These tools will no longer be maintained as of December 31, 2024. Archived website can be found here. PubMed4Hh GitHub repository can be found here. Contact NLM Customer Service if you have questions.
2. A Novel PORCN Frameshift Mutation Leading to Focal Dermal Hypoplasia: A Case Report. Durmaz CD; McGrath J; Liu L; Karabulut HG Cytogenet Genome Res; 2018; 154(3):119-121. PubMed ID: 29525789 [TBL] [Abstract][Full Text] [Related]
3. Goltz-Gorlin (focal dermal hypoplasia) and the microphthalmia with linear skin defects (MLS) syndrome: no evidence of genetic overlap. Harmsen MB; Azzarello-Burri S; García González MM; Gillessen-Kaesbach G; Meinecke P; Müller D; Rauch A; Rossier E; Seemanova E; Spaich C; Steiner B; Wieczorek D; Zenker M; Kutsche K Eur J Hum Genet; 2009 Oct; 17(10):1207-15. PubMed ID: 19277062 [TBL] [Abstract][Full Text] [Related]
4. Prenatal diagnosis of focal dermal hypoplasia: Report of three fetuses and review of the literature. Mary L; Scheidecker S; Kohler M; Lombardi MP; Delezoide AL; Auberger E; Triau S; Colin E; Gerard M; Grzeschik KH; Dollfus H; Antal MC Am J Med Genet A; 2017 Feb; 173(2):479-486. PubMed ID: 27623003 [TBL] [Abstract][Full Text] [Related]
5. Phenotypic and molecular characterization of focal dermal hypoplasia in 18 individuals. Bostwick B; Fang P; Patel A; Sutton VR Am J Med Genet C Semin Med Genet; 2016 Mar; 172C(1):9-20. PubMed ID: 26853229 [TBL] [Abstract][Full Text] [Related]
6. Novel and recurrent PORCN gene mutations in almost unilateral and typical focal dermal hypoplasia patients. Nakanishi G; Hasegawa K; Oono T; Koshida S; Fujimoto N; Iwatsuki K; Tanaka H; Tanaka T Eur J Dermatol; 2013; 23(1):64-7. PubMed ID: 23399492 [TBL] [Abstract][Full Text] [Related]
7. Deletion of Porcn in mice leads to multiple developmental defects and models human focal dermal hypoplasia (Goltz syndrome). Liu W; Shaver TM; Balasa A; Ljungberg MC; Wang X; Wen S; Nguyen H; Van den Veyver IB PLoS One; 2012; 7(3):e32331. PubMed ID: 22412863 [TBL] [Abstract][Full Text] [Related]
8. Focal dermal hypoplasia (Goltz-Gorlin syndrome): a new case with a novel variant in the PORCN gene (c.1250T>C:p.F417S) and unusual spinal anomaly. Garavelli L; Simonte G; Rosato S; Wischmeijer A; Albertini E; Guareschi E; Longo C; Albertini G; Gelmini C; Greco C; Errico S; Savino G; Pavanello M; Happle R; Unger S; Superti-Furga A; Grzeschik KH Am J Med Genet A; 2013 Jul; 161A(7):1750-4. PubMed ID: 23696273 [TBL] [Abstract][Full Text] [Related]
9. Goltz syndrome and PORCN: A view from Europe. Happle R Am J Med Genet C Semin Med Genet; 2016 Mar; 172C(1):21-3. PubMed ID: 26799923 [TBL] [Abstract][Full Text] [Related]
10. Fragmented Elastic Fibers in Focal Dermal Hypoplasia (Goltz-Gorlin Syndrome) Without Focal Dermal Hypoplasia: Report of a Male Case and Review of the Literature. Rohdenburg C; Liersch J; Kutsche K; Schaller J Am J Dermatopathol; 2020 Sep; 42(9):653-661. PubMed ID: 31789838 [TBL] [Abstract][Full Text] [Related]
11. Focal dermal hypoplasia resulting from a new nonsense mutation, p.E300X, in the PORCN gene. Clements SE; Wessagowit V; Lai-Cheong JE; Arita K; McGrath JA J Dermatol Sci; 2008 Jan; 49(1):39-42. PubMed ID: 17951029 [TBL] [Abstract][Full Text] [Related]
12. A nonsense porcn mutation in severe focal dermal hypoplasia with natal teeth. Dias C; Basto J; Pinho O; Barbêdo C; Mártins M; Bornholdt D; Fortuna A; Grzeschik KH; Lima M Fetal Pediatr Pathol; 2010; 29(5):305-13. PubMed ID: 20704476 [TBL] [Abstract][Full Text] [Related]
13. Goltz syndrome and PORCN mosaicism. Stevenson DA; Chirpich M; Contreras Y; Hanson H; Dent K Int J Dermatol; 2014 Dec; 53(12):1481-4. PubMed ID: 25040319 [TBL] [Abstract][Full Text] [Related]
14. Implementation of high-resolution melting analysis of the porcupine (PORCN) gene for molecular diagnosis of focal dermal hypoplasia: Identification of a novel mutation. Martínez-Saucedo M; Ornelas-Fuentes C; Dedden M; Sánchez-Urbina R; Díaz-García H; Aquino-Jarquin G; Moreno-Salgado R; Granados-Riveron JT J Gene Med; 2020 May; 22(5):e3165. PubMed ID: 31984575 [TBL] [Abstract][Full Text] [Related]
15. Phenotype and genotype in 17 patients with Goltz-Gorlin syndrome. Maas SM; Lombardi MP; van Essen AJ; Wakeling EL; Castle B; Temple IK; Kumar VK; Writzl K; Hennekam RC J Med Genet; 2009 Oct; 46(10):716-20. PubMed ID: 19586929 [TBL] [Abstract][Full Text] [Related]
16. PORCN gene mutations and the protean nature of focal dermal hypoplasia. Clements SE; Mellerio JE; Holden ST; McCauley J; McGrath JA Br J Dermatol; 2009 May; 160(5):1103-9. PubMed ID: 19292719 [TBL] [Abstract][Full Text] [Related]