194 related articles for article (PubMed ID: 23903056)
1. Subcellular localization of dystrophin isoforms in cardiomyocytes and phenotypic analysis of dystrophin-deficient mice reveal cardiac myopathy is predominantly caused by a deficiency in full-length dystrophin.
Masubuchi N; Shidoh Y; Kondo S; Takatoh J; Hanaoka K
Exp Anim; 2013; 62(3):211-7. PubMed ID: 23903056
[TBL] [Abstract][Full Text] [Related]
2. Investigating the role of dystrophin isoform deficiency in motor function in Duchenne muscular dystrophy.
Chesshyre M; Ridout D; Hashimoto Y; Ookubo Y; Torelli S; Maresh K; Ricotti V; Abbott L; Gupta VA; Main M; Ferrari G; Kowala A; Lin YY; Tedesco FS; Scoto M; Baranello G; Manzur A; Aoki Y; Muntoni F
J Cachexia Sarcopenia Muscle; 2022 Apr; 13(2):1360-1372. PubMed ID: 35083887
[TBL] [Abstract][Full Text] [Related]
3. Exacerbation of dystrophic cardiomyopathy by phospholamban deficiency mediated chronically increased cardiac Ca
Law ML; Prins KW; Olander ME; Metzger JM
Am J Physiol Heart Circ Physiol; 2018 Dec; 315(6):H1544-H1552. PubMed ID: 30118340
[TBL] [Abstract][Full Text] [Related]
4. Dystrophin-deficient cardiomyopathy in mouse: expression of Nox4 and Lox are associated with fibrosis and altered functional parameters in the heart.
Spurney CF; Knoblach S; Pistilli EE; Nagaraju K; Martin GR; Hoffman EP
Neuromuscul Disord; 2008 May; 18(5):371-81. PubMed ID: 18440230
[TBL] [Abstract][Full Text] [Related]
5. Cardiovascular phenotype of the
Szabó PL; Ebner J; Koenig X; Hamza O; Watzinger S; Trojanek S; Abraham D; Todt H; Kubista H; Schicker K; Remy S; Anegon I; Kiss A; Podesser BK; Hilber K
Dis Model Mech; 2021 Feb; 14(2):. PubMed ID: 33619211
[TBL] [Abstract][Full Text] [Related]
6. Startle responses in Duchenne muscular dystrophy: a novel biomarker of brain dystrophin deficiency.
Maresh K; Papageorgiou A; Ridout D; Harrison NA; Mandy W; Skuse D; Muntoni F
Brain; 2023 Jan; 146(1):252-265. PubMed ID: 35136951
[TBL] [Abstract][Full Text] [Related]
7. Acute AT
Meyers TA; Heitzman JA; Krebsbach AM; Aufdembrink LM; Hughes R; Bartolomucci A; Townsend D
J Mol Cell Cardiol; 2019 Mar; 128():51-61. PubMed ID: 30664850
[TBL] [Abstract][Full Text] [Related]
8. Dystrophin Deficiency Causes Progressive Depletion of Cardiovascular Progenitor Cells in the Heart.
Jelinkova S; Sleiman Y; Fojtík P; Aimond F; Finan A; Hugon G; Scheuermann V; Beckerová D; Cazorla O; Vincenti M; Amedro P; Richard S; Jaros J; Dvorak P; Lacampagne A; Carnac G; Rotrekl V; Meli AC
Int J Mol Sci; 2021 May; 22(9):. PubMed ID: 34068508
[TBL] [Abstract][Full Text] [Related]
9. Full-length dystrophin expression in half of the heart cells ameliorates beta-isoproterenol-induced cardiomyopathy in mdx mice.
Yue Y; Skimming JW; Liu M; Strawn T; Duan D
Hum Mol Genet; 2004 Aug; 13(15):1669-75. PubMed ID: 15190010
[TBL] [Abstract][Full Text] [Related]
10. Natural History of a Mouse Model Overexpressing the Dp71 Dystrophin Isoform.
Lim KRQ; Shah MNA; Woo S; Wilton-Clark H; Zhabyeyev P; Wang F; Maruyama R; Oudit GY; Yokota T
Int J Mol Sci; 2021 Nov; 22(23):. PubMed ID: 34884423
[TBL] [Abstract][Full Text] [Related]
11. Combined deficiency of dystrophin and beta1 integrin in the cardiac myocyte causes myocardial dysfunction, fibrosis and calcification.
Elsherif L; Huang MS; Shai SY; Yang Y; Li RY; Chun J; Mekany MA; Chu AL; Kaufman SJ; Ross RS
Circ Res; 2008 May; 102(9):1109-17. PubMed ID: 18340010
[TBL] [Abstract][Full Text] [Related]
12. The role of reactive oxygen species in the hearts of dystrophin-deficient mdx mice.
Williams IA; Allen DG
Am J Physiol Heart Circ Physiol; 2007 Sep; 293(3):H1969-77. PubMed ID: 17573457
[TBL] [Abstract][Full Text] [Related]
13. Ryanodine receptor dysfunction causes senescence and fibrosis in Duchenne dilated cardiomyopathy.
Souidi M; Resta J; Dridi H; Sleiman Y; Reiken S; Formoso K; Colombani S; Amédro P; Meyer P; Charrabi A; Vincenti M; Liu Y; Soni RK; Lezoualc'h F; Stéphane Blot DVM; Rivier F; Cazorla O; Parini A; Marks AR; Mialet-Perez J; Lacampagne A; Meli AC
J Cachexia Sarcopenia Muscle; 2024 Apr; 15(2):536-551. PubMed ID: 38221511
[TBL] [Abstract][Full Text] [Related]
14. Redefinition of dystrophin isoform distribution in mouse tissue by RT-PCR implies role in nonmuscle manifestations of duchenne muscular dystrophy.
Tokarz SA; Duncan NM; Rash SM; Sadeghi A; Dewan AK; Pillers DA
Mol Genet Metab; 1998 Dec; 65(4):272-81. PubMed ID: 9889014
[TBL] [Abstract][Full Text] [Related]
15. Modeling Duchenne Muscular Dystrophy Cardiomyopathy with Patients' Induced Pluripotent Stem-Cell-Derived Cardiomyocytes.
Eisen B; Binah O
Int J Mol Sci; 2023 May; 24(10):. PubMed ID: 37240001
[TBL] [Abstract][Full Text] [Related]
16. AAV micro-dystrophin gene therapy alleviates stress-induced cardiac death but not myocardial fibrosis in >21-m-old mdx mice, an end-stage model of Duchenne muscular dystrophy cardiomyopathy.
Bostick B; Shin JH; Yue Y; Wasala NB; Lai Y; Duan D
J Mol Cell Cardiol; 2012 Aug; 53(2):217-22. PubMed ID: 22587991
[TBL] [Abstract][Full Text] [Related]
17. Altered presynaptic ultrastructure in excitatory hippocampal synapses of mice lacking dystrophins Dp427 or Dp71.
Miranda R; Nudel U; Laroche S; Vaillend C
Neurobiol Dis; 2011 Jul; 43(1):134-41. PubMed ID: 21397023
[TBL] [Abstract][Full Text] [Related]
18. The long dystrophin gene product Dp427 modulates retinal function and vascular morphology in response to age and retinal ischemia.
Bucher F; Friedlander MSH; Aguilar E; Kurihara T; Krohne TU; Usui Y; Friedlander M
Neurochem Int; 2019 Oct; 129():104489. PubMed ID: 31199961
[TBL] [Abstract][Full Text] [Related]
19. Characterization of brain dystrophins absence and impact in dystrophin-deficient Dmdmdx rat model.
Caudal D; François V; Lafoux A; Ledevin M; Anegon I; Le Guiner C; Larcher T; Huchet C
PLoS One; 2020; 15(3):e0230083. PubMed ID: 32160266
[TBL] [Abstract][Full Text] [Related]
20. Absence of full-length dystrophin impairs normal maturation and contraction of cardiomyocytes derived from human-induced pluripotent stem cells.
Pioner JM; Guan X; Klaiman JM; Racca AW; Pabon L; Muskheli V; Macadangdang J; Ferrantini C; Hoopmann MR; Moritz RL; Kim DH; Tesi C; Poggesi C; Murry CE; Childers MK; Mack DL; Regnier M
Cardiovasc Res; 2020 Feb; 116(2):368-382. PubMed ID: 31049579
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]