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6. Prenatal diagnosis of 3-hydroxy-3-methylglutaric aciduria via enzyme activity measurements in chorionic villi, chorionic villous fibroblasts or amniocytes using a simple spectrophotometric method. Wanders RJ; Schutgens RB; Zoeters BH J Inherit Metab Dis; 1988; 11(4):430. PubMed ID: 2468820 [No Abstract] [Full Text] [Related]
7. 3-hydroxy-3-methylglutaric, 3-methylglutaconic and 3-methylglutaric acids can be non-specific indicators of metabolic disease. Hammond J; Wilcken B J Inherit Metab Dis; 1984; 7 Suppl 2():117-8. PubMed ID: 6207381 [No Abstract] [Full Text] [Related]
8. 3-Hydroxy-3-methylglutaric aciduria: response to carnitine therapy and fat and leucine restriction. Dasouki M; Buchanan D; Mercer N; Gibson KM; Thoene J J Inherit Metab Dis; 1987; 10(2):142-6. PubMed ID: 2443756 [TBL] [Abstract][Full Text] [Related]
9. Prenatal diagnosis of 3-hydroxy-3-methylglutaric aciduria by GC-MS and enzymology on cultured amniocytes and chorionic villi. Chalmers RA; Tracey BM; Mistry J; Stacey TE; McFadyen IR J Inherit Metab Dis; 1989; 12(3):286-92. PubMed ID: 2482386 [TBL] [Abstract][Full Text] [Related]
10. 3-hydroxy-3-methylglutaric aciduria: a new assay of 3-hydroxy-3-methylglutaryl-coa lyase using high performance liquid chromatography. Gibson KM; Sweetman L; Nyhan WL; Page TM; Greene C; Cann HM Clin Chim Acta; 1982 Dec; 126(2):171-81. PubMed ID: 6185253 [TBL] [Abstract][Full Text] [Related]
11. Dizygotic twins with 3-hydroxy-3-methylglutaric aciduria; unusual presentation, family studies and dietary management. Stacey TE; de Sousa C; Tracey BM; Whitelaw A; Mistry J; Timbrell P; Chalmers RA Eur J Pediatr; 1985 Jul; 144(2):177-81. PubMed ID: 2412823 [TBL] [Abstract][Full Text] [Related]
12. 3-Methylglutaconic and 3-methylglutaric aciduria in a patient with suspected 3-methylglutaconyl-CoA hydratase deficiency. Lehnert W; Scharf J; Wendel U Eur J Pediatr; 1985 Mar; 143(4):301-3. PubMed ID: 2580710 [TBL] [Abstract][Full Text] [Related]
13. 3-Hydroxy-3-methylglutaryl-CoA lyase in human skin fibroblasts: study of its properties and deficient activity in 3-hydroxy-3-methylglutaric aciduria patients using a simple spectrophotometric method. Wanders RJ; Schutgens RB; Zoeters PH Clin Chim Acta; 1988 Jan; 171(1):95-101. PubMed ID: 2450702 [TBL] [Abstract][Full Text] [Related]
14. Mitochondrial DNA depletion associated with partial complex II and IV deficiencies and 3-methylglutaconic aciduria. Scaglia F; Sutton VR; Bodamer OA; Vogel H; Shapira SK; Naviaux RK; Vladutiu GD J Child Neurol; 2001 Feb; 16(2):136-8. PubMed ID: 11292221 [TBL] [Abstract][Full Text] [Related]
15. The contribution of protein catabolism to metabolic decompensation in 3-hydroxy-3-methylglutaric aciduria. Thompson GN; Chalmers RA; Halliday D Eur J Pediatr; 1990 Feb; 149(5):346-50. PubMed ID: 1690129 [TBL] [Abstract][Full Text] [Related]
16. 3-Methylglutaconic aciduria in two adults. Kuhara T; Matsumoto I; Saiki K; Takabayashi H; Kuwabara S Clin Chim Acta; 1992 Apr; 207(1-2):151-3. PubMed ID: 1375542 [No Abstract] [Full Text] [Related]
17. Urinary excretion of 3-hydroxy-3-methylglutaric acid in the diabetic condition. Deana R; Lippe G; Galzigna L Clin Biochem; 1982 Apr; 15(2):73-5. PubMed ID: 6178532 [TBL] [Abstract][Full Text] [Related]
18. Age-dependent excretion of 3-hydroxy-3-methylglutaric acid (HMG) and ketone bodies in the urine of full-term and pre-term newborns. Lippe G; Galzigna L; Francesconi M; Zorzi C; Deana R Clin Chim Acta; 1982 Dec; 126(3):291-5. PubMed ID: 6185254 [TBL] [Abstract][Full Text] [Related]
19. Inherited 3-methylglutaconic aciduria in two brothers--another defect of leucine metabolism. Duran M; Beemer FA; Tibosch AS; Bruinvis L; Ketting D; Wadman SK J Pediatr; 1982 Oct; 101(4):551-4. PubMed ID: 6181239 [TBL] [Abstract][Full Text] [Related]
20. Phenotypic heterogeneity in the syndromes of 3-methylglutaconic aciduria. Gibson KM; Sherwood WG; Hoffman GF; Stumpf DA; Dianzani I; Schutgens RB; Barth PG; Weismann U; Bachmann C; Schrynemackers-Pitance P J Pediatr; 1991 Jun; 118(6):885-90. PubMed ID: 1710267 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]