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7. Short trunk stature, brachydactyly, and platyspondyly in three sibs: a new form of brachyolmia or a new skeletal dysplasia? Tüysüz B; Ungür S Am J Med Genet A; 2003 Jun; 119A(3):375-80. PubMed ID: 12784309 [TBL] [Abstract][Full Text] [Related]
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12. Autosomal dominant brachyolmia: transient metaphyseal striations. Lim YJ; Lee HR; Kim OH; Cho TJ; Park KB Skeletal Radiol; 2017 Sep; 46(9):1297-1300. PubMed ID: 28601949 [TBL] [Abstract][Full Text] [Related]
13. TRPV4-pathy, a novel channelopathy affecting diverse systems. Dai J; Cho TJ; Unger S; Lausch E; Nishimura G; Kim OH; Superti-Furga A; Ikegawa S J Hum Genet; 2010 Jul; 55(7):400-2. PubMed ID: 20505684 [TBL] [Abstract][Full Text] [Related]
14. TRPV4 expresses in bone cell lineages and TRPV4-R616Q mutant causing Brachyolmia in human reveals "loss-of-interaction" with cholesterol. Das R; Goswami C Biochem Biophys Res Commun; 2019 Oct; 517(4):566-574. PubMed ID: 31387748 [TBL] [Abstract][Full Text] [Related]
15. The importance of conventional radiography in the mutational analysis of skeletal dysplasias (the TRPV4 mutational family). Nemec SF; Cohn DH; Krakow D; Funari VA; Rimoin DL; Lachman RS Pediatr Radiol; 2012 Jan; 42(1):15-23. PubMed ID: 21863289 [TBL] [Abstract][Full Text] [Related]
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17. Natural history of TRPV4-Related disorders: From skeletal dysplasia to neuromuscular phenotype. Ürel-Demir G; Şimşek-Kiper PÖ; Öncel İ; Utine GE; Haliloğlu G; Boduroğlu K Eur J Paediatr Neurol; 2021 May; 32():46-55. PubMed ID: 33774370 [TBL] [Abstract][Full Text] [Related]
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19. Protein informatics combined with multiple data sources enriches the clinical characterization of novel TRPV4 variant causing an intermediate skeletal dysplasia. Hines SL; Richter JE; Mohammad AN; Mahim J; Atwal PS; Caulfield TR Mol Genet Genomic Med; 2019 Mar; 7(3):e566. PubMed ID: 30693671 [TBL] [Abstract][Full Text] [Related]