241 related articles for article (PubMed ID: 24594605)
21. Protective effects of L-carnitine on behavioral alterations and neuroinflammation in striatum of glutaryl-COA dehydrogenase deficient mice.
Guerreiro G; Faverzani J; Moura AP; Volfart V; Gome Dos Reis B; Sitta A; Gonzalez EA; de Lima Rosa G; Coitinho AS; Baldo G; Wajner M; Vargas CR
Arch Biochem Biophys; 2021 Sep; 709():108970. PubMed ID: 34181873
[TBL] [Abstract][Full Text] [Related]
22. Acute renal proximal tubule alterations during induced metabolic crises in a mouse model of glutaric aciduria type 1.
Thies B; Meyer-Schwesinger C; Lamp J; Schweizer M; Koeller DM; Ullrich K; Braulke T; Mühlhausen C
Biochim Biophys Acta; 2013 Oct; 1832(10):1463-72. PubMed ID: 23623985
[TBL] [Abstract][Full Text] [Related]
23. Molecular genetic study of glutaric aciduria, type I: Identification of a novel mutation.
Shadmehri AA; Fattahi N; Pourreza MR; Koohiyan M; Zarifi S; Darbouy M; Sharifi R; Tavakkoly Bazzaz J; Tabatabaiefar MA
J Cell Biochem; 2019 Mar; 120(3):3367-3372. PubMed ID: 30203563
[TBL] [Abstract][Full Text] [Related]
24. Increased susceptibility to quinolinic acid-induced seizures and long-term changes in brain oscillations in an animal model of glutaric acidemia type I.
Barbieri Caus L; Pasquetti MV; Seminotti B; Woontner M; Wajner M; Calcagnotto ME
J Neurosci Res; 2022 Apr; 100(4):992-1007. PubMed ID: 34713466
[TBL] [Abstract][Full Text] [Related]
25. Marked reduction of Na(+), K(+)-ATPase and creatine kinase activities induced by acute lysine administration in glutaryl-CoA dehydrogenase deficient mice.
Amaral AU; Cecatto C; Seminotti B; Zanatta Â; Fernandes CG; Busanello EN; Braga LM; Ribeiro CA; de Souza DO; Woontner M; Koeller DM; Goodman S; Wajner M
Mol Genet Metab; 2012 Sep; 107(1-2):81-6. PubMed ID: 22578804
[TBL] [Abstract][Full Text] [Related]
26. Long Lasting High Lysine Diet Aggravates White Matter Injury in Glutaryl-CoA Dehydrogenase Deficient (Gcdh-/-) Mice.
Olivera-Bravo S; Seminotti B; Isasi E; Ribeiro CA; Leipnitz G; Woontner M; Goodman SI; Souza D; Barbeito L; Wajner M
Mol Neurobiol; 2019 Jan; 56(1):648-657. PubMed ID: 29779173
[TBL] [Abstract][Full Text] [Related]
27. Subependymal mass lesions and peripheral polyneuropathy in adult-onset glutaric aciduria type I.
Herskovitz M; Goldsher D; Sela BA; Mandel H
Neurology; 2013 Aug; 81(9):849-50. PubMed ID: 23884036
[TBL] [Abstract][Full Text] [Related]
28. Induction of oxidative stress in brain of glutaryl-CoA dehydrogenase deficient mice by acute lysine administration.
Seminotti B; da Rosa MS; Fernandes CG; Amaral AU; Braga LM; Leipnitz G; de Souza DO; Woontner M; Koeller DM; Goodman S; Wajner M
Mol Genet Metab; 2012 May; 106(1):31-8. PubMed ID: 22445450
[TBL] [Abstract][Full Text] [Related]
29. Pathogenesis of brain damage in glutaric acidemia type I: Lessons from the genetic mice model.
Wajner M; Amaral AU; Leipnitz G; Seminotti B
Int J Dev Neurosci; 2019 Nov; 78():215-221. PubMed ID: 31125684
[TBL] [Abstract][Full Text] [Related]
30. Multifactorial modulation of susceptibility to l-lysine in an animal model of glutaric aciduria type I.
Sauer SW; Opp S; Komatsuzaki S; Blank AE; Mittelbronn M; Burgard P; Koeller DM; Okun JG; Kölker S
Biochim Biophys Acta; 2015 May; 1852(5):768-77. PubMed ID: 25558815
[TBL] [Abstract][Full Text] [Related]
31. Interaction of glutaric aciduria type 1-related glutaryl-CoA dehydrogenase with mitochondrial matrix proteins.
Schmiesing J; Schlüter H; Ullrich K; Braulke T; Mühlhausen C
PLoS One; 2014; 9(2):e87715. PubMed ID: 24498361
[TBL] [Abstract][Full Text] [Related]
32. Disease-causing mutations affecting surface residues of mitochondrial glutaryl-CoA dehydrogenase impair stability, heteromeric complex formation and mitochondria architecture.
Schmiesing J; Lohmöller B; Schweizer M; Tidow H; Gersting SW; Muntau AC; Braulke T; Mühlhausen C
Hum Mol Genet; 2017 Feb; 26(3):538-551. PubMed ID: 28062662
[TBL] [Abstract][Full Text] [Related]
33. [Effect of glutaryl-CoA dehydrogenase gene silencing and high-concentration lysine on the viability of BRL hepatocytes].
Gao JZ; Zhang C; Yi Q; Ying YQ; Luo XP
Zhongguo Dang Dai Er Ke Za Zhi; 2017 Sep; 19(9):1014-1019. PubMed ID: 28899474
[TBL] [Abstract][Full Text] [Related]
34. Animal models for glutaryl-CoA dehydrogenase deficiency.
Koeller DM; Sauer S; Wajner M; de Mello CF; Goodman SI; Woontner M; Mühlhausen C; Okun JG; Kölker S
J Inherit Metab Dis; 2004; 27(6):813-8. PubMed ID: 15505386
[TBL] [Abstract][Full Text] [Related]
35. Ionotropic glutamate receptor mRNA expression in the human thalamus: absence of change in schizophrenia.
Dracheva S; Byne W; Chin B; Haroutunian V
Brain Res; 2008 Jun; 1214():23-34. PubMed ID: 18462708
[TBL] [Abstract][Full Text] [Related]
36. [Mutation analysis of GCDH gene in eight patients with glutaric aciduria type I].
Chen J; Wang ZX; Zhang JL; Yang YL; Chen J; Huang YN
Zhonghua Yi Xue Yi Chuan Xue Za Zhi; 2011 Aug; 28(4):374-8. PubMed ID: 21811973
[TBL] [Abstract][Full Text] [Related]
37. Altered hippocampal expression of glutamate receptors and transporters in GRM2 and GRM3 knockout mice.
Lyon L; Kew JN; Corti C; Harrison PJ; Burnet PW
Synapse; 2008 Nov; 62(11):842-50. PubMed ID: 18720515
[TBL] [Abstract][Full Text] [Related]
38. Potential complementation effects of two disease-associated mutations in tetrameric glutaryl-CoA dehydrogenase is due to inter subunit stability-activity counterbalance.
Ribeiro JV; Lucas TG; Bross P; Gomes CM; Henriques BJ
Biochim Biophys Acta Proteins Proteom; 2020 Jan; 1868(1):140269. PubMed ID: 31491587
[TBL] [Abstract][Full Text] [Related]
39. Induction of S100B secretion in C6 astroglial cells by the major metabolites accumulating in glutaric acidemia type I.
Quincozes-Santos A; Rosa RB; Leipnitz G; de Souza DF; Seminotti B; Wajner M; Gonçalves CA
Metab Brain Dis; 2010 Jun; 25(2):191-8. PubMed ID: 20437086
[TBL] [Abstract][Full Text] [Related]
40. Chronic ethanol upregulates NMDA and AMPA, but not kainate receptor subunit proteins in rat primary cortical cultures.
Chandler LJ; Norwood D; Sutton G
Alcohol Clin Exp Res; 1999 Feb; 23(2):363-70. PubMed ID: 10069569
[TBL] [Abstract][Full Text] [Related]
[Previous] [Next] [New Search]
