183 related articles for article (PubMed ID: 24183914)
1. Genotype-specific alterations in vascular smooth muscle cell function in cystic fibrosis piglets.
Guo JJ; Stoltz DA; Zhu V; Volk KA; Segar JL; McCray PB; Roghair RD
J Cyst Fibros; 2014 May; 13(3):251-9. PubMed ID: 24183914
[TBL] [Abstract][Full Text] [Related]
2. Reduced blood pressure of CFTR-F508del carriers correlates with diminished arterial reactivity rather than circulating blood volume in mice.
Peotta VA; Bhandary P; Ogu U; Volk KA; Roghair RD
PLoS One; 2014; 9(5):e96756. PubMed ID: 24801204
[TBL] [Abstract][Full Text] [Related]
3. F508del-CFTR increases intracellular Ca(2+) signaling that causes enhanced calcium-dependent Cl(-) conductance in cystic fibrosis.
Martins JR; Kongsuphol P; Sammels E; Dahimène S; Aldehni F; Clarke LA; Schreiber R; de Smedt H; Amaral MD; Kunzelmann K
Biochim Biophys Acta; 2011 Nov; 1812(11):1385-92. PubMed ID: 21907281
[TBL] [Abstract][Full Text] [Related]
4. Abnormal spatial diffusion of Ca2+ in F508del-CFTR airway epithelial cells.
Antigny F; Norez C; Cantereau A; Becq F; Vandebrouck C
Respir Res; 2008 Oct; 9(1):70. PubMed ID: 18973672
[TBL] [Abstract][Full Text] [Related]
5. Calcium homeostasis is abnormal in cystic fibrosis airway epithelial cells but is normalized after rescue of F508del-CFTR.
Antigny F; Norez C; Becq F; Vandebrouck C
Cell Calcium; 2008 Feb; 43(2):175-83. PubMed ID: 17590432
[TBL] [Abstract][Full Text] [Related]
6. Increasing the Endoplasmic Reticulum Pool of the F508del Allele of the Cystic Fibrosis Transmembrane Conductance Regulator Leads to Greater Folding Correction by Small Molecule Therapeutics.
Chung WJ; Goeckeler-Fried JL; Havasi V; Chiang A; Rowe SM; Plyler ZE; Hong JS; Mazur M; Piazza GA; Keeton AB; White EL; Rasmussen L; Weissman AM; Denny RA; Brodsky JL; Sorscher EJ
PLoS One; 2016; 11(10):e0163615. PubMed ID: 27732613
[TBL] [Abstract][Full Text] [Related]
7. Control of cystic fibrosis transmembrane conductance regulator membrane trafficking: not just from the endoplasmic reticulum to the Golgi.
Farinha CM; Matos P; Amaral MD
FEBS J; 2013 Sep; 280(18):4396-406. PubMed ID: 23773658
[TBL] [Abstract][Full Text] [Related]
8. Maintaining low Ca2+ level in the endoplasmic reticulum restores abnormal endogenous F508del-CFTR trafficking in airway epithelial cells.
Norez C; Antigny F; Becq F; Vandebrouck C
Traffic; 2006 May; 7(5):562-73. PubMed ID: 16643279
[TBL] [Abstract][Full Text] [Related]
9. Pseudomonas aeruginosa Homoserine lactone activates store-operated cAMP and cystic fibrosis transmembrane regulator-dependent Cl- secretion by human airway epithelia.
Schwarzer C; Wong S; Shi J; Matthes E; Illek B; Ianowski JP; Arant RJ; Isacoff E; Vais H; Foskett JK; Maiellaro I; Hofer AM; Machen TE
J Biol Chem; 2010 Nov; 285(45):34850-63. PubMed ID: 20739289
[TBL] [Abstract][Full Text] [Related]
10. Probing conformational rescue induced by a chemical corrector of F508del-cystic fibrosis transmembrane conductance regulator (CFTR) mutant.
Yu W; Kim Chiaw P; Bear CE
J Biol Chem; 2011 Jul; 286(28):24714-25. PubMed ID: 21602569
[TBL] [Abstract][Full Text] [Related]
11. Cystic Fibrosis Transmembrane Conductance Regulator in Sarcoplasmic Reticulum of Airway Smooth Muscle. Implications for Airway Contractility.
Cook DP; Rector MV; Bouzek DC; Michalski AS; Gansemer ND; Reznikov LR; Li X; Stroik MR; Ostedgaard LS; Abou Alaiwa MH; Thompson MA; Prakash YS; Krishnan R; Meyerholz DK; Seow CY; Stoltz DA
Am J Respir Crit Care Med; 2016 Feb; 193(4):417-26. PubMed ID: 26488271
[TBL] [Abstract][Full Text] [Related]
12. Trimethylangelicin promotes the functional rescue of mutant F508del CFTR protein in cystic fibrosis airway cells.
Favia M; Mancini MT; Bezzerri V; Guerra L; Laselva O; Abbattiscianni AC; Debellis L; Reshkin SJ; Gambari R; Cabrini G; Casavola V
Am J Physiol Lung Cell Mol Physiol; 2014 Jul; 307(1):L48-61. PubMed ID: 24816489
[TBL] [Abstract][Full Text] [Related]
13. Cystic fibrosis transmembrane conductance regulator in human muscle: Dysfunction causes abnormal metabolic recovery in exercise.
Lamhonwah AM; Bear CE; Huan LJ; Kim Chiaw P; Ackerley CA; Tein I
Ann Neurol; 2010 Jun; 67(6):802-8. PubMed ID: 20517942
[TBL] [Abstract][Full Text] [Related]
14. Two Small Molecules Restore Stability to a Subpopulation of the Cystic Fibrosis Transmembrane Conductance Regulator with the Predominant Disease-causing Mutation.
Meng X; Wang Y; Wang X; Wrennall JA; Rimington TL; Li H; Cai Z; Ford RC; Sheppard DN
J Biol Chem; 2017 Mar; 292(9):3706-3719. PubMed ID: 28087700
[TBL] [Abstract][Full Text] [Related]
15. Lack of CFTR in skeletal muscle predisposes to muscle wasting and diaphragm muscle pump failure in cystic fibrosis mice.
Divangahi M; Balghi H; Danialou G; Comtois AS; Demoule A; Ernest S; Haston C; Robert R; Hanrahan JW; Radzioch D; Petrof BJ
PLoS Genet; 2009 Jul; 5(7):e1000586. PubMed ID: 19649303
[TBL] [Abstract][Full Text] [Related]
16. Cystic Fibrosis: Proteostatic correctors of CFTR trafficking and alternative therapeutic targets.
Hanrahan JW; Sato Y; Carlile GW; Jansen G; Young JC; Thomas DY
Expert Opin Ther Targets; 2019 Aug; 23(8):711-724. PubMed ID: 31169041
[No Abstract] [Full Text] [Related]
17. Revertant mutants G550E and 4RK rescue cystic fibrosis mutants in the first nucleotide-binding domain of CFTR by different mechanisms.
Roxo-Rosa M; Xu Z; Schmidt A; Neto M; Cai Z; Soares CM; Sheppard DN; Amaral MD
Proc Natl Acad Sci U S A; 2006 Nov; 103(47):17891-6. PubMed ID: 17098864
[TBL] [Abstract][Full Text] [Related]
18. ERp29 regulates DeltaF508 and wild-type cystic fibrosis transmembrane conductance regulator (CFTR) trafficking to the plasma membrane in cystic fibrosis (CF) and non-CF epithelial cells.
Suaud L; Miller K; Alvey L; Yan W; Robay A; Kebler C; Kreindler JL; Guttentag S; Hubbard MJ; Rubenstein RC
J Biol Chem; 2011 Jun; 286(24):21239-53. PubMed ID: 21525008
[TBL] [Abstract][Full Text] [Related]
19. Calumenin contributes to ER-Ca
Philippe R; Antigny F; Buscaglia P; Norez C; Huguet F; Castelbou C; Trouvé P; Becq F; Frieden M; Férec C; Mignen O
Cell Calcium; 2017 Mar; 62():47-59. PubMed ID: 28189267
[TBL] [Abstract][Full Text] [Related]
20. Unravelling the Regions of Mutant F508del-CFTR More Susceptible to the Action of Four Cystic Fibrosis Correctors.
Amico G; Brandas C; Moran O; Baroni D
Int J Mol Sci; 2019 Nov; 20(21):. PubMed ID: 31683989
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]