [Abstract][Full Text] [Related]
7. In vivo correction of COX deficiency by activation of the AMPK/PGC-1α axis.
Viscomi C; Bottani E; Civiletto G; Cerutti R; Moggio M; Fagiolari G; Schon EA; Lamperti C; Zeviani M
Cell Metab; 2011 Jul; 14(1):80-90. PubMed ID: 21723506
[TBL] [Abstract][Full Text] [Related]
8. Pharmacologic activation of mitochondrial biogenesis exerts widespread beneficial effects in a transgenic mouse model of Huntington's disease.
Johri A; Calingasan NY; Hennessey TM; Sharma A; Yang L; Wille E; Chandra A; Beal MF
Hum Mol Genet; 2012 Mar; 21(5):1124-37. PubMed ID: 22095692
[TBL] [Abstract][Full Text] [Related]
9. Hydroxytyrosol promotes mitochondrial biogenesis and mitochondrial function in 3T3-L1 adipocytes.
Hao J; Shen W; Yu G; Jia H; Li X; Feng Z; Wang Y; Weber P; Wertz K; Sharman E; Liu J
J Nutr Biochem; 2010 Jul; 21(7):634-44. PubMed ID: 19576748
[TBL] [Abstract][Full Text] [Related]
10. Endurance exercise is protective for mice with mitochondrial myopathy.
Wenz T; Diaz F; Hernandez D; Moraes CT
J Appl Physiol (1985); 2009 May; 106(5):1712-9. PubMed ID: 19286571
[TBL] [Abstract][Full Text] [Related]
11. Bezafibrate ameliorates diabetes via reduced steatosis and improved hepatic insulin sensitivity in diabetic TallyHo mice.
Franko A; Neschen S; Rozman J; Rathkolb B; Aichler M; Feuchtinger A; Brachthäuser L; Neff F; Kovarova M; Wolf E; Fuchs H; Häring HU; Peter A; Hrabě de Angelis M
Mol Metab; 2017 Mar; 6(3):256-266. PubMed ID: 28271032
[TBL] [Abstract][Full Text] [Related]
12. Retinoic acid treatment increases lipid oxidation capacity in skeletal muscle of mice.
Amengual J; Ribot J; Bonet ML; Palou A
Obesity (Silver Spring); 2008 Mar; 16(3):585-91. PubMed ID: 18239600
[TBL] [Abstract][Full Text] [Related]
13. Mice lacking COX10 in skeletal muscle recapitulate the phenotype of progressive mitochondrial myopathies associated with cytochrome c oxidase deficiency.
Diaz F; Thomas CK; Garcia S; Hernandez D; Moraes CT
Hum Mol Genet; 2005 Sep; 14(18):2737-48. PubMed ID: 16103131
[TBL] [Abstract][Full Text] [Related]
14. Dual and pan-peroxisome proliferator-activated receptors (PPAR) co-agonism: the bezafibrate lessons.
Tenenbaum A; Motro M; Fisman EZ
Cardiovasc Diabetol; 2005 Sep; 4():14. PubMed ID: 16168052
[TBL] [Abstract][Full Text] [Related]
15. Long-term bezafibrate treatment improves skin and spleen phenotypes of the mtDNA mutator mouse.
Dillon LM; Hida A; Garcia S; Prolla TA; Moraes CT
PLoS One; 2012; 7(9):e44335. PubMed ID: 22962610
[TBL] [Abstract][Full Text] [Related]
16. Bezafibrate activation of PPAR drives disturbances in mitochondrial redox bioenergetics and decreases the viability of cells from patients with VLCAD deficiency.
Lund M; Andersen KG; Heaton R; Hargreaves IP; Gregersen N; Olsen RKJ
Biochim Biophys Acta Mol Basis Dis; 2021 Jun; 1867(6):166100. PubMed ID: 33549744
[TBL] [Abstract][Full Text] [Related]
17. Bezafibrate upregulates carnitine palmitoyltransferase II expression and promotes mitochondrial energy crisis dissipation in fibroblasts of patients with influenza-associated encephalopathy.
Yao M; Yao D; Yamaguchi M; Chida J; Yao D; Kido H
Mol Genet Metab; 2011 Nov; 104(3):265-72. PubMed ID: 21816645
[TBL] [Abstract][Full Text] [Related]
18. Clinical progression of mitochondrial myopathy is associated with the random accumulation of cytochrome c oxidase negative skeletal muscle fibres.
Chinnery PF; Howel D; Turnbull DM; Johnson MA
J Neurol Sci; 2003 Jul; 211(1-2):63-6. PubMed ID: 12767499
[TBL] [Abstract][Full Text] [Related]
19. Metabolic effects of bezafibrate in mitochondrial disease.
Steele H; Gomez-Duran A; Pyle A; Hopton S; Newman J; Stefanetti RJ; Charman SJ; Parikh JD; He L; Viscomi C; Jakovljevic DG; Hollingsworth KG; Robinson AJ; Taylor RW; Bottolo L; Horvath R; Chinnery PF
EMBO Mol Med; 2020 Mar; 12(3):e11589. PubMed ID: 32107855
[TBL] [Abstract][Full Text] [Related]
20. Myopathy caused by mammalian target of rapamycin complex 1 (mTORC1) inactivation is not reversed by restoring mitochondrial function.
Romanino K; Mazelin L; Albert V; Conjard-Duplany A; Lin S; Bentzinger CF; Handschin C; Puigserver P; Zorzato F; Schaeffer L; Gangloff YG; Rüegg MA
Proc Natl Acad Sci U S A; 2011 Dec; 108(51):20808-13. PubMed ID: 22143799
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]
