287 related articles for article (PubMed ID: 2427264)
1. Accumulation and defective beta-oxidation of very long chain fatty acids in Zellweger's syndrome, adrenoleukodystrophy and Refsum's disease variants.
Poulos A; Singh H; Paton B; Sharp P; Derwas N
Clin Genet; 1986 May; 29(5):397-408. PubMed ID: 2427264
[TBL] [Abstract][Full Text] [Related]
2. Beta-oxidation of very-long-chain fatty acids and their coenzyme A derivatives by human skin fibroblasts.
Singh H; Derwas N; Poulos A
Arch Biochem Biophys; 1987 May; 254(2):526-33. PubMed ID: 2437859
[TBL] [Abstract][Full Text] [Related]
3. Peroxisomal very long-chain fatty acid beta-oxidation in human skin fibroblasts: activity in Zellweger syndrome and other peroxisomal disorders.
Wanders RJ; van Roermund CW; van Wijland MJ; Heikoop J; Schutgens RB; Schram AW; Tager JM; van den Bosch H; Poll-Thé BT; Saudubray JM
Clin Chim Acta; 1987 Jul; 166(2-3):255-63. PubMed ID: 2441904
[TBL] [Abstract][Full Text] [Related]
4. Metabolism of saturated and polyunsaturated very-long-chain fatty acids in fibroblasts from patients with defects in peroxisomal beta-oxidation.
Street JM; Singh H; Poulos A
Biochem J; 1990 Aug; 269(3):671-7. PubMed ID: 2117919
[TBL] [Abstract][Full Text] [Related]
5. Plasma polyenoic very-long-chain fatty acids in peroxisomal disease: biochemical discrimination of Zellweger's syndrome from other phenotypes.
Poulos A; Sharp P; Johnson D
Neurology; 1989 Jan; 39(1):44-7. PubMed ID: 2462697
[TBL] [Abstract][Full Text] [Related]
6. Formation of a novel arachidonic acid metabolite in peroxisomes.
Gordon JA; Heller SK; Rhead WJ; Watkins PA; Spector AA
Prostaglandins Leukot Essent Fatty Acids; 1995; 52(2-3):77-81. PubMed ID: 7540307
[TBL] [Abstract][Full Text] [Related]
7. Peroxisomal integral membrane proteins in livers of patients with Zellweger syndrome, infantile Refsum's disease and X-linked adrenoleukodystrophy.
Small GM; Santos MJ; Imanaka T; Poulos A; Danks DM; Moser HW; Lazarow PB
J Inherit Metab Dis; 1988; 11(4):358-71. PubMed ID: 2468817
[TBL] [Abstract][Full Text] [Related]
8. Phytanic acid and very long chain fatty acids in genetic peroxisomal disorders.
Molzer B; Kainz-Korschinsky M; Sundt-Heller R; Bernheimer H
J Clin Chem Clin Biochem; 1989 May; 27(5):309-14. PubMed ID: 2474624
[TBL] [Abstract][Full Text] [Related]
9. A comparative study of straight chain and branched chain fatty acid oxidation in skin fibroblasts from patients with peroxisomal disorders.
Singh H; Usher S; Johnson D; Poulos A
J Lipid Res; 1990 Feb; 31(2):217-25. PubMed ID: 1691260
[TBL] [Abstract][Full Text] [Related]
10. Cellular oxidation of lignoceric acid is regulated by the subcellular localization of lignoceroyl-CoA ligases.
Lazo O; Contreras M; Yoshida Y; Singh AK; Stanley W; Weise M; Singh I
J Lipid Res; 1990 Apr; 31(4):583-95. PubMed ID: 2141053
[TBL] [Abstract][Full Text] [Related]
11. Very long-chain fatty acids in peroxisomal disease.
Poulos A; Beckman K; Johnson DW; Paton BC; Robinson BS; Sharp P; Usher S; Singh H
Adv Exp Med Biol; 1992; 318():331-40. PubMed ID: 1378993
[TBL] [Abstract][Full Text] [Related]
12. Cerebro-hepato-renal (Zellweger) syndrome, adrenoleukodystrophy, and Refsum's disease: plasma changes and skin fibroblast phytanic acid oxidase.
Poulos A; Sharp P; Fellenberg AJ; Danks DM
Hum Genet; 1985; 70(2):172-7. PubMed ID: 2408988
[TBL] [Abstract][Full Text] [Related]
13. Peroxisomal beta-oxidation of branched chain fatty acids in human skin fibroblasts.
Singh H; Brogan M; Johnson D; Poulos A
J Lipid Res; 1992 Nov; 33(11):1597-605. PubMed ID: 1464743
[TBL] [Abstract][Full Text] [Related]
14. Lignoceric acid is oxidized in the peroxisome: implications for the Zellweger cerebro-hepato-renal syndrome and adrenoleukodystrophy.
Singh I; Moser AE; Goldfischer S; Moser HW
Proc Natl Acad Sci U S A; 1984 Jul; 81(13):4203-7. PubMed ID: 6588384
[TBL] [Abstract][Full Text] [Related]
15. Phytanic acid alpha-oxidation and complementation analysis of classical Refsum and peroxisomal disorders.
Poll-The BT; Skjeldal OH; Stokke O; Poulos A; Demaugre F; Saudubray JM
Hum Genet; 1989 Jan; 81(2):175-81. PubMed ID: 2463966
[TBL] [Abstract][Full Text] [Related]
16. The deficient degradation of synthetic 2- and 3-methyl-branched fatty acids in fibroblasts from patients with peroxisomal disorders.
Van Veldhoven PP; Huang S; Eyssen HJ; Mannaerts GP
J Inherit Metab Dis; 1993; 16(2):381-91. PubMed ID: 7692128
[TBL] [Abstract][Full Text] [Related]
17. Infantile Refsum's disease (phytanic acid storage disease): a variant of Zellweger's syndrome?
Poulos A; Sharp P; Whiting M
Clin Genet; 1984 Dec; 26(6):579-86. PubMed ID: 6209040
[TBL] [Abstract][Full Text] [Related]
18. Localization of nervonic acid beta-oxidation in human and rodent peroxisomes: impaired oxidation in Zellweger syndrome and X-linked adrenoleukodystrophy.
Sandhir R; Khan M; Chahal A; Singh I
J Lipid Res; 1998 Nov; 39(11):2161-71. PubMed ID: 9799802
[TBL] [Abstract][Full Text] [Related]
19. Peroxisomal functions in classical Refsum's disease: comparison with the infantile form of Refsum's disease.
Wanders RJ; Heymans HS; Schutgens RB; Poll-Thé BT; Saudubray JM; Tager JM; Schrakamp G; van den Bosch H
J Neurol Sci; 1988 Apr; 84(2-3):147-55. PubMed ID: 2454298
[TBL] [Abstract][Full Text] [Related]
20. Clinical and biochemical heterogeneity in conditions with phytanic acid accumulation.
Skjeldal OH; Stokke O; Refsum S; Norseth J; Petit H
J Neurol Sci; 1987 Jan; 77(1):87-96. PubMed ID: 2433405
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]