134 related articles for article (PubMed ID: 2302222)
1. Galactosylceramide and galactosylsphingosine loading studies in cultured skin fibroblasts in human and murine globoid cell leukodystrophy.
Ida H; Kusano K; Suzuki H; Tokoro T; Eto Y
Biochem Biophys Res Commun; 1990 Jan; 166(2):1053-60. PubMed ID: 2302222
[TBL] [Abstract][Full Text] [Related]
2. Infantile and fetal globoid cell leukodystrophy: analysis of galactosylceramide and galactosylsphingosine.
Kobayashi T; Goto I; Yamanaka T; Suzuki Y; Nakano T; Suzuki K
Ann Neurol; 1988 Oct; 24(4):517-22. PubMed ID: 3239954
[TBL] [Abstract][Full Text] [Related]
3. Study of pathogenesis in twitcher mouse, an enzymatically authentic model of Krabbe's disease.
Inui K; Nishimoto J; Taniike M; Midorikawa M; Tsukamoto H; Okada S; Yabuuchi H
J Neurol Sci; 1990 Dec; 100(1-2):124-30. PubMed ID: 2128519
[TBL] [Abstract][Full Text] [Related]
4. Globoid cell leukodystrophy (Krabbe's disease). Metabolic studies with cultured fibroblasts.
Tanaka H; Suzuki K
J Neurol Sci; 1978 Oct; 38(3):409-19. PubMed ID: 731265
[TBL] [Abstract][Full Text] [Related]
5. The effects of psychosine upon growth of human skin fibroblasts from patients with globoid cell leukodystrophy.
Dickerman LH; Kurczynski TW; Macbride RG
J Neurol Sci; 1981 May; 50(2):181-90. PubMed ID: 7229663
[TBL] [Abstract][Full Text] [Related]
6. Hematopoietic cell transplantation in murine globoid cell leukodystrophy (the twitcher mouse): effects on levels of galactosylceramidase, psychosine, and galactocerebrosides.
Ichioka T; Kishimoto Y; Brennan S; Santos GW; Yeager AM
Proc Natl Acad Sci U S A; 1987 Jun; 84(12):4259-63. PubMed ID: 2884662
[TBL] [Abstract][Full Text] [Related]
7. Metabolism of cerebroside sulfate and subcellular distribution of its metabolites in cultured skin fibroblasts from controls, metachromatic leukodystrophy, and globoid cell leukodystrophy.
Inui K; Furukawa M; Okada S; Yabuuchi H
J Clin Invest; 1988 Feb; 81(2):310-7. PubMed ID: 3339122
[TBL] [Abstract][Full Text] [Related]
8. Metabolism of galactosylceramide in the twitcher mouse, an animal model of human globoid cell leukodystrophy.
Kobayashi T; Shinnoh N; Kuroiwa Y
Biochim Biophys Acta; 1986 Nov; 879(2):215-20. PubMed ID: 3094585
[TBL] [Abstract][Full Text] [Related]
9. Hydrolysis of galactosylceramide is catalyzed by two genetically distinct acid beta-galactosidases.
Kobayashi T; Shinnoh N; Goto I; Kuroiwa Y
J Biol Chem; 1985 Dec; 260(28):14982-7. PubMed ID: 3934152
[TBL] [Abstract][Full Text] [Related]
10. Globoid cell leukodystrophy is a generalized galactosylsphingosine (psychosine) storage disease.
Kobayashi T; Shinoda H; Goto I; Yamanaka T; Suzuki Y
Biochem Biophys Res Commun; 1987 Apr; 144(1):41-6. PubMed ID: 3579916
[TBL] [Abstract][Full Text] [Related]
11. Galactosylceramide- and lactosylceramide-loading studies in cultured fibroblasts from normal individuals and patients with globoid cell leukodystrophy (Krabbe's disease) and GM1-gangliosidosis.
Kobayashi T; Shinnoh N; Goto I; Kuroiwa Y; Okawauchi M; Sugihara G; Tanaka M
Biochim Biophys Acta; 1985 Jul; 835(3):456-64. PubMed ID: 3926002
[TBL] [Abstract][Full Text] [Related]
12. Biochemical pathogenesis of demyelination in globoid cell leukodystrophy (Krabbe's disease): the effects of psychosine upon oligodendroglial cell culture.
Ida H; Eto Y; Maekawa K
Acta Paediatr Jpn; 1990 Feb; 32(1):20-6. PubMed ID: 2109485
[TBL] [Abstract][Full Text] [Related]
13. Metabolism of cerebroside sulphate and subcellular distribution of its metabolites in cultured skin fibroblasts derived from controls, metachromatic leukodystrophy, globoid cell leukodystrophy and Farber disease.
Inui K; Furukawa M; Nishimoto J; Okada S; Yabuuchi H
J Inherit Metab Dis; 1987; 10(3):293-6. PubMed ID: 3123795
[No Abstract] [Full Text] [Related]
14. Sphingolipid profile in the CNS of the twitcher (globoid cell leukodystrophy) mouse: a lipidomics approach.
Esch SW; Williams TD; Biswas S; Chakrabarty A; LeVine SM
Cell Mol Biol (Noisy-le-grand); 2003 Jul; 49(5):779-87. PubMed ID: 14528915
[TBL] [Abstract][Full Text] [Related]
15. [The origin of renal galactosylceramide in the twitcher mouse, an animal model of human globoid cell leukodystrophy].
Katayama M
Fukuoka Igaku Zasshi; 1988 Jul; 79(7):529-36. PubMed ID: 3235022
[No Abstract] [Full Text] [Related]
16. Chemical pathology of Krabbe disease: the occurrence of psychosine and other neutral sphingoglycolipids.
Vanier M; Svennerholm L
Adv Exp Med Biol; 1976; 68():115-26. PubMed ID: 937104
[No Abstract] [Full Text] [Related]
17. Aberrant production of tenascin-C in globoid cell leukodystrophy alters psychosine-induced microglial functions.
Claycomb KI; Winokur PN; Johnson KM; Nicaise AM; Giampetruzzi AW; Sacino AV; Snyder EY; Barbarese E; Bongarzone ER; Crocker SJ
J Neuropathol Exp Neurol; 2014 Oct; 73(10):964-74. PubMed ID: 25192051
[TBL] [Abstract][Full Text] [Related]
18. Saposins (sap) A and C activate the degradation of galactosylsphingosine.
Harzer K; Hiraiwa M; Paton BC
FEBS Lett; 2001 Nov; 508(1):107-10. PubMed ID: 11707278
[TBL] [Abstract][Full Text] [Related]
19. Progressive accumulation of toxic metabolite in a genetic leukodystrophy.
Igisu H; Suzuki K
Science; 1984 May; 224(4650):753-5. PubMed ID: 6719111
[TBL] [Abstract][Full Text] [Related]
20. Krabbe disease: a galactosylsphingosine (psychosine) lipidosis.
Svennerholm L; Vanier MT; Månsson JE
J Lipid Res; 1980 Jan; 21(1):53-64. PubMed ID: 7354254
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]
