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7. 3-Methylglutaconic and 3-methylglutaric aciduria in a patient with suspected 3-methylglutaconyl-CoA hydratase deficiency. Lehnert W; Scharf J; Wendel U Eur J Pediatr; 1985 Mar; 143(4):301-3. PubMed ID: 2580710 [TBL] [Abstract][Full Text] [Related]
8. 3-hydroxy-3-methylglutaric aciduria: a new assay of 3-hydroxy-3-methylglutaryl-coa lyase using high performance liquid chromatography. Gibson KM; Sweetman L; Nyhan WL; Page TM; Greene C; Cann HM Clin Chim Acta; 1982 Dec; 126(2):171-81. PubMed ID: 6185253 [TBL] [Abstract][Full Text] [Related]
9. Prevention by L-carnitine of DNA damage induced by 3-hydroxy-3-methylglutaric and 3-methylglutaric acids and experimental evidence of lipid and DNA damage in patients with 3-hydroxy-3-methylglutaric aciduria. Delgado CA; Balbueno Guerreiro GB; Diaz Jacques CE; de Moura Coelho D; Sitta A; Manfredini V; Wajner M; Vargas CR Arch Biochem Biophys; 2019 Jun; 668():16-22. PubMed ID: 31047871 [TBL] [Abstract][Full Text] [Related]
10. GC/MS analysis of urine in 3-hydroxy-3-methylglutaryl-CoA lyase deficiency. Shinka T; Kuhara T; Inoue Y; Matsumoto M; Matsumoto I; Nakamura H; Irimichi H; Hasumi K; Endo A Acta Paediatr Jpn; 1992 Apr; 34(2):157-65. PubMed ID: 1377861 [TBL] [Abstract][Full Text] [Related]
11. A neonatal case of 3-hydroxy-3-methylglutaric-coenzyme A lyase deficiency. Santarelli F; Cassanello M; Enea A; Poma F; D'Onofrio V; Guala G; Garrone G; Puccinelli P; Caruso U; Porta F; Spada M Ital J Pediatr; 2013 May; 39():33. PubMed ID: 23705938 [TBL] [Abstract][Full Text] [Related]
13. 3-Hydroxy-3-methylglutaryl-CoA lyase in human skin fibroblasts: study of its properties and deficient activity in 3-hydroxy-3-methylglutaric aciduria patients using a simple spectrophotometric method. Wanders RJ; Schutgens RB; Zoeters PH Clin Chim Acta; 1988 Jan; 171(1):95-101. PubMed ID: 2450702 [TBL] [Abstract][Full Text] [Related]
14. The contribution of protein catabolism to metabolic decompensation in 3-hydroxy-3-methylglutaric aciduria. Thompson GN; Chalmers RA; Halliday D Eur J Pediatr; 1990 Feb; 149(5):346-50. PubMed ID: 1690129 [TBL] [Abstract][Full Text] [Related]
15. A case of organic aciduria--suspected 3-hydroxy-3-methylglutaric aciduria. Kulczycka H; Mielniczuk Z; Kamińska H; Lewanowicz W; Pronicka E Mater Med Pol; 1991; 23(4):312-4. PubMed ID: 1726825 [TBL] [Abstract][Full Text] [Related]
16. 3-hydroxy-3-methylglutaric, 3-methylglutaconic and 3-methylglutaric acids can be non-specific indicators of metabolic disease. Hammond J; Wilcken B J Inherit Metab Dis; 1984; 7 Suppl 2():117-8. PubMed ID: 6207381 [No Abstract] [Full Text] [Related]
17. Prenatal diagnosis of 3-hydroxy-3-methylglutaric aciduria by GC-MS and enzymology on cultured amniocytes and chorionic villi. Chalmers RA; Tracey BM; Mistry J; Stacey TE; McFadyen IR J Inherit Metab Dis; 1989; 12(3):286-92. PubMed ID: 2482386 [TBL] [Abstract][Full Text] [Related]
18. Inherited 3-methylglutaconic aciduria in two brothers--another defect of leucine metabolism. Duran M; Beemer FA; Tibosch AS; Bruinvis L; Ketting D; Wadman SK J Pediatr; 1982 Oct; 101(4):551-4. PubMed ID: 6181239 [TBL] [Abstract][Full Text] [Related]