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2. A systematic immunoprecipitation approach reinforces the concept of common conformational alterations in amyotrophic lateral sclerosis-linked SOD1 mutants. Fujisawa T; Yamaguchi N; Kadowaki H; Tsukamoto Y; Tsuburaya N; Tsubota A; Takahashi H; Naguro I; Takahashi Y; Goto J; Tsuji S; Nishitoh H; Homma K; Ichijo H Neurobiol Dis; 2015 Oct; 82():478-486. PubMed ID: 26297318 [TBL] [Abstract][Full Text] [Related]
3. Immunodetection of disease-associated conformers of mutant cu/zn superoxide dismutase 1 selectively expressed in degenerating neurons in amyotrophic lateral sclerosis. Sábado J; Casanovas A; Hernández S; Piedrafita L; Hereu M; Esquerda JE J Neuropathol Exp Neurol; 2013 Jul; 72(7):646-61. PubMed ID: 23771221 [TBL] [Abstract][Full Text] [Related]
4. Human Cu/Zn superoxide dismutase (SOD1) overexpression in mice causes mitochondrial vacuolization, axonal degeneration, and premature motoneuron death and accelerates motoneuron disease in mice expressing a familial amyotrophic lateral sclerosis mutant SOD1. Jaarsma D; Haasdijk ED; Grashorn JA; Hawkins R; van Duijn W; Verspaget HW; London J; Holstege JC Neurobiol Dis; 2000 Dec; 7(6 Pt B):623-43. PubMed ID: 11114261 [TBL] [Abstract][Full Text] [Related]
5. Neuregulin 1 confers neuroprotection in SOD1-linked amyotrophic lateral sclerosis mice via restoration of C-boutons of spinal motor neurons. Lasiene J; Komine O; Fujimori-Tonou N; Powers B; Endo F; Watanabe S; Shijie J; Ravits J; Horner P; Misawa H; Yamanaka K Acta Neuropathol Commun; 2016 Feb; 4():15. PubMed ID: 26891847 [TBL] [Abstract][Full Text] [Related]
6. A copper-deficient form of mutant Cu/Zn-superoxide dismutase as an early pathological species in amyotrophic lateral sclerosis. Tokuda E; Nomura T; Ohara S; Watanabe S; Yamanaka K; Morisaki Y; Misawa H; Furukawa Y Biochim Biophys Acta Mol Basis Dis; 2018 Jun; 1864(6 Pt A):2119-2130. PubMed ID: 29551730 [TBL] [Abstract][Full Text] [Related]
7. Intracellular conformational alterations of mutant SOD1 and the implications for fALS-associated SOD1 mutant induced motor neuron cell death. Zhang F; Zhu H Biochim Biophys Acta; 2006 Mar; 1760(3):404-14. PubMed ID: 16431026 [TBL] [Abstract][Full Text] [Related]
8. ALS-linked mutant SOD1 induces ER stress- and ASK1-dependent motor neuron death by targeting Derlin-1. Nishitoh H; Kadowaki H; Nagai A; Maruyama T; Yokota T; Fukutomi H; Noguchi T; Matsuzawa A; Takeda K; Ichijo H Genes Dev; 2008 Jun; 22(11):1451-64. PubMed ID: 18519638 [TBL] [Abstract][Full Text] [Related]
9. Chromogranin-mediated secretion of mutant superoxide dismutase proteins linked to amyotrophic lateral sclerosis. Urushitani M; Sik A; Sakurai T; Nukina N; Takahashi R; Julien JP Nat Neurosci; 2006 Jan; 9(1):108-18. PubMed ID: 16369483 [TBL] [Abstract][Full Text] [Related]
10. Amyotrophic lateral sclerosis-related mutant superoxide dismutase 1 aggregates inhibit 14-3-3-mediated cell survival by sequestration into the JUNQ compartment. Park JH; Jang HR; Lee IY; Oh HK; Choi EJ; Rhim H; Kang S Hum Mol Genet; 2017 Sep; 26(18):3615-3629. PubMed ID: 28666328 [TBL] [Abstract][Full Text] [Related]
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13. ALS mutant SOD1 interacts with G3BP1 and affects stress granule dynamics. Gal J; Kuang L; Barnett KR; Zhu BZ; Shissler SC; Korotkov KV; Hayward LJ; Kasarskis EJ; Zhu H Acta Neuropathol; 2016 Oct; 132(4):563-76. PubMed ID: 27481264 [TBL] [Abstract][Full Text] [Related]
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