These tools will no longer be maintained as of December 31, 2024. Archived website can be found here. PubMed4Hh GitHub repository can be found here. Contact NLM Customer Service if you have questions.
23. A colorimetric assay for 7-dehydrocholesterol with potential application to screening for Smith-Lemli-Opitz syndrome. Xiong Q; Ruan B; Whitby FG; Tuohy RP; Belanger TL; Kelley RI; Wilson WK; Schroepfer GJ Chem Phys Lipids; 2002 May; 115(1-2):1-15. PubMed ID: 12047895 [TBL] [Abstract][Full Text] [Related]
24. Identification of three patients with a very mild form of Smith-Lemli-Opitz syndrome. Langius FA; Waterham HR; Romeijn GJ; Oostheim W; de Barse MM; Dorland L; Duran M; Beemer FA; Wanders RJ; Poll-The BT Am J Med Genet A; 2003 Sep; 122A(1):24-9. PubMed ID: 12949967 [TBL] [Abstract][Full Text] [Related]
25. Abnormal cholesterol biosynthesis as in Smith-Lemli-Opitz syndrome disrupts normal skeletal development in the rat. Kolf-Clauw M; Chevy F; Ponsart C J Lab Clin Med; 1998 Mar; 131(3):222-7. PubMed ID: 9523845 [TBL] [Abstract][Full Text] [Related]
26. Relation between biomarkers and clinical severity in patients with Smith-Lemli-Opitz syndrome. Oláh AV; Szabó GP; Varga J; Balogh L; Csábi G; Csákváry V; Erwa W; Balogh I Eur J Pediatr; 2013 May; 172(5):623-30. PubMed ID: 23319240 [TBL] [Abstract][Full Text] [Related]
27. Smith-Lemli-Opitz syndrome: new mutation with a mild phenotype. Prasad C; Marles S; Prasad AN; Nikkel S; Longstaffe S; Peabody D; Eng B; Wright S; Waye JS; Nowaczyk MJ Am J Med Genet; 2002 Feb; 108(1):64-8. PubMed ID: 11857552 [TBL] [Abstract][Full Text] [Related]
28. The p.Phe174Ser mutation is associated with mild forms of Smith Lemli Opitz Syndrome. Tucci A; Ronzoni L; Arduino C; Salmin P; Esposito S; Milani D BMC Med Genet; 2016 Mar; 17():22. PubMed ID: 26969503 [TBL] [Abstract][Full Text] [Related]
29. Prenatal diagnosis of the RSH/Smith-Lemli-Opitz syndrome. Kratz LE; Kelley RI Am J Med Genet; 1999 Feb; 82(5):376-81. PubMed ID: 10069707 [TBL] [Abstract][Full Text] [Related]
32. Two novel mutations of the human delta7-sterol reductase (DHCR7) gene in children with Smith-Lemli-Opitz syndrome. Patrono C; Dionisi-Vici C; Giannotti A; Bembi B; Digilio MC; Rizzo C; Purificato C; Martini C; Pierini R; Santorelli FM Mol Cell Probes; 2002 Aug; 16(4):315-8. PubMed ID: 12270273 [TBL] [Abstract][Full Text] [Related]
33. [Smith-Lemli-Opitz syndrome; a special defect in cholesterol metabolism]. Aalfs CM; Hennekam RC; Wanders RJ; Jira PE; Pilon JW; Wijburg FA Ned Tijdschr Geneeskd; 1996 Jul; 140(28):1463-6. PubMed ID: 8766772 [TBL] [Abstract][Full Text] [Related]
34. Molecular prenatal diagnosis of Smith-Lemli-Opitz syndrome is reliable and efficient. Loeffler J; Utermann G; Witsch-Baumgartner M Prenat Diagn; 2002 Sep; 22(9):827-30. PubMed ID: 12224080 [TBL] [Abstract][Full Text] [Related]
35. Photosensitive Smith-Lemli-Opitz syndrome is not caused by a single gene mutation: analysis of the gene encoding 7-dehydrocholesterol reductase in five U.K. families. Anstey AV; Azurdia RM; Rhodes LE; Pearse AD; Bowden PE Br J Dermatol; 2005 Oct; 153(4):774-9. PubMed ID: 16181459 [TBL] [Abstract][Full Text] [Related]
36. [Biochemical diagnosis of Smith-Lemli-Opitz syndrome in a patient with congenital adrenal hyperplasia]. GarcíaFuentes E; icioso Recio MV ; del Castillo Acedo Del Olmo E ; atas Jurado MM ; Arana Agüera M ; López López J An Esp Pediatr; 2000 Nov; 53(5):482-7. PubMed ID: 11141372 [TBL] [Abstract][Full Text] [Related]
37. A novel mutation of the DHCR7 gene in a sicilian compound heterozygote with Smith-Lemli-Opitz Syndrome. Romano F; Fiore B; Pezzino FM; Longombardo MT; Cefalù AB; Noto D; Puglisi A; Brogna A; Mattina T; Averna M; Travali S Mol Diagn; 2005; 9(4):201-4. PubMed ID: 16392899 [TBL] [Abstract][Full Text] [Related]
38. Founder effect for the T93M DHCR7 mutation in Smith-Lemli-Opitz syndrome. Nowaczyk MJ; Martin-Garcia D; Aquino-Perna A; Rodriguez-Vazquez M; McCaughey D; Eng B; Nakamura LM; Waye JS Am J Med Genet A; 2004 Mar; 125A(2):173-6. PubMed ID: 14981719 [TBL] [Abstract][Full Text] [Related]