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3. Clinical and radiographic features of the autosomal recessive form of brachyolmia caused by PAPSS2 mutations. Iida A; Simsek-Kiper PÖ; Mizumoto S; Hoshino T; Elcioglu N; Horemuzova E; Geiberger S; Yesil G; Kayserili H; Utine GE; Boduroglu K; Watanabe S; Ohashi H; Alanay Y; Sugahara K; Nishimura G; Ikegawa S Hum Mutat; 2013 Oct; 34(10):1381-6. PubMed ID: 23824674 [TBL] [Abstract][Full Text] [Related]
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5. PAPSS2 mutations cause autosomal recessive brachyolmia. Miyake N; Elcioglu NH; Iida A; Isguven P; Dai J; Murakami N; Takamura K; Cho TJ; Kim OH; Hasegawa T; Nagai T; Ohashi H; Nishimura G; Matsumoto N; Ikegawa S J Med Genet; 2012 Aug; 49(8):533-8. PubMed ID: 22791835 [TBL] [Abstract][Full Text] [Related]
6. Distinct, autosomal recessive form of spondyloepimetaphyseal dysplasia segregating in an inbred Pakistani kindred. Ahmad M; Faiyaz Ul Haque M; Ahmad W; Abbas H; Haque S; Krakow D; Rimoin DL; Lachman RS; Cohn DH Am J Med Genet; 1998 Aug; 78(5):468-73. PubMed ID: 9714015 [TBL] [Abstract][Full Text] [Related]
7. Exclusion of the dymeclin and PAPSS2 genes in a novel form of spondyloepimetaphyseal dysplasia and mental retardation. Geneviève D; Héron D; El Ghouzzi V; Prost-Squarcioni C; Le Merrer M; Jacquette A; Sanlaville D; Pinton F; Villeneuve N; Kalifa G; Munnich A; Cormier-Daire V Eur J Hum Genet; 2005 May; 13(5):541-6. PubMed ID: 15726110 [TBL] [Abstract][Full Text] [Related]
8. Short trunk stature, brachydactyly, and platyspondyly in three sibs: a new form of brachyolmia or a new skeletal dysplasia? Tüysüz B; Ungür S Am J Med Genet A; 2003 Jun; 119A(3):375-80. PubMed ID: 12784309 [TBL] [Abstract][Full Text] [Related]
9. PAPSS2 deficiency causes androgen excess via impaired DHEA sulfation--in vitro and in vivo studies in a family harboring two novel PAPSS2 mutations. Oostdijk W; Idkowiak J; Mueller JW; House PJ; Taylor AE; O'Reilly MW; Hughes BA; de Vries MC; Kant SG; Santen GW; Verkerk AJ; Uitterlinden AG; Wit JM; Losekoot M; Arlt W J Clin Endocrinol Metab; 2015 Apr; 100(4):E672-80. PubMed ID: 25594860 [TBL] [Abstract][Full Text] [Related]
10. Spondyloepimetaphyseal dysplasia (SEMD) Shohat type. Figuera LE; Ramírez-Dueñas ML; Gallegos-Arreola MP; Cantú JM Am J Med Genet; 1994 Jul; 51(3):213-5. PubMed ID: 8074146 [TBL] [Abstract][Full Text] [Related]
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12. Variants in SULT2A1 affect the DHEA sulphate to DHEA ratio in patients with polycystic ovary syndrome but not the hyperandrogenic phenotype. Louwers YV; de Jong FH; van Herwaarden NA; Stolk L; Fauser BC; Uitterlinden AG; Laven JS J Clin Endocrinol Metab; 2013 Sep; 98(9):3848-55. PubMed ID: 23861462 [TBL] [Abstract][Full Text] [Related]
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15. New form of spondyloepimetaphyseal dysplasia (SEMD) in Jewish family of Iraqi origin. Shohat M; Lachman R; Carmi R; Bar Ziv J; Rimoin D Am J Med Genet; 1993 Jun; 46(4):358-62. PubMed ID: 8357004 [TBL] [Abstract][Full Text] [Related]
16. Inactivating PAPSS2 mutations in a patient with premature pubarche. Noordam C; Dhir V; McNelis JC; Schlereth F; Hanley NA; Krone N; Smeitink JA; Smeets R; Sweep FC; Claahsen-van der Grinten HL; Arlt W N Engl J Med; 2009 May; 360(22):2310-8. PubMed ID: 19474428 [TBL] [Abstract][Full Text] [Related]
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19. The novel R211Q POP1 homozygous mutation causes different pathogenesis and skeletal changes from those of previously reported POP1-associated anauxetic dysplasia. Abdulhadi-Atwan M; Klopstock T; Sharaf M; Weinberg-Shukron A; Renbaum P; Levy-Lahad E; Zangen D Am J Med Genet A; 2020 May; 182(5):1268-1272. PubMed ID: 32134183 [TBL] [Abstract][Full Text] [Related]
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