266 related articles for article (PubMed ID: 23794606)
1. Pioglitazone halts axonal degeneration in a mouse model of X-linked adrenoleukodystrophy.
Morató L; Galino J; Ruiz M; Calingasan NY; Starkov AA; Dumont M; Naudí A; Martínez JJ; Aubourg P; Portero-Otín M; Pamplona R; Galea E; Beal MF; Ferrer I; Fourcade S; Pujol A
Brain; 2013 Aug; 136(Pt 8):2432-43. PubMed ID: 23794606
[TBL] [Abstract][Full Text] [Related]
2. Antioxidants halt axonal degeneration in a mouse model of X-adrenoleukodystrophy.
López-Erauskin J; Fourcade S; Galino J; Ruiz M; Schlüter A; Naudi A; Jove M; Portero-Otin M; Pamplona R; Ferrer I; Pujol A
Ann Neurol; 2011 Jul; 70(1):84-92. PubMed ID: 21786300
[TBL] [Abstract][Full Text] [Related]
3. Therapeutic potential of deuterium-stabilized (R)-pioglitazone-PXL065-for X-linked adrenoleukodystrophy.
Monternier PA; Singh J; Parasar P; Theurey P; DeWitt S; Jacques V; Klett E; Kaur N; Nagaraja TN; Moller DE; Hallakou-Bozec S
J Inherit Metab Dis; 2022 Jul; 45(4):832-847. PubMed ID: 35510808
[TBL] [Abstract][Full Text] [Related]
4. Metformin-induced mitochondrial function and ABCD2 up-regulation in X-linked adrenoleukodystrophy involves AMP-activated protein kinase.
Singh J; Olle B; Suhail H; Felicella MM; Giri S
J Neurochem; 2016 Jul; 138(1):86-100. PubMed ID: 26849413
[TBL] [Abstract][Full Text] [Related]
5. Aberrant regulation of the GSK-3β/NRF2 axis unveils a novel therapy for adrenoleukodystrophy.
Ranea-Robles P; Launay N; Ruiz M; Calingasan NY; Dumont M; Naudí A; Portero-Otín M; Pamplona R; Ferrer I; Beal MF; Fourcade S; Pujol A
EMBO Mol Med; 2018 Aug; 10(8):. PubMed ID: 29997171
[TBL] [Abstract][Full Text] [Related]
6. Oxidative damage compromises energy metabolism in the axonal degeneration mouse model of X-adrenoleukodystrophy.
Galino J; Ruiz M; Fourcade S; Schlüter A; López-Erauskin J; Guilera C; Jove M; Naudi A; García-Arumí E; Andreu AL; Starkov AA; Pamplona R; Ferrer I; Portero-Otin M; Pujol A
Antioxid Redox Signal; 2011 Oct; 15(8):2095-107. PubMed ID: 21453200
[TBL] [Abstract][Full Text] [Related]
7. Mitochondrial dysfunction and oxidative damage cooperatively fuel axonal degeneration in X-linked adrenoleukodystrophy.
Fourcade S; López-Erauskin J; Ruiz M; Ferrer I; Pujol A
Biochimie; 2014 Mar; 98():143-9. PubMed ID: 24076127
[TBL] [Abstract][Full Text] [Related]
8. The peroxisomal fatty acid transporter ABCD1/PMP-4 is required in the C. elegans hypodermis for axonal maintenance: A worm model for adrenoleukodystrophy.
Coppa A; Guha S; Fourcade S; Parameswaran J; Ruiz M; Moser AB; Schlüter A; Murphy MP; Lizcano JM; Miranda-Vizuete A; Dalfó E; Pujol A
Free Radic Biol Med; 2020 May; 152():797-809. PubMed ID: 32017990
[TBL] [Abstract][Full Text] [Related]
9. Impaired mitochondrial oxidative phosphorylation in the peroxisomal disease X-linked adrenoleukodystrophy.
López-Erauskin J; Galino J; Ruiz M; Cuezva JM; Fabregat I; Cacabelos D; Boada J; Martínez J; Ferrer I; Pamplona R; Villarroya F; Portero-Otín M; Fourcade S; Pujol A
Hum Mol Genet; 2013 Aug; 22(16):3296-305. PubMed ID: 23604518
[TBL] [Abstract][Full Text] [Related]
10. Oxidative stress modulates mitochondrial failure and cyclophilin D function in X-linked adrenoleukodystrophy.
López-Erauskin J; Galino J; Bianchi P; Fourcade S; Andreu AL; Ferrer I; Muñoz-Pinedo C; Pujol A
Brain; 2012 Dec; 135(Pt 12):3584-98. PubMed ID: 23250880
[TBL] [Abstract][Full Text] [Related]
11. ABCD1 deletion-induced mitochondrial dysfunction is corrected by SAHA: implication for adrenoleukodystrophy.
Baarine M; Beeson C; Singh A; Singh I
J Neurochem; 2015 May; 133(3):380-96. PubMed ID: 25393703
[TBL] [Abstract][Full Text] [Related]
12. Pathomechanisms underlying X-adrenoleukodystrophy: a three-hit hypothesis.
Singh I; Pujol A
Brain Pathol; 2010 Jul; 20(4):838-44. PubMed ID: 20626745
[TBL] [Abstract][Full Text] [Related]
13. Targeted Brain Delivery of Dendrimer-4-Phenylbutyrate Ameliorates Neurological Deficits in a Long-Term ABCD1-Deficient Mouse Model of X-Linked Adrenoleukodystrophy.
Nemeth CL; Gӧk Ö; Tomlinson SN; Sharma A; Moser AB; Kannan S; Kannan RM; Fatemi A
Neurotherapeutics; 2023 Jan; 20(1):272-283. PubMed ID: 36207570
[TBL] [Abstract][Full Text] [Related]
14. Beneficial Effects of the Direct AMP-Kinase Activator PXL770 in In Vitro and In Vivo Models of X-Linked Adrenoleukodystrophy.
Monternier PA; Parasar P; Theurey P; Gluais Dagorn P; Kaur N; Nagaraja TN; Fouqueray P; Bolze S; Moller DE; Singh J; Hallakou-Bozec S
J Pharmacol Exp Ther; 2022 Aug; 382(2):208-222. PubMed ID: 35764327
[TBL] [Abstract][Full Text] [Related]
15. Late onset neurological phenotype of the X-ALD gene inactivation in mice: a mouse model for adrenomyeloneuropathy.
Pujol A; Hindelang C; Callizot N; Bartsch U; Schachner M; Mandel JL
Hum Mol Genet; 2002 Mar; 11(5):499-505. PubMed ID: 11875044
[TBL] [Abstract][Full Text] [Related]
16. Lack of adrenoleukodystrophy protein enhances oligodendrocyte disturbance and microglia activation in mice with combined Abcd1/Mag deficiency.
Dumser M; Bauer J; Lassmann H; Berger J; Forss-Petter S
Acta Neuropathol; 2007 Dec; 114(6):573-86. PubMed ID: 17828604
[TBL] [Abstract][Full Text] [Related]
17. Valproic acid induces antioxidant effects in X-linked adrenoleukodystrophy.
Fourcade S; Ruiz M; Guilera C; Hahnen E; Brichta L; Naudi A; Portero-Otín M; Dacremont G; Cartier N; Wanders R; Kemp S; Mandel JL; Wirth B; Pamplona R; Aubourg P; Pujol A
Hum Mol Genet; 2010 May; 19(10):2005-14. PubMed ID: 20179078
[TBL] [Abstract][Full Text] [Related]
18. Tauroursodeoxycholic bile acid arrests axonal degeneration by inhibiting the unfolded protein response in X-linked adrenoleukodystrophy.
Launay N; Ruiz M; Grau L; Ortega FJ; Ilieva EV; Martínez JJ; Galea E; Ferrer I; Knecht E; Pujol A; Fourcade S
Acta Neuropathol; 2017 Feb; 133(2):283-301. PubMed ID: 28004277
[TBL] [Abstract][Full Text] [Related]
19. Functional genomic analysis unravels a metabolic-inflammatory interplay in adrenoleukodystrophy.
Schlüter A; Espinosa L; Fourcade S; Galino J; López E; Ilieva E; Morató L; Asheuer M; Cook T; McLaren A; Reid J; Kelly F; Bates S; Aubourg P; Galea E; Pujol A
Hum Mol Genet; 2012 Mar; 21(5):1062-77. PubMed ID: 22095690
[TBL] [Abstract][Full Text] [Related]
20. Modulation of mitochondrial and inflammatory homeostasis through RIP140 is neuroprotective in an adrenoleukodystrophy mouse model.
Ranea-Robles P; Galino J; Espinosa L; Schlüter A; Ruiz M; Calingasan NY; Villarroya F; Naudí A; Pamplona R; Ferrer I; Beal MF; Portero-Otín M; Fourcade S; Pujol A
Neuropathol Appl Neurobiol; 2022 Feb; 48(1):e12747. PubMed ID: 34237158
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]