204 related articles for article (PubMed ID: 22761419)
21. Puromycin-sensitive aminopeptidase protects against aggregation-prone proteins via autophagy.
Menzies FM; Hourez R; Imarisio S; Raspe M; Sadiq O; Chandraratna D; O'Kane C; Rock KL; Reits E; Goldberg AL; Rubinsztein DC
Hum Mol Genet; 2010 Dec; 19(23):4573-86. PubMed ID: 20829225
[TBL] [Abstract][Full Text] [Related]
22. Ataxin-3 consolidates the MDC1-dependent DNA double-strand break response by counteracting the SUMO-targeted ubiquitin ligase RNF4.
Pfeiffer A; Luijsterburg MS; Acs K; Wiegant WW; Helfricht A; Herzog LK; Minoia M; Böttcher C; Salomons FA; van Attikum H; Dantuma NP
EMBO J; 2017 Apr; 36(8):1066-1083. PubMed ID: 28275011
[TBL] [Abstract][Full Text] [Related]
23. CHIP protects from the neurotoxicity of expanded and wild-type ataxin-1 and promotes their ubiquitination and degradation.
Al-Ramahi I; Lam YC; Chen HK; de Gouyon B; Zhang M; Pérez AM; Branco J; de Haro M; Patterson C; Zoghbi HY; Botas J
J Biol Chem; 2006 Sep; 281(36):26714-24. PubMed ID: 16831871
[TBL] [Abstract][Full Text] [Related]
24. [Polyglutamine-expanded ataxin-3 is degraded by autophagy].
Xiao H; Tang J; Hu Z; Tan J; Tang B; Jiang Z
Zhonghua Yi Xue Yi Chuan Xue Za Zhi; 2010 Feb; 27(1):23-8. PubMed ID: 20140862
[TBL] [Abstract][Full Text] [Related]
25. SUMO-1 modification on K166 of polyQ-expanded ataxin-3 strengthens its stability and increases its cytotoxicity.
Zhou YF; Liao SS; Luo YY; Tang JG; Wang JL; Lei LF; Chi JW; Du J; Jiang H; Xia K; Tang BS; Shen L
PLoS One; 2013; 8(1):e54214. PubMed ID: 23382880
[TBL] [Abstract][Full Text] [Related]
26. Overexpressed wild-type superoxide dismutase 1 exhibits amyotrophic lateral sclerosis-related misfolded conformation in induced pluripotent stem cell-derived spinal motor neurons.
Komatsu K; Imamura K; Yamashita H; Julien JP; Takahashi R; Inoue H
Neuroreport; 2018 Jan; 29(1):25-29. PubMed ID: 29140847
[TBL] [Abstract][Full Text] [Related]
27. Proteasomal inhibition by misfolded mutant superoxide dismutase 1 induces selective motor neuron death in familial amyotrophic lateral sclerosis.
Urushitani M; Kurisu J; Tsukita K; Takahashi R
J Neurochem; 2002 Dec; 83(5):1030-42. PubMed ID: 12437574
[TBL] [Abstract][Full Text] [Related]
28. Crystal structure of a Josephin-ubiquitin complex: evolutionary restraints on ataxin-3 deubiquitinating activity.
Weeks SD; Grasty KC; Hernandez-Cuebas L; Loll PJ
J Biol Chem; 2011 Feb; 286(6):4555-65. PubMed ID: 21118805
[TBL] [Abstract][Full Text] [Related]
29. Striatal and nigral pathology in a lentiviral rat model of Machado-Joseph disease.
Alves S; Régulier E; Nascimento-Ferreira I; Hassig R; Dufour N; Koeppen A; Carvalho AL; Simões S; de Lima MC; Brouillet E; Gould VC; Déglon N; de Almeida LP
Hum Mol Genet; 2008 Jul; 17(14):2071-83. PubMed ID: 18385100
[TBL] [Abstract][Full Text] [Related]
30. Superoxide dismutase 1 mutants related to amyotrophic lateral sclerosis induce endoplasmic stress in neuro2a cells.
Oh YK; Shin KS; Yuan J; Kang SJ
J Neurochem; 2008 Feb; 104(4):993-1005. PubMed ID: 18233996
[TBL] [Abstract][Full Text] [Related]
31. Bid Promotes K63-Linked Polyubiquitination of Tumor Necrosis Factor Receptor Associated Factor 6 (TRAF6) and Sensitizes to Mutant SOD1-Induced Proinflammatory Signaling in Microglia.
Kinsella S; König HG; Prehn JH
eNeuro; 2016; 3(2):. PubMed ID: 27257617
[TBL] [Abstract][Full Text] [Related]
32. Ataxin-3 deubiquitination is coupled to Parkin ubiquitination via E2 ubiquitin-conjugating enzyme.
Durcan TM; Kontogiannea M; Bedard N; Wing SS; Fon EA
J Biol Chem; 2012 Jan; 287(1):531-541. PubMed ID: 22081612
[TBL] [Abstract][Full Text] [Related]
33. Calpain inhibition is sufficient to suppress aggregation of polyglutamine-expanded ataxin-3.
Haacke A; Hartl FU; Breuer P
J Biol Chem; 2007 Jun; 282(26):18851-6. PubMed ID: 17488727
[TBL] [Abstract][Full Text] [Related]
34. Ubiquitin ligase ITCH recruitment suppresses the aggregation and cellular toxicity of cytoplasmic misfolded proteins.
Chhangani D; Upadhyay A; Amanullah A; Joshi V; Mishra A
Sci Rep; 2014 May; 4():5077. PubMed ID: 24865853
[TBL] [Abstract][Full Text] [Related]
35. Wild-type Cu/Zn superoxide dismutase stabilizes mutant variants by heterodimerization.
Weichert A; Besemer AS; Liebl M; Hellmann N; Koziollek-Drechsler I; Ip P; Decker H; Robertson J; Chakrabartty A; Behl C; Clement AM
Neurobiol Dis; 2014 Feb; 62():479-88. PubMed ID: 24200866
[TBL] [Abstract][Full Text] [Related]
36. Ataxin-3 protein modification as a treatment strategy for spinocerebellar ataxia type 3: removal of the CAG containing exon.
Evers MM; Tran HD; Zalachoras I; Pepers BA; Meijer OC; den Dunnen JT; van Ommen GJ; Aartsma-Rus A; van Roon-Mom WM
Neurobiol Dis; 2013 Oct; 58():49-56. PubMed ID: 23659897
[TBL] [Abstract][Full Text] [Related]
37. Nuclear localization of ataxin-3 is required for the manifestation of symptoms in SCA3: in vivo evidence.
Bichelmeier U; Schmidt T; Hübener J; Boy J; Rüttiger L; Häbig K; Poths S; Bonin M; Knipper M; Schmidt WJ; Wilbertz J; Wolburg H; Laccone F; Riess O
J Neurosci; 2007 Jul; 27(28):7418-28. PubMed ID: 17626202
[TBL] [Abstract][Full Text] [Related]
38. Macrophage migration inhibitory factor as a chaperone inhibiting accumulation of misfolded SOD1.
Israelson A; Ditsworth D; Sun S; Song S; Liang J; Hruska-Plochan M; McAlonis-Downes M; Abu-Hamad S; Zoltsman G; Shani T; Maldonado M; Bui A; Navarro M; Zhou H; Marsala M; Kaspar BK; Da Cruz S; Cleveland DW
Neuron; 2015 Apr; 86(1):218-32. PubMed ID: 25801706
[TBL] [Abstract][Full Text] [Related]
39. Regulation of retrotranslocation by p97-associated deubiquitinating enzyme ataxin-3.
Wang Q; Li L; Ye Y
J Cell Biol; 2006 Sep; 174(7):963-71. PubMed ID: 17000876
[TBL] [Abstract][Full Text] [Related]
40. A mutant ataxin-3 fragment results from processing at a site N-terminal to amino acid 190 in brain of Machado-Joseph disease-like transgenic mice.
Colomer Gould VF; Goti D; Pearce D; Gonzalez GA; Gao H; Bermudez de Leon M; Jenkins NA; Copeland NG; Ross CA; Brown DR
Neurobiol Dis; 2007 Sep; 27(3):362-9. PubMed ID: 17632007
[TBL] [Abstract][Full Text] [Related]
[Previous] [Next] [New Search]