252 related articles for article (PubMed ID: 24591516)
1. Long-chain acyl-CoA dehydrogenase deficiency as a cause of pulmonary surfactant dysfunction.
Goetzman ES; Alcorn JF; Bharathi SS; Uppala R; McHugh KJ; Kosmider B; Chen R; Zuo YY; Beck ME; McKinney RW; Skilling H; Suhrie KR; Karunanidhi A; Yeasted R; Otsubo C; Ellis B; Tyurina YY; Kagan VE; Mallampalli RK; Vockley J
J Biol Chem; 2014 Apr; 289(15):10668-10679. PubMed ID: 24591516
[TBL] [Abstract][Full Text] [Related]
2. The common K333Q polymorphism in long-chain acyl-CoA dehydrogenase (LCAD) reduces enzyme stability and function.
Beck ME; Zhang Y; Bharathi SS; Kosmider B; Bahmed K; Dahmer MK; Nogee LM; Goetzman ES
Mol Genet Metab; 2020; 131(1-2):83-89. PubMed ID: 32389575
[TBL] [Abstract][Full Text] [Related]
3. Tissue-specific strategies of the very-long chain acyl-CoA dehydrogenase-deficient (VLCAD-/-) mouse to compensate a defective fatty acid β-oxidation.
Tucci S; Herebian D; Sturm M; Seibt A; Spiekerkoetter U
PLoS One; 2012; 7(9):e45429. PubMed ID: 23024820
[TBL] [Abstract][Full Text] [Related]
4. Gestational, pathologic and biochemical differences between very long-chain acyl-CoA dehydrogenase deficiency and long-chain acyl-CoA dehydrogenase deficiency in the mouse.
Cox KB; Hamm DA; Millington DS; Matern D; Vockley J; Rinaldo P; Pinkert CA; Rhead WJ; Lindsey JR; Wood PA
Hum Mol Genet; 2001 Sep; 10(19):2069-77. PubMed ID: 11590124
[TBL] [Abstract][Full Text] [Related]
5. 2,6-Dimethylheptanoyl-CoA is a specific substrate for long-chain acyl-CoA dehydrogenase (LCAD): evidence for a major role of LCAD in branched-chain fatty acid oxidation.
Wanders RJ; Denis S; Ruiter JP; IJlst L; Dacremont G
Biochim Biophys Acta; 1998 Jul; 1393(1):35-40. PubMed ID: 9714723
[TBL] [Abstract][Full Text] [Related]
6. Targeted disruption of mouse long-chain acyl-CoA dehydrogenase gene reveals crucial roles for fatty acid oxidation.
Kurtz DM; Rinaldo P; Rhead WJ; Tian L; Millington DS; Vockley J; Hamm DA; Brix AE; Lindsey JR; Pinkert CA; O'Brien WE; Wood PA
Proc Natl Acad Sci U S A; 1998 Dec; 95(26):15592-7. PubMed ID: 9861014
[TBL] [Abstract][Full Text] [Related]
7. Is autism a disorder of fatty acid metabolism? Possible dysfunction of mitochondrial beta-oxidation by long chain acyl-CoA dehydrogenase.
Clark-Taylor T; Clark-Taylor BE
Med Hypotheses; 2004; 62(6):970-5. PubMed ID: 15142659
[TBL] [Abstract][Full Text] [Related]
8. Long-chain Acylcarnitines Reduce Lung Function by Inhibiting Pulmonary Surfactant.
Otsubo C; Bharathi S; Uppala R; Ilkayeva OR; Wang D; McHugh K; Zou Y; Wang J; Alcorn JF; Zuo YY; Hirschey MD; Goetzman ES
J Biol Chem; 2015 Sep; 290(39):23897-904. PubMed ID: 26240137
[TBL] [Abstract][Full Text] [Related]
9. Influence of dietary fatty acid chain-length on metabolic tolerance in mouse models of inherited defects in mitochondrial fatty acid beta-oxidation.
Schuler AM; Gower BA; Matern D; Rinaldo P; Wood PA
Mol Genet Metab; 2004 Dec; 83(4):322-9. PubMed ID: 15589119
[TBL] [Abstract][Full Text] [Related]
10. The fatty acid oxidation enzyme long-chain acyl-CoA dehydrogenase can be a source of mitochondrial hydrogen peroxide.
Zhang Y; Bharathi SS; Beck ME; Goetzman ES
Redox Biol; 2019 Sep; 26():101253. PubMed ID: 31234015
[TBL] [Abstract][Full Text] [Related]
11. Myocardial energy shortage and unmet anaplerotic needs in the fasted long-chain acyl-CoA dehydrogenase knockout mouse.
Bakermans AJ; Dodd MS; Nicolay K; Prompers JJ; Tyler DJ; Houten SM
Cardiovasc Res; 2013 Dec; 100(3):441-9. PubMed ID: 24042017
[TBL] [Abstract][Full Text] [Related]
12. Food withdrawal lowers energy expenditure and induces inactivity in long-chain fatty acid oxidation-deficient mouse models.
Diekman EF; van Weeghel M; Wanders RJ; Visser G; Houten SM
FASEB J; 2014 Jul; 28(7):2891-900. PubMed ID: 24648546
[TBL] [Abstract][Full Text] [Related]
13. Immunochemical characterization of variant long-chain acyl-CoA dehydrogenase in cultured fibroblasts from nine patients with long-chain acyl-CoA dehydrogenase deficiency.
Indo Y; Coates PM; Hale DE; Tanaka K
Pediatr Res; 1991 Sep; 30(3):211-5. PubMed ID: 1945557
[TBL] [Abstract][Full Text] [Related]
14. Characterization of carnitine and fatty acid metabolism in the long-chain acyl-CoA dehydrogenase-deficient mouse.
van Vlies N; Tian L; Overmars H; Bootsma AH; Kulik W; Wanders RJ; Wood PA; Vaz FM
Biochem J; 2005 Apr; 387(Pt 1):185-93. PubMed ID: 15535801
[TBL] [Abstract][Full Text] [Related]
15. Synergistic heterozygosity in mice with inherited enzyme deficiencies of mitochondrial fatty acid beta-oxidation.
Schuler AM; Gower BA; Matern D; Rinaldo P; Vockley J; Wood PA
Mol Genet Metab; 2005 May; 85(1):7-11. PubMed ID: 15862275
[TBL] [Abstract][Full Text] [Related]
16. Cardiac hypertrophy in mice with long-chain acyl-CoA dehydrogenase or very long-chain acyl-CoA dehydrogenase deficiency.
Cox KB; Liu J; Tian L; Barnes S; Yang Q; Wood PA
Lab Invest; 2009 Dec; 89(12):1348-54. PubMed ID: 19736549
[TBL] [Abstract][Full Text] [Related]
17. Increased mortality from influenza infection in long-chain acyl-CoA dehydrogenase knockout mice.
Shinde A; Luo J; Bharathi SS; Shi H; Beck ME; McHugh KJ; Alcorn JF; Wang J; Goetzman ES
Biochem Biophys Res Commun; 2018 Mar; 497(2):700-704. PubMed ID: 29458021
[TBL] [Abstract][Full Text] [Related]
18. Slc22a5 haploinsufficiency does not aggravate the phenotype of the long-chain acyl-CoA dehydrogenase KO mouse.
Ranea-Robles P; Yu C; van Vlies N; Vaz FM; Houten SM
J Inherit Metab Dis; 2020 May; 43(3):486-495. PubMed ID: 31845336
[TBL] [Abstract][Full Text] [Related]
19. De novo fatty acid biosynthesis and elongation in very long-chain acyl-CoA dehydrogenase-deficient mice supplemented with odd or even medium-chain fatty acids.
Tucci S; Behringer S; Spiekerkoetter U
FEBS J; 2015 Nov; 282(21):4242-53. PubMed ID: 26284828
[TBL] [Abstract][Full Text] [Related]
20. Acadl-SNP based genotyping assay for long-chain acyl-CoA dehydrogenase deficient mice.
Luther RJ; Almodovar AJ; Fullerton R; Wood PA
Mol Genet Metab; 2012 May; 106(1):62-7. PubMed ID: 22386849
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]
