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2. SRD5A3-CDG: Expanding the phenotype of a congenital disorder of glycosylation with emphasis on adult onset features. Wheeler PG; Ng BG; Sanford L; Sutton VR; Bartholomew DW; Pastore MT; Bamshad MJ; Kircher M; Buckingham KJ; Nickerson DA; Shendure J; Freeze HH Am J Med Genet A; 2016 Dec; 170(12):3165-3171. PubMed ID: 27480077 [TBL] [Abstract][Full Text] [Related]
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6. Association of Steroid 5α-Reductase Type 3 Congenital Disorder of Glycosylation With Early-Onset Retinal Dystrophy. Taylor RL; Arno G; Poulter JA; Khan KN; Morarji J; Hull S; Pontikos N; Rueda Martin A; Smith KR; Ali M; Toomes C; McKibbin M; Clayton-Smith J; Grunewald S; Michaelides M; Moore AT; Hardcastle AJ; Inglehearn CF; Webster AR; Black GC; JAMA Ophthalmol; 2017 Apr; 135(4):339-347. PubMed ID: 28253385 [TBL] [Abstract][Full Text] [Related]
7. Review of SRD5A3 Disease-Causing Sequence Variants and Ocular Findings in Steroid 5α-Reductase Type 3 Congenital Disorder of Glycosylation, and a Detailed New Case. Kousal B; Honzík T; Hansíková H; Ondrušková N; Čechová A; Tesařová M; Stránecký V; Meliška M; Michaelides M; Lišková P Folia Biol (Praha); 2019; 65(3):134-141. PubMed ID: 31638560 [TBL] [Abstract][Full Text] [Related]
8. SRD5A3-CDG: 3D structure modeling, clinical spectrum, and computer-based dysmorphic facial recognition. Ben Ayed I; Ouarda W; Frikha F; Kammoun F; Souissi A; Ben Said M; Bouzid A; Elloumi I; Hamdani TM; Gharbi N; Baklouti N; Guirat M; Mejdoub F; Kharrat N; Boujelbene I; Abdelhedi F; Belguith N; Keskes L; Gibriel AA; Kamoun H; Triki C; Alimi AM; Masmoudi S Am J Med Genet A; 2021 Apr; 185(4):1081-1090. PubMed ID: 33403770 [TBL] [Abstract][Full Text] [Related]
9. Deficiency of dolichol-phosphate-mannose synthase-1 causes congenital disorder of glycosylation type Ie. Imbach T; Schenk B; Schollen E; Burda P; Stutz A; Grunewald S; Bailie NM; King MD; Jaeken J; Matthijs G; Berger EG; Aebi M; Hennet T J Clin Invest; 2000 Jan; 105(2):233-9. PubMed ID: 10642602 [TBL] [Abstract][Full Text] [Related]
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11. Next generation sequencing in a family with autosomal recessive Kahrizi syndrome (OMIM 612713) reveals a homozygous frameshift mutation in SRD5A3. Kahrizi K; Hu CH; Garshasbi M; Abedini SS; Ghadami S; Kariminejad R; Ullmann R; Chen W; Ropers HH; Kuss AW; Najmabadi H; Tzschach A Eur J Hum Genet; 2011 Jan; 19(1):115-7. PubMed ID: 20700148 [TBL] [Abstract][Full Text] [Related]
12. Adult phenotype and further phenotypic variability in SRD5A3-CDG. Kara B; Ayhan Ö; Gökçay G; Başboğaoğlu N; Tolun A BMC Med Genet; 2014 Jan; 15():10. PubMed ID: 24433453 [TBL] [Abstract][Full Text] [Related]
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