These tools will no longer be maintained as of December 31, 2024. Archived website can be found here. PubMed4Hh GitHub repository can be found here. Contact NLM Customer Service if you have questions.
6. Twinkle mutations associated with autosomal dominant progressive external ophthalmoplegia lead to impaired helicase function and in vivo mtDNA replication stalling. Goffart S; Cooper HM; Tyynismaa H; Wanrooij S; Suomalainen A; Spelbrink JN Hum Mol Genet; 2009 Jan; 18(2):328-40. PubMed ID: 18971204 [TBL] [Abstract][Full Text] [Related]
7. TWINKLE is an essential mitochondrial helicase required for synthesis of nascent D-loop strands and complete mtDNA replication. Milenkovic D; Matic S; Kühl I; Ruzzenente B; Freyer C; Jemt E; Park CB; Falkenberg M; Larsson NG Hum Mol Genet; 2013 May; 22(10):1983-93. PubMed ID: 23393161 [TBL] [Abstract][Full Text] [Related]
8. Lack of Parkin Anticipates the Phenotype and Affects Mitochondrial Morphology and mtDNA Levels in a Mouse Model of Parkinson's Disease. Pinto M; Nissanka N; Moraes CT J Neurosci; 2018 Jan; 38(4):1042-1053. PubMed ID: 29222404 [No Abstract] [Full Text] [Related]
9. Preserved striatal innervation maintains motor function despite severe loss of nigral dopaminergic neurons. Paß T; Ricke KM; Hofmann P; Chowdhury RS; Nie Y; Chinnery P; Endepols H; Neumaier B; Carvalho A; Rigoux L; Steculorum SM; Prudent J; Riemer T; Aswendt M; Liss B; Brachvogel B; Wiesner RJ Brain; 2024 Sep; 147(9):3189-3203. PubMed ID: 38574200 [TBL] [Abstract][Full Text] [Related]
10. Progressive nigrostriatal terminal dysfunction and degeneration in the engrailed1 heterozygous mouse model of Parkinson's disease. Nordströma U; Beauvais G; Ghosh A; Pulikkaparambil Sasidharan BC; Lundblad M; Fuchs J; Joshi RL; Lipton JW; Roholt A; Medicetty S; Feinstein TN; Steiner JA; Escobar Galvis ML; Prochiantz A; Brundin P Neurobiol Dis; 2015 Jan; 73():70-82. PubMed ID: 25281317 [TBL] [Abstract][Full Text] [Related]
11. Parkin deficiency exacerbate ethanol-induced dopaminergic neurodegeneration by P38 pathway dependent inhibition of autophagy and mitochondrial function. Hwang CJ; Kim YE; Son DJ; Park MH; Choi DY; Park PH; Hellström M; Han SB; Oh KW; Park EK; Hong JT Redox Biol; 2017 Apr; 11():456-468. PubMed ID: 28086194 [TBL] [Abstract][Full Text] [Related]
12. Mitochondrial DNA deletions/rearrangements in parkinson disease and related neurodegenerative disorders. Gu G; Reyes PE; Golden GT; Woltjer RL; Hulette C; Montine TJ; Zhang J J Neuropathol Exp Neurol; 2002 Jul; 61(7):634-9. PubMed ID: 12125742 [TBL] [Abstract][Full Text] [Related]
13. Overexpression of TFAM or twinkle increases mtDNA copy number and facilitates cardioprotection associated with limited mitochondrial oxidative stress. Ikeda M; Ide T; Fujino T; Arai S; Saku K; Kakino T; Tyynismaa H; Yamasaki T; Yamada K; Kang D; Suomalainen A; Sunagawa K PLoS One; 2015; 10(3):e0119687. PubMed ID: 25822152 [TBL] [Abstract][Full Text] [Related]
14. Mutant mitochondrial helicase Twinkle causes multiple mtDNA deletions and a late-onset mitochondrial disease in mice. Tyynismaa H; Mjosund KP; Wanrooij S; Lappalainen I; Ylikallio E; Jalanko A; Spelbrink JN; Paetau A; Suomalainen A Proc Natl Acad Sci U S A; 2005 Dec; 102(49):17687-92. PubMed ID: 16301523 [TBL] [Abstract][Full Text] [Related]
15. Trib3 Is Elevated in Parkinson's Disease and Mediates Death in Parkinson's Disease Models. Aimé P; Sun X; Zareen N; Rao A; Berman Z; Volpicelli-Daley L; Bernd P; Crary JF; Levy OA; Greene LA J Neurosci; 2015 Jul; 35(30):10731-49. PubMed ID: 26224857 [TBL] [Abstract][Full Text] [Related]
17. PARK14 (D331Y) PLA2G6 Causes Early-Onset Degeneration of Substantia Nigra Dopaminergic Neurons by Inducing Mitochondrial Dysfunction, ER Stress, Mitophagy Impairment and Transcriptional Dysregulation in a Knockin Mouse Model. Chiu CC; Lu CS; Weng YH; Chen YL; Huang YZ; Chen RS; Cheng YC; Huang YC; Liu YC; Lai SC; Lin KJ; Lin YW; Chen YJ; Chen CL; Yeh TH; Wang HL Mol Neurobiol; 2019 Jun; 56(6):3835-3853. PubMed ID: 30088174 [TBL] [Abstract][Full Text] [Related]
18. Dysregulation of parkin in the substantia nigra of db/db and high-fat diet mice. Khang R; Park C; Shin JH Neuroscience; 2015 May; 294():182-92. PubMed ID: 25779963 [TBL] [Abstract][Full Text] [Related]
19. The Absence of Parkin Does Not Promote Dopamine or Mitochondrial Dysfunction in PolgA Scott L; Karuppagounder SS; Neifert S; Kang BG; Wang H; Dawson VL; Dawson TM J Neurosci; 2022 Dec; 42(49):9263-9277. PubMed ID: 36280265 [TBL] [Abstract][Full Text] [Related]
20. Detrimental effects of oxidative losses in parkin activity in a model of sporadic Parkinson's disease are attenuated by restoration of PGC1alpha. Siddiqui A; Rane A; Rajagopalan S; Chinta SJ; Andersen JK Neurobiol Dis; 2016 Sep; 93():115-20. PubMed ID: 27185595 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]