269 related articles for article (PubMed ID: 22423102)
1. Motor neuron rescue in spinal muscular atrophy mice demonstrates that sensory-motor defects are a consequence, not a cause, of motor neuron dysfunction.
Gogliotti RG; Quinlan KA; Barlow CB; Heier CR; Heckman CJ; Didonato CJ
J Neurosci; 2012 Mar; 32(11):3818-29. PubMed ID: 22423102
[TBL] [Abstract][Full Text] [Related]
2. Early functional impairment of sensory-motor connectivity in a mouse model of spinal muscular atrophy.
Mentis GZ; Blivis D; Liu W; Drobac E; Crowder ME; Kong L; Alvarez FJ; Sumner CJ; O'Donovan MJ
Neuron; 2011 Feb; 69(3):453-67. PubMed ID: 21315257
[TBL] [Abstract][Full Text] [Related]
3. Reduced survival of motor neuron (SMN) protein in motor neuronal progenitors functions cell autonomously to cause spinal muscular atrophy in model mice expressing the human centromeric (SMN2) gene.
Park GH; Maeno-Hikichi Y; Awano T; Landmesser LT; Monani UR
J Neurosci; 2010 Sep; 30(36):12005-19. PubMed ID: 20826664
[TBL] [Abstract][Full Text] [Related]
4. Improvement of neuromuscular synaptic phenotypes without enhanced survival and motor function in severe spinal muscular atrophy mice selectively rescued in motor neurons.
Paez-Colasante X; Seaberg B; Martinez TL; Kong L; Sumner CJ; Rimer M
PLoS One; 2013; 8(9):e75866. PubMed ID: 24086650
[TBL] [Abstract][Full Text] [Related]
5. Peripheral SMN restoration is essential for long-term rescue of a severe spinal muscular atrophy mouse model.
Hua Y; Sahashi K; Rigo F; Hung G; Horev G; Bennett CF; Krainer AR
Nature; 2011 Oct; 478(7367):123-6. PubMed ID: 21979052
[TBL] [Abstract][Full Text] [Related]
6. Hyperexcitability precedes motoneuron loss in the
Quinlan KA; Reedich EJ; Arnold WD; Puritz AC; Cavarsan CF; Heckman CJ; DiDonato CJ
J Neurophysiol; 2019 Oct; 122(4):1297-1311. PubMed ID: 31365319
[TBL] [Abstract][Full Text] [Related]
7. Calpain Inhibition Increases SMN Protein in Spinal Cord Motoneurons and Ameliorates the Spinal Muscular Atrophy Phenotype in Mice.
de la Fuente S; Sansa A; Periyakaruppiah A; Garcera A; Soler RM
Mol Neurobiol; 2019 Jun; 56(6):4414-4427. PubMed ID: 30327977
[TBL] [Abstract][Full Text] [Related]
8. Selective loss of alpha motor neurons with sparing of gamma motor neurons and spinal cord cholinergic neurons in a mouse model of spinal muscular atrophy.
Powis RA; Gillingwater TH
J Anat; 2016 Mar; 228(3):443-51. PubMed ID: 26576026
[TBL] [Abstract][Full Text] [Related]
9. Survival motor neuron protein in motor neurons determines synaptic integrity in spinal muscular atrophy.
Martinez TL; Kong L; Wang X; Osborne MA; Crowder ME; Van Meerbeke JP; Xu X; Davis C; Wooley J; Goldhamer DJ; Lutz CM; Rich MM; Sumner CJ
J Neurosci; 2012 Jun; 32(25):8703-15. PubMed ID: 22723710
[TBL] [Abstract][Full Text] [Related]
10. Glial Activation and Central Synapse Loss, but Not Motoneuron Degeneration, Are Prevented by the Sigma-1 Receptor Agonist PRE-084 in the Smn2B/- Mouse Model of Spinal Muscular Atrophy.
Cerveró C; Blasco A; Tarabal O; Casanovas A; Piedrafita L; Navarro X; Esquerda JE; Calderó J
J Neuropathol Exp Neurol; 2018 Jul; 77(7):577-597. PubMed ID: 29767748
[TBL] [Abstract][Full Text] [Related]
11. Limited phenotypic effects of selectively augmenting the SMN protein in the neurons of a mouse model of severe spinal muscular atrophy.
Lee AJ; Awano T; Park GH; Monani UR
PLoS One; 2012; 7(9):e46353. PubMed ID: 23029491
[TBL] [Abstract][Full Text] [Related]
12. Plastin 3 ameliorates spinal muscular atrophy via delayed axon pruning and improves neuromuscular junction functionality.
Ackermann B; Kröber S; Torres-Benito L; Borgmann A; Peters M; Hosseini Barkooie SM; Tejero R; Jakubik M; Schreml J; Milbradt J; Wunderlich TF; Riessland M; Tabares L; Wirth B
Hum Mol Genet; 2013 Apr; 22(7):1328-47. PubMed ID: 23263861
[TBL] [Abstract][Full Text] [Related]
13. Stasimon Contributes to the Loss of Sensory Synapses and Motor Neuron Death in a Mouse Model of Spinal Muscular Atrophy.
Simon CM; Van Alstyne M; Lotti F; Bianchetti E; Tisdale S; Watterson DM; Mentis GZ; Pellizzoni L
Cell Rep; 2019 Dec; 29(12):3885-3901.e5. PubMed ID: 31851921
[TBL] [Abstract][Full Text] [Related]
14. Mechanisms involved in spinal cord central synapse loss in a mouse model of spinal muscular atrophy.
Tarabal O; Caraballo-Miralles V; Cardona-Rossinyol A; Correa FJ; Olmos G; Lladó J; Esquerda JE; Calderó J
J Neuropathol Exp Neurol; 2014 Jun; 73(6):519-35. PubMed ID: 24806302
[TBL] [Abstract][Full Text] [Related]
15. Activation of Muscle-Specific Kinase (MuSK) Reduces Neuromuscular Defects in the Delta7 Mouse Model of Spinal Muscular Atrophy (SMA).
Feng Z; Lam S; Tenn ES; Ghosh AS; Cantor S; Zhang W; Yen PF; Chen KS; Burden S; Paushkin S; Ayalon G; Ko CP
Int J Mol Sci; 2021 Jul; 22(15):. PubMed ID: 34360794
[TBL] [Abstract][Full Text] [Related]
16. Chronic Pharmacological Increase of Neuronal Activity Improves Sensory-Motor Dysfunction in Spinal Muscular Atrophy Mice.
Simon CM; Blanco-Redondo B; Buettner JM; Pagiazitis JG; Fletcher EV; Sime Longang JK; Mentis GZ
J Neurosci; 2021 Jan; 41(2):376-389. PubMed ID: 33219005
[TBL] [Abstract][Full Text] [Related]
17. Chronic treatment with lithium does not improve neuromuscular phenotype in a mouse model of severe spinal muscular atrophy.
Dachs E; Piedrafita L; Hereu M; Esquerda JE; Calderó J
Neuroscience; 2013 Oct; 250():417-33. PubMed ID: 23876328
[TBL] [Abstract][Full Text] [Related]
18. Reduced P53 levels ameliorate neuromuscular junction loss without affecting motor neuron pathology in a mouse model of spinal muscular atrophy.
Courtney NL; Mole AJ; Thomson AK; Murray LM
Cell Death Dis; 2019 Jul; 10(7):515. PubMed ID: 31273192
[TBL] [Abstract][Full Text] [Related]
19. Calpain system is altered in survival motor neuron-reduced cells from in vitro and in vivo spinal muscular atrophy models.
de la Fuente S; Sansa A; Hidalgo I; Vivancos N; Romero-Guevara R; Garcera A; Soler RM
Cell Death Dis; 2020 Jun; 11(6):487. PubMed ID: 32587237
[TBL] [Abstract][Full Text] [Related]
20. Sensory neurons do not induce motor neuron loss in a human stem cell model of spinal muscular atrophy.
Schwab AJ; Ebert AD
PLoS One; 2014; 9(7):e103112. PubMed ID: 25054590
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]
