198 related articles for article (PubMed ID: 23180777)
1. Functional and histopathological identification of the respiratory failure in a DMSXL transgenic mouse model of myotonic dystrophy.
Panaite PA; Kuntzer T; Gourdon G; Lobrinus JA; Barakat-Walter I
Dis Model Mech; 2013 May; 6(3):622-31. PubMed ID: 23180777
[TBL] [Abstract][Full Text] [Related]
2. Myotonic dystrophy transgenic mice exhibit pathologic abnormalities in diaphragm neuromuscular junctions and phrenic nerves.
Panaite PA; Gantelet E; Kraftsik R; Gourdon G; Kuntzer T; Barakat-Walter I
J Neuropathol Exp Neurol; 2008 Aug; 67(8):763-72. PubMed ID: 18648326
[TBL] [Abstract][Full Text] [Related]
3. Peripheral neuropathy is linked to a severe form of myotonic dystrophy in transgenic mice.
Panaite PA; Kielar M; Kraftsik R; Gourdon G; Kuntzer T; Barakat-Walter I
J Neuropathol Exp Neurol; 2011 Aug; 70(8):678-85. PubMed ID: 21760538
[TBL] [Abstract][Full Text] [Related]
4. Respiratory failure in a mouse model of myotonic dystrophy does not correlate with the CTG repeat length.
Panaite PA; Kuntzer T; Gourdon G; Barakat-Walter I
Respir Physiol Neurobiol; 2013 Oct; 189(1):22-6. PubMed ID: 23811192
[TBL] [Abstract][Full Text] [Related]
5. Molecular, physiological, and motor performance defects in DMSXL mice carrying >1,000 CTG repeats from the human DM1 locus.
Huguet A; Medja F; Nicole A; Vignaud A; Guiraud-Dogan C; Ferry A; Decostre V; Hogrel JY; Metzger F; Hoeflich A; Baraibar M; Gomes-Pereira M; Puymirat J; Bassez G; Furling D; Munnich A; Gourdon G
PLoS Genet; 2012; 8(11):e1003043. PubMed ID: 23209425
[TBL] [Abstract][Full Text] [Related]
6. Degeneration of phrenic motor neurons induces long-term diaphragm deficits following mid-cervical spinal contusion in mice.
Nicaise C; Putatunda R; Hala TJ; Regan KA; Frank DM; Brion JP; Leroy K; Pochet R; Wright MC; Lepore AC
J Neurotrauma; 2012 Dec; 29(18):2748-60. PubMed ID: 23176637
[TBL] [Abstract][Full Text] [Related]
7. Abnormal sodium current properties contribute to cardiac electrical and contractile dysfunction in a mouse model of myotonic dystrophy type 1.
Algalarrondo V; Wahbi K; Sebag F; Gourdon G; Beldjord C; Azibi K; Balse E; Coulombe A; Fischmeister R; Eymard B; Duboc D; Hatem SN
Neuromuscul Disord; 2015 Apr; 25(4):308-20. PubMed ID: 25613807
[TBL] [Abstract][Full Text] [Related]
8. DM1 Transgenic Mice Exhibit Abnormal Neurotransmitter Homeostasis and Synaptic Plasticity in Association with RNA Foci and Mis-Splicing in the Hippocampus.
Potier B; Lallemant L; Parrot S; Huguet-Lachon A; Gourdon G; Dutar P; Gomes-Pereira M
Int J Mol Sci; 2022 Jan; 23(2):. PubMed ID: 35054778
[TBL] [Abstract][Full Text] [Related]
9. Enhanced Delivery of Ligand-Conjugated Antisense Oligonucleotides (C16-HA-ASO) Targeting Dystrophia Myotonica Protein Kinase Transcripts for the Treatment of Myotonic Dystrophy Type 1.
Ait Benichou S; Jauvin D; De Serres-Bérard T; Bennett F; Rigo F; Gourdon G; Boutjdir M; Chahine M; Puymirat J
Hum Gene Ther; 2022 Aug; 33(15-16):810-820. PubMed ID: 35794764
[TBL] [Abstract][Full Text] [Related]
10. Longitudinal in vivo muscle function analysis of the DMSXL mouse model of myotonic dystrophy type 1.
Decostre V; Vignaud A; Matot B; Huguet A; Ledoux I; Bertil E; Gjata B; Carlier PG; Gourdon G; Hogrel JY
Neuromuscul Disord; 2013 Dec; 23(12):1016-25. PubMed ID: 24139022
[TBL] [Abstract][Full Text] [Related]
11. The expansion of 300 CTG repeats in myotonic dystrophy transgenic mice does not induce sensory or motor neuropathy.
Gantelet E; Kraftsik R; Delaloye S; Gourdon G; Kuntzer T; Barakat-Walter I
Acta Neuropathol; 2007 Aug; 114(2):175-85. PubMed ID: 17318633
[TBL] [Abstract][Full Text] [Related]
12. Characteristics of respiratory muscle involvement in myotonic dystrophy type 1.
Henke C; Spiesshoefer J; Kabitz HJ; Herkenrath S; Randerath W; Brix T; Görlich D; Young P; Boentert M
Neuromuscul Disord; 2020 Jan; 30(1):17-27. PubMed ID: 31839403
[TBL] [Abstract][Full Text] [Related]
13. Integrative Cell Type-Specific Multi-Omics Approaches Reveal Impaired Programs of Glial Cell Differentiation in Mouse Culture Models of DM1.
González-Barriga A; Lallemant L; Dincã DM; Braz SO; Polvèche H; Magneron P; Pionneau C; Huguet-Lachon A; Claude JB; Chhuon C; Guerrera IC; Bourgeois CF; Auboeuf D; Gourdon G; Gomes-Pereira M
Front Cell Neurosci; 2021; 15():662035. PubMed ID: 34025359
[TBL] [Abstract][Full Text] [Related]
14. Phrenic motor neuron degeneration compromises phrenic axonal circuitry and diaphragm activity in a unilateral cervical contusion model of spinal cord injury.
Nicaise C; Hala TJ; Frank DM; Parker JL; Authelet M; Leroy K; Brion JP; Wright MC; Lepore AC
Exp Neurol; 2012 Jun; 235(2):539-52. PubMed ID: 22465264
[TBL] [Abstract][Full Text] [Related]
15. Central and peripheral respiratory electrophysiological studies in myotonic dystrophy.
Zifko UA; Hahn AF; Remtulla H; George CF; Wihlidal W; Bolton CF
Brain; 1996 Dec; 119 ( Pt 6)():1911-22. PubMed ID: 9009997
[TBL] [Abstract][Full Text] [Related]
16. A low absolute number of expanded transcripts is involved in myotonic dystrophy type 1 manifestation in muscle.
Gudde AE; González-Barriga A; van den Broek WJ; Wieringa B; Wansink DG
Hum Mol Genet; 2016 Apr; 25(8):1648-62. PubMed ID: 26908607
[TBL] [Abstract][Full Text] [Related]
17. Chronic exercise mitigates disease mechanisms and improves muscle function in myotonic dystrophy type 1 mice.
Manta A; Stouth DW; Xhuti D; Chi L; Rebalka IA; Kalmar JM; Hawke TJ; Ljubicic V
J Physiol; 2019 Mar; 597(5):1361-1381. PubMed ID: 30628727
[TBL] [Abstract][Full Text] [Related]
18. Sense and Antisense DMPK RNA Foci Accumulate in DM1 Tissues during Development.
Michel L; Huguet-Lachon A; Gourdon G
PLoS One; 2015; 10(9):e0137620. PubMed ID: 26339785
[TBL] [Abstract][Full Text] [Related]
19. Compensatory plasticity in diaphragm and intercostal muscle utilization in a rat model of ALS.
Seven YB; Nichols NL; Kelly MN; Hobson OR; Satriotomo I; Mitchell GS
Exp Neurol; 2018 Jan; 299(Pt A):148-156. PubMed ID: 29056361
[TBL] [Abstract][Full Text] [Related]
20. Excessive rest time during active phase is reliably detected in a mouse model of myotonic dystrophy type 1 using home cage monitoring.
Golini E; Rigamonti M; Raspa M; Scavizzi F; Falcone G; Gourdon G; Mandillo S
Front Behav Neurosci; 2023; 17():1130055. PubMed ID: 36935893
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]