These tools will no longer be maintained as of December 31, 2024. Archived website can be found here. PubMed4Hh GitHub repository can be found here. Contact NLM Customer Service if you have questions.


BIOMARKERS

Molecular Biopsy of Human Tumors

- a resource for Precision Medicine *

161 related articles for article (PubMed ID: 23049915)

  • 1. Peripheral nervous system neuropathology and progressive sensory impairments in a mouse model of Mucopolysaccharidosis IIIB.
    Fu H; Bartz JD; Stephens RL; McCarty DM
    PLoS One; 2012; 7(9):e45992. PubMed ID: 23049915
    [TBL] [Abstract][Full Text] [Related]  

  • 2. Neuropathology in mouse models of mucopolysaccharidosis type I, IIIA and IIIB.
    Wilkinson FL; Holley RJ; Langford-Smith KJ; Badrinath S; Liao A; Langford-Smith A; Cooper JD; Jones SA; Wraith JE; Wynn RF; Merry CL; Bigger BW
    PLoS One; 2012; 7(4):e35787. PubMed ID: 22558223
    [TBL] [Abstract][Full Text] [Related]  

  • 3. Restoration of central nervous system alpha-N-acetylglucosaminidase activity and therapeutic benefits in mucopolysaccharidosis IIIB mice by a single intracisternal recombinant adeno-associated viral type 2 vector delivery.
    Fu H; DiRosario J; Kang L; Muenzer J; McCarty DM
    J Gene Med; 2010 Jul; 12(7):624-33. PubMed ID: 20603889
    [TBL] [Abstract][Full Text] [Related]  

  • 4. Central nervous system pathology in preclinical MPS IIIB dogs reveals progressive changes in clinically relevant brain regions.
    Egeland MT; Tarczyluk-Wells MM; Asmar MM; Adintori EG; Lawrence R; Snella EM; Jens JK; Crawford BE; Wait JCM; McCullagh E; Pinkstaff J; Cooper JD; Ellinwood NM
    Sci Rep; 2020 Nov; 10(1):20365. PubMed ID: 33230178
    [TBL] [Abstract][Full Text] [Related]  

  • 5. Accelerated clinical disease and pathology in mucopolysaccharidosis type IIIB and GalNAc transferase double knockout mice.
    Mohammed EE; Snella EM; Rutz-Mendicino MM; Echevarria FD; Awedikian R; Whitley EM; Ellinwood NM
    Mol Genet Metab; 2012 Sep; 107(1-2):129-35. PubMed ID: 22867887
    [TBL] [Abstract][Full Text] [Related]  

  • 6. A model of mucopolysaccharidosis IIIB (Sanfilippo syndrome type IIIB): N-acetyl-alpha-D-glucosaminidase deficiency in Schipperke dogs.
    Ellinwood NM; Wang P; Skeen T; Sharp NJ; Cesta M; Decker S; Edwards NJ; Bublot I; Thompson JN; Bush W; Hardam E; Haskins ME; Giger U
    J Inherit Metab Dis; 2003; 26(5):489-504. PubMed ID: 14518829
    [TBL] [Abstract][Full Text] [Related]  

  • 7. Amyloidosis, synucleinopathy, and prion encephalopathy in a neuropathic lysosomal storage disease: the CNS-biomarker potential of peripheral blood.
    Naughton BJ; Duncan FJ; Murrey D; Ware T; Meadows A; McCarty DM; Fu H
    PLoS One; 2013; 8(11):e80142. PubMed ID: 24278249
    [TBL] [Abstract][Full Text] [Related]  

  • 8. Diversity of satellite glia in sympathetic and sensory ganglia.
    Mapps AA; Thomsen MB; Boehm E; Zhao H; Hattar S; Kuruvilla R
    Cell Rep; 2022 Feb; 38(5):110328. PubMed ID: 35108545
    [TBL] [Abstract][Full Text] [Related]  

  • 9. Mucopolysaccharidosis IIIB, a lysosomal storage disease, triggers a pathogenic CNS autoimmune response.
    Killedar S; Dirosario J; Divers E; Popovich PG; McCarty DM; Fu H
    J Neuroinflammation; 2010 Jul; 7():39. PubMed ID: 20637096
    [TBL] [Abstract][Full Text] [Related]  

  • 10. Differential distribution of heparan sulfate glycoforms and elevated expression of heparan sulfate biosynthetic enzyme genes in the brain of mucopolysaccharidosis IIIB mice.
    McCarty DM; DiRosario J; Gulaid K; Killedar S; Oosterhof A; van Kuppevelt TH; Martin PT; Fu H
    Metab Brain Dis; 2011 Mar; 26(1):9-19. PubMed ID: 21225451
    [TBL] [Abstract][Full Text] [Related]  

  • 11. Near-Complete Correction of Profound Metabolomic Impairments Corresponding to Functional Benefit in MPS IIIB Mice after IV rAAV9-hNAGLU Gene Delivery.
    Fu H; Meadows AS; Ware T; Mohney RP; McCarty DM
    Mol Ther; 2017 Mar; 25(3):792-802. PubMed ID: 28143737
    [TBL] [Abstract][Full Text] [Related]  

  • 12. Genistein reduces lysosomal storage in peripheral tissues of mucopolysaccharide IIIB mice.
    Malinowska M; Wilkinson FL; Bennett W; Langford-Smith KJ; O'Leary HA; Jakobkiewicz-Banecka J; Wynn R; Wraith JE; Wegrzyn G; Bigger BW
    Mol Genet Metab; 2009 Nov; 98(3):235-42. PubMed ID: 19632871
    [TBL] [Abstract][Full Text] [Related]  

  • 13. Correction of neurological disease of mucopolysaccharidosis IIIB in adult mice by rAAV9 trans-blood-brain barrier gene delivery.
    Fu H; Dirosario J; Killedar S; Zaraspe K; McCarty DM
    Mol Ther; 2011 Jun; 19(6):1025-33. PubMed ID: 21386820
    [TBL] [Abstract][Full Text] [Related]  

  • 14. Distribution of the adhesion molecules N-CAM and L1 on peripheral neurons and glia in adult rats.
    Mirsky R; Jessen KR; Schachner M; Goridis C
    J Neurocytol; 1986 Dec; 15(6):799-815. PubMed ID: 3819781
    [TBL] [Abstract][Full Text] [Related]  

  • 15. Serum global metabolomics profiling reveals profound metabolic impairments in patients with MPS IIIA and MPS IIIB.
    Fu H; Meadows AS; Pineda RJ; Mohney RP; Stirdivant S; McCarty DM
    Metab Brain Dis; 2017 Oct; 32(5):1403-1415. PubMed ID: 28382573
    [TBL] [Abstract][Full Text] [Related]  

  • 16. Temporospatial Development of Neuropathologic Findings in a Canine Model of Mucopolysaccharidosis IIIB.
    Harm TA; Hostetter SJ; Nenninger AS; Valentine BN; Ellinwood NM; Smith JD
    Vet Pathol; 2021 Jan; 58(1):205-222. PubMed ID: 33205707
    [TBL] [Abstract][Full Text] [Related]  

  • 17. Macrophage enzyme and reduced inflammation drive brain correction of mucopolysaccharidosis IIIB by stem cell gene therapy.
    Holley RJ; Ellison SM; Fil D; O'Leary C; McDermott J; Senthivel N; Langford-Smith AWW; Wilkinson FL; D'Souza Z; Parker H; Liao A; Rowlston S; Gleitz HFE; Kan SH; Dickson PI; Bigger BW
    Brain; 2018 Jan; 141(1):99-116. PubMed ID: 29186350
    [TBL] [Abstract][Full Text] [Related]  

  • 18. Competitive binding of extracellular accumulated heparan sulfate reduces lysosomal storage defects and triggers neuronal differentiation in a model of Mucopolysaccharidosis IIIB.
    De Pasquale V; Scerra G; Scarcella M; D'Agostino M; Pavone LM
    Biochim Biophys Acta Mol Cell Res; 2021 Oct; 1868(11):119113. PubMed ID: 34329663
    [TBL] [Abstract][Full Text] [Related]  

  • 19. Analysis of low affinity neurotrophin receptor (p75) expression in glia of the CNS-PNS transition zone following dorsal root transection.
    Gai WP; Zhou XF; Rush RA
    Neuropathol Appl Neurobiol; 1996 Oct; 22(5):434-9. PubMed ID: 8930955
    [TBL] [Abstract][Full Text] [Related]  

  • 20. Innate and adaptive immune activation in the brain of MPS IIIB mouse model.
    DiRosario J; Divers E; Wang C; Etter J; Charrier A; Jukkola P; Auer H; Best V; Newsom DL; McCarty DM; Fu H
    J Neurosci Res; 2009 Mar; 87(4):978-90. PubMed ID: 18951493
    [TBL] [Abstract][Full Text] [Related]  

    [Next]    [New Search]
    of 9.