287 related articles for article (PubMed ID: 24393714)
1. Loss of dystrophin and β-sarcoglycan significantly exacerbates the phenotype of laminin α2 chain-deficient animals.
Gawlik KI; Holmberg J; Durbeej M
Am J Pathol; 2014 Mar; 184(3):740-52. PubMed ID: 24393714
[TBL] [Abstract][Full Text] [Related]
2. Sub-physiological sarcoglycan expression contributes to compensatory muscle protection in mdx mice.
Li D; Long C; Yue Y; Duan D
Hum Mol Genet; 2009 Apr; 18(7):1209-20. PubMed ID: 19131360
[TBL] [Abstract][Full Text] [Related]
3. Fibrosis and inflammation are greater in muscles of beta-sarcoglycan-null mouse than mdx mouse.
Gibertini S; Zanotti S; Savadori P; Curcio M; Saredi S; Salerno F; Andreetta F; Bernasconi P; Mantegazza R; Mora M
Cell Tissue Res; 2014 May; 356(2):427-43. PubMed ID: 24723230
[TBL] [Abstract][Full Text] [Related]
4. Severe muscular dystrophy in mice that lack dystrophin and alpha7 integrin.
Rooney JE; Welser JV; Dechert MA; Flintoff-Dye NL; Kaufman SJ; Burkin DJ
J Cell Sci; 2006 Jun; 119(Pt 11):2185-95. PubMed ID: 16684813
[TBL] [Abstract][Full Text] [Related]
5. Three mouse models of muscular dystrophy: the natural history of strength and fatigue in dystrophin-, dystrophin/utrophin-, and laminin alpha2-deficient mice.
Connolly AM; Keeling RM; Mehta S; Pestronk A; Sanes JR
Neuromuscul Disord; 2001 Nov; 11(8):703-12. PubMed ID: 11595512
[TBL] [Abstract][Full Text] [Related]
6. Exon Skipping Using Antisense Oligonucleotides for Laminin-Alpha2-Deficient Muscular Dystrophy.
Hara Y; Mizobe Y; Miyatake S; Takizawa H; Nagata T; Yokota T; Takeda S; Aoki Y
Methods Mol Biol; 2018; 1828():553-564. PubMed ID: 30171567
[TBL] [Abstract][Full Text] [Related]
7. Secondary reduction of alpha7B integrin in laminin alpha2 deficient congenital muscular dystrophy supports an additional transmembrane link in skeletal muscle.
Cohn RD; Mayer U; Saher G; Herrmann R; van der Flier A; Sonnenberg A; Sorokin L; Voit T
J Neurol Sci; 1999 Mar; 163(2):140-52. PubMed ID: 10371075
[TBL] [Abstract][Full Text] [Related]
8. Proteasome inhibition improves the muscle of laminin α2 chain-deficient mice.
Carmignac V; Quéré R; Durbeej M
Hum Mol Genet; 2011 Feb; 20(3):541-52. PubMed ID: 21084425
[TBL] [Abstract][Full Text] [Related]
9. Animal models for muscular dystrophy show different patterns of sarcolemmal disruption.
Straub V; Rafael JA; Chamberlain JS; Campbell KP
J Cell Biol; 1997 Oct; 139(2):375-85. PubMed ID: 9334342
[TBL] [Abstract][Full Text] [Related]
10. Highly efficient in vivo delivery of PMO into regenerating myotubes and rescue in laminin-α2 chain-null congenital muscular dystrophy mice.
Aoki Y; Nagata T; Yokota T; Nakamura A; Wood MJ; Partridge T; Takeda S
Hum Mol Genet; 2013 Dec; 22(24):4914-28. PubMed ID: 23882132
[TBL] [Abstract][Full Text] [Related]
11. Bortezomib partially improves laminin α2 chain-deficient muscular dystrophy.
Körner Z; Fontes-Oliveira CC; Holmberg J; Carmignac V; Durbeej M
Am J Pathol; 2014 May; 184(5):1518-28. PubMed ID: 24631023
[TBL] [Abstract][Full Text] [Related]
12. Overexpression of mini-agrin in skeletal muscle increases muscle integrity and regenerative capacity in laminin-alpha2-deficient mice.
Bentzinger CF; Barzaghi P; Lin S; Ruegg MA
FASEB J; 2005 Jun; 19(8):934-42. PubMed ID: 15923403
[TBL] [Abstract][Full Text] [Related]
13. Absence of alpha 7 integrin in dystrophin-deficient mice causes a myopathy similar to Duchenne muscular dystrophy.
Guo C; Willem M; Werner A; Raivich G; Emerson M; Neyses L; Mayer U
Hum Mol Genet; 2006 Mar; 15(6):989-98. PubMed ID: 16476707
[TBL] [Abstract][Full Text] [Related]
14. A comparative freeze-fracture study of plasma membrane of dystrophic skeletal muscles in dy/dy mice with merosin (laminin 2) deficiency and mdx mice with dystrophin deficiency.
Shibuya S; Wakayama Y; Oniki H; Kojima H; Saito M; Etou T; Nonaka I
Neuropathol Appl Neurobiol; 1997 Apr; 23(2):123-31. PubMed ID: 9160897
[TBL] [Abstract][Full Text] [Related]
15. Deletion of integrin α7 subunit does not aggravate the phenotype of laminin α2 chain-deficient mice.
Gawlik KI; Durbeej M
Sci Rep; 2015 Sep; 5():13916. PubMed ID: 26355035
[TBL] [Abstract][Full Text] [Related]
16. Early skeletal muscle pathology and disease progress in the dy
Gawlik KI; Körner Z; Oliveira BM; Durbeej M
Sci Rep; 2019 Oct; 9(1):14324. PubMed ID: 31586140
[TBL] [Abstract][Full Text] [Related]
17. Extraocular muscle is spared despite the absence of an intact sarcoglycan complex in gamma- or delta-sarcoglycan-deficient mice.
Porter JD; Merriam AP; Hack AA; Andrade FH; McNally EM
Neuromuscul Disord; 2001 Mar; 11(2):197-207. PubMed ID: 11257478
[TBL] [Abstract][Full Text] [Related]
18. Electrotransfer of naked DNA in the skeletal muscles of animal models of muscular dystrophies.
Vilquin JT; Kennel PF; Paturneau-Jouas M; Chapdelaine P; Boissel N; Delaère P; Tremblay JP; Scherman D; Fiszman MY; Schwartz K
Gene Ther; 2001 Jul; 8(14):1097-107. PubMed ID: 11526457
[TBL] [Abstract][Full Text] [Related]
19. Potent pro-inflammatory and pro-fibrotic molecules, osteopontin and galectin-3, are not major disease modulators of laminin α2 chain-deficient muscular dystrophy.
Gawlik KI; Holmberg J; Svensson M; Einerborg M; Oliveira BM; Deierborg T; Durbeej M
Sci Rep; 2017 Mar; 7():44059. PubMed ID: 28281577
[TBL] [Abstract][Full Text] [Related]
20. Differential requirement for individual sarcoglycans and dystrophin in the assembly and function of the dystrophin-glycoprotein complex.
Hack AA; Lam MY; Cordier L; Shoturma DI; Ly CT; Hadhazy MA; Hadhazy MR; Sweeney HL; McNally EM
J Cell Sci; 2000 Jul; 113 ( Pt 14)():2535-44. PubMed ID: 10862711
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]