323 related articles for article (PubMed ID: 22323289)
1. The human mitochondrial ISCA1, ISCA2, and IBA57 proteins are required for [4Fe-4S] protein maturation.
Sheftel AD; Wilbrecht C; Stehling O; Niggemeyer B; Elsässer HP; Mühlenhoff U; Lill R
Mol Biol Cell; 2012 Apr; 23(7):1157-66. PubMed ID: 22323289
[TBL] [Abstract][Full Text] [Related]
2. Specialized function of yeast Isa1 and Isa2 proteins in the maturation of mitochondrial [4Fe-4S] proteins.
Mühlenhoff U; Richter N; Pines O; Pierik AJ; Lill R
J Biol Chem; 2011 Dec; 286(48):41205-41216. PubMed ID: 21987576
[TBL] [Abstract][Full Text] [Related]
3. ISCA1 Orchestrates ISCA2 and NFU1 in the Maturation of Human Mitochondrial [4Fe-4S] Proteins.
Suraci D; Saudino G; Nasta V; Ciofi-Baffoni S; Banci L
J Mol Biol; 2021 May; 433(10):166924. PubMed ID: 33711344
[TBL] [Abstract][Full Text] [Related]
4. Mitochondrial [4Fe-4S] protein assembly involves reductive [2Fe-2S] cluster fusion on ISCA1-ISCA2 by electron flow from ferredoxin FDX2.
Weiler BD; Brück MC; Kothe I; Bill E; Lill R; Mühlenhoff U
Proc Natl Acad Sci U S A; 2020 Aug; 117(34):20555-20565. PubMed ID: 32817474
[TBL] [Abstract][Full Text] [Related]
5. Formation of [4Fe-4S] clusters in the mitochondrial iron-sulfur cluster assembly machinery.
Brancaccio D; Gallo A; Mikolajczyk M; Zovo K; Palumaa P; Novellino E; Piccioli M; Ciofi-Baffoni S; Banci L
J Am Chem Soc; 2014 Nov; 136(46):16240-50. PubMed ID: 25347204
[TBL] [Abstract][Full Text] [Related]
6. The iron-sulfur cluster assembly (ISC) protein Iba57 executes a tetrahydrofolate-independent function in mitochondrial [4Fe-4S] protein maturation.
Mühlenhoff U; Weiler BD; Nadler F; Millar R; Kothe I; Freibert SA; Altegoer F; Bange G; Lill R
J Biol Chem; 2022 Oct; 298(10):102465. PubMed ID: 36075292
[TBL] [Abstract][Full Text] [Related]
7. Structural properties of [2Fe-2S] ISCA2-IBA57: a complex of the mitochondrial iron-sulfur cluster assembly machinery.
Nasta V; Da Vela S; Gourdoupis S; Ciofi-Baffoni S; Svergun DI; Banci L
Sci Rep; 2019 Dec; 9(1):18986. PubMed ID: 31831856
[TBL] [Abstract][Full Text] [Related]
8. Structural Plasticity of NFU1 Upon Interaction with Binding Partners: Insights into the Mitochondrial [4Fe-4S] Cluster Pathway.
Da Vela S; Saudino G; Lucarelli F; Banci L; Svergun DI; Ciofi-Baffoni S
J Mol Biol; 2023 Aug; 435(15):168154. PubMed ID: 37211204
[TBL] [Abstract][Full Text] [Related]
9. Molecular Basis of Rare Diseases Associated to the Maturation of Mitochondrial [4Fe-4S]-Containing Proteins.
Camponeschi F; Ciofi-Baffoni S; Calderone V; Banci L
Biomolecules; 2022 Jul; 12(7):. PubMed ID: 35883565
[TBL] [Abstract][Full Text] [Related]
10. ISCA1 mutation in a patient with infantile-onset leukodystrophy causes defects in mitochondrial [4Fe-4S] proteins.
Torraco A; Stehling O; Stümpfig C; Rösser R; De Rasmo D; Fiermonte G; Verrigni D; Rizza T; Vozza A; Di Nottia M; Diodato D; Martinelli D; Piemonte F; Dionisi-Vici C; Bertini E; Lill R; Carrozzo R
Hum Mol Genet; 2018 Aug; 27(15):2739-2754. PubMed ID: 29767723
[TBL] [Abstract][Full Text] [Related]
11. Human ISCA1 interacts with IOP1/NARFL and functions in both cytosolic and mitochondrial iron-sulfur protein biogenesis.
Song D; Tu Z; Lee FS
J Biol Chem; 2009 Dec; 284(51):35297-307. PubMed ID: 19864422
[TBL] [Abstract][Full Text] [Related]
12. IBA57 Recruits ISCA2 to Form a [2Fe-2S] Cluster-Mediated Complex.
Gourdoupis S; Nasta V; Calderone V; Ciofi-Baffoni S; Banci L
J Am Chem Soc; 2018 Oct; 140(43):14401-14412. PubMed ID: 30269484
[TBL] [Abstract][Full Text] [Related]
13. Impact of mutations within the [Fe-S] cluster or the lipoic acid biosynthesis pathways on mitochondrial protein expression profiles in fibroblasts from patients.
Lebigot E; Gaignard P; Dorboz I; Slama A; Rio M; de Lonlay P; Héron B; Sabourdy F; Boespflug-Tanguy O; Cardoso A; Habarou F; Ottolenghi C; Thérond P; Bouton C; Golinelli-Cohen MP; Boutron A
Mol Genet Metab; 2017 Nov; 122(3):85-94. PubMed ID: 28803783
[TBL] [Abstract][Full Text] [Related]
14. ISCA1 is essential for mitochondrial Fe
Beilschmidt LK; Ollagnier de Choudens S; Fournier M; Sanakis I; Hograindleur MA; Clémancey M; Blondin G; Schmucker S; Eisenmann A; Weiss A; Koebel P; Messaddeq N; Puccio H; Martelli A
Nat Commun; 2017 May; 8():15124. PubMed ID: 28492233
[TBL] [Abstract][Full Text] [Related]
15. Assembly of the [4Fe-4S] cluster of NFU1 requires the coordinated donation of two [2Fe-2S] clusters from the scaffold proteins, ISCU2 and ISCA1.
Jain A; Singh A; Maio N; Rouault TA
Hum Mol Genet; 2020 Nov; 29(19):3165-3182. PubMed ID: 32776106
[TBL] [Abstract][Full Text] [Related]
16. Mechanisms of Mitochondrial Iron-Sulfur Protein Biogenesis.
Lill R; Freibert SA
Annu Rev Biochem; 2020 Jun; 89():471-499. PubMed ID: 31935115
[TBL] [Abstract][Full Text] [Related]
17. The Arabidopsis Mitochondrial Glutaredoxin GRXS15 Provides [2Fe-2S] Clusters for ISCA-Mediated [4Fe-4S] Cluster Maturation.
Azam T; Przybyla-Toscano J; Vignols F; Couturier J; Rouhier N; Johnson MK
Int J Mol Sci; 2020 Dec; 21(23):. PubMed ID: 33287436
[TBL] [Abstract][Full Text] [Related]
18. Requirements for the biogenesis of [2Fe-2S] proteins in the human and yeast cytosol.
Braymer JJ; Stehling O; Stümpfig M; Rösser R; Spantgar F; Blinn CM; Mühlenhoff U; Pierik AJ; Lill R
Proc Natl Acad Sci U S A; 2024 May; 121(21):e2400740121. PubMed ID: 38743629
[TBL] [Abstract][Full Text] [Related]
19. Loss-of-function mutations in ISCA2 disrupt 4Fe-4S cluster machinery and cause a fatal leukodystrophy with hyperglycinemia and mtDNA depletion.
Alaimo JT; Besse A; Alston CL; Pang K; Appadurai V; Samanta M; Smpokou P; McFarland R; Taylor RW; Bonnen PE
Hum Mutat; 2018 Apr; 39(4):537-549. PubMed ID: 29297947
[TBL] [Abstract][Full Text] [Related]
20. A pathway for assembling [4Fe-4S]
Nasta V; Suraci D; Gourdoupis S; Ciofi-Baffoni S; Banci L
FEBS J; 2020 Jun; 287(11):2312-2327. PubMed ID: 31724821
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]
