These tools will no longer be maintained as of December 31, 2024. Archived website can be found here. PubMed4Hh GitHub repository can be found here. Contact NLM Customer Service if you have questions.
236 related articles for article (PubMed ID: 23591631)
21. Restoration of Functional Glycosylation of α-Dystroglycan in FKRP Mutant Mice Is Associated with Muscle Regeneration. Awano H; Blaeser A; Keramaris E; Xu L; Tucker J; Wu B; Lu P; Lu QL Am J Pathol; 2015 Jul; 185(7):2025-37. PubMed ID: 25976249 [TBL] [Abstract][Full Text] [Related]
22. AAV-mediated transfer of FKRP shows therapeutic efficacy in a murine model but requires control of gene expression. Gicquel E; Maizonnier N; Foltz SJ; Martin WJ; Bourg N; Svinartchouk F; Charton K; Beedle AM; Richard I Hum Mol Genet; 2017 May; 26(10):1952-1965. PubMed ID: 28334834 [TBL] [Abstract][Full Text] [Related]
23. Phenotypic Spectrum of α-Dystroglycanopathies Associated With the c.919T>a Variant in the FKRP Gene in Humans and Mice. Brown SC; Fernandez-Fuente M; Muntoni F; Vissing J J Neuropathol Exp Neurol; 2020 Dec; 79(12):1257-1264. PubMed ID: 33051673 [TBL] [Abstract][Full Text] [Related]
24. Post-Natal knockdown of fukutin-related protein expression in muscle by long-termRNA interference induces dystrophic pathology [corrected]. Wang CH; Chan YM; Tang RH; Xiao B; Lu P; Keramaris-Vrantsis E; Zheng H; Qiao C; Jiang J; Li J; Ma HI; Lu Q; Xiao X Am J Pathol; 2011 Jan; 178(1):261-72. PubMed ID: 21224063 [TBL] [Abstract][Full Text] [Related]
25. FKRP-dependent glycosylation of fibronectin regulates muscle pathology in muscular dystrophy. Wood AJ; Lin CH; Li M; Nishtala K; Alaei S; Rossello F; Sonntag C; Hersey L; Miles LB; Krisp C; Dudczig S; Fulcher AJ; Gibertini S; Conroy PJ; Siegel A; Mora M; Jusuf P; Packer NH; Currie PD Nat Commun; 2021 May; 12(1):2951. PubMed ID: 34012031 [TBL] [Abstract][Full Text] [Related]
26. Mutations in the fukutin-related protein gene (FKRP) identify limb girdle muscular dystrophy 2I as a milder allelic variant of congenital muscular dystrophy MDC1C. Brockington M; Yuva Y; Prandini P; Brown SC; Torelli S; Benson MA; Herrmann R; Anderson LV; Bashir R; Burgunder JM; Fallet S; Romero N; Fardeau M; Straub V; Storey G; Pollitt C; Richard I; Sewry CA; Bushby K; Voit T; Blake DJ; Muntoni F Hum Mol Genet; 2001 Dec; 10(25):2851-9. PubMed ID: 11741828 [TBL] [Abstract][Full Text] [Related]
27. Defective autophagy and increased apoptosis contribute toward the pathogenesis of FKRP-associated muscular dystrophies. Ortiz-Cordero C; Bincoletto C; Dhoke NR; Selvaraj S; Magli A; Zhou H; Kim DH; Bang AG; Perlingeiro RCR Stem Cell Reports; 2021 Nov; 16(11):2752-2767. PubMed ID: 34653404 [TBL] [Abstract][Full Text] [Related]
28. Elevated serum creatine kinase and small cerebellum prompt diagnosis of congenital muscular dystrophy due to FKRP mutations. Trovato R; Astrea G; Bartalena L; Ghirri P; Baldacci J; Giampietri M; Battini R; Santorelli FM; Fiorillo C J Child Neurol; 2014 Mar; 29(3):394-8. PubMed ID: 23420653 [TBL] [Abstract][Full Text] [Related]
29. [Recent advances in congenital muscular dystrophy research]. Nonaka I No To Hattatsu; 2005 Mar; 37(2):115-21. PubMed ID: 15773323 [TBL] [Abstract][Full Text] [Related]
30. Limb girdle muscular dystrophy type 2I: No correlation between clinical severity, histopathology and glycosylated α-dystroglycan levels in patients homozygous for common FKRP mutation. Alhamidi M; Brox V; Stensland E; Liset M; Lindal S; Nilssen Ø Neuromuscul Disord; 2017 Jul; 27(7):619-626. PubMed ID: 28479227 [TBL] [Abstract][Full Text] [Related]
31. Distinct expression of functionally glycosylated alpha-dystroglycan in muscle and non-muscle tissues of FKRP mutant mice. Blaeser A; Awano H; Lu P; Lu QL PLoS One; 2018; 13(1):e0191016. PubMed ID: 29320543 [TBL] [Abstract][Full Text] [Related]
32. Congenital muscular dystrophies with defective glycosylation of dystroglycan: a population study. Mercuri E; Messina S; Bruno C; Mora M; Pegoraro E; Comi GP; D'Amico A; Aiello C; Biancheri R; Berardinelli A; Boffi P; Cassandrini D; Laverda A; Moggio M; Morandi L; Moroni I; Pane M; Pezzani R; Pichiecchio A; Pini A; Minetti C; Mongini T; Mottarelli E; Ricci E; Ruggieri A; Saredi S; Scuderi C; Tessa A; Toscano A; Tortorella G; Trevisan CP; Uggetti C; Vasco G; Santorelli FM; Bertini E Neurology; 2009 May; 72(21):1802-9. PubMed ID: 19299310 [TBL] [Abstract][Full Text] [Related]
33. Fukutin-related protein alters the deposition of laminin in the eye and brain. Ackroyd MR; Whitmore C; Prior S; Kaluarachchi M; Nikolic M; Mayer U; Muntoni F; Brown SC J Neurosci; 2011 Sep; 31(36):12927-35. PubMed ID: 21900571 [TBL] [Abstract][Full Text] [Related]
34. Mutations alter secretion of fukutin-related protein. Lu PJ; Zillmer A; Wu X; Lochmuller H; Vachris J; Blake D; Chan YM; Lu QL Biochim Biophys Acta; 2010 Feb; 1802(2):253-8. PubMed ID: 19900540 [TBL] [Abstract][Full Text] [Related]
35. Prenatal muscle development in a mouse model for the secondary dystroglycanopathies. Kim J; Hopkinson M; Kavishwar M; Fernandez-Fuente M; Brown SC Skelet Muscle; 2016; 6():3. PubMed ID: 26900448 [TBL] [Abstract][Full Text] [Related]
36. The transgenic expression of LARGE exacerbates the muscle phenotype of dystroglycanopathy mice. Whitmore C; Fernandez-Fuente M; Booler H; Parr C; Kavishwar M; Ashraf A; Lacey E; Kim J; Terry R; Ackroyd MR; Wells KE; Muntoni F; Wells DJ; Brown SC Hum Mol Genet; 2014 Apr; 23(7):1842-55. PubMed ID: 24234655 [TBL] [Abstract][Full Text] [Related]
38. FKRP gene mutations cause congenital muscular dystrophy, mental retardation, and cerebellar cysts. Topaloglu H; Brockington M; Yuva Y; Talim B; Haliloglu G; Blake D; Torelli S; Brown SC; Muntoni F Neurology; 2003 Mar; 60(6):988-92. PubMed ID: 12654965 [TBL] [Abstract][Full Text] [Related]
39. Abnormalities in alpha-dystroglycan expression in MDC1C and LGMD2I muscular dystrophies. Brown SC; Torelli S; Brockington M; Yuva Y; Jimenez C; Feng L; Anderson L; Ugo I; Kroger S; Bushby K; Voit T; Sewry C; Muntoni F Am J Pathol; 2004 Feb; 164(2):727-37. PubMed ID: 14742276 [TBL] [Abstract][Full Text] [Related]
40. A homozygous FKRP start codon mutation is associated with Walker-Warburg syndrome, the severe end of the clinical spectrum. Van Reeuwijk J; Olderode-Berends MJ; Van den Elzen C; Brouwer OF; Roscioli T; Van Pampus MG; Scheffer H; Brunner HG; Van Bokhoven H; Hol FA Clin Genet; 2010 Sep; 78(3):275-81. PubMed ID: 20236121 [TBL] [Abstract][Full Text] [Related] [Previous] [Next] [New Search]