323 related articles for article (PubMed ID: 24761004)
1. Neutral aminoaciduria in cystathionine β-synthase-deficient mice; an animal model of homocystinuria.
Akahoshi N; Kamata S; Kubota M; Hishiki T; Nagahata Y; Matsuura T; Yamazaki C; Yoshida Y; Yamada H; Ishizaki Y; Suematsu M; Kasahara T; Ishii I
Am J Physiol Renal Physiol; 2014 Jun; 306(12):F1462-76. PubMed ID: 24761004
[TBL] [Abstract][Full Text] [Related]
2. Abnormal Amino Acid Profiles of Blood and Cerebrospinal Fluid from Cystathionine β-Synthase-Deficient Mice, an Animal Model of Homocystinuria.
Akahoshi N; Yokoyama A; Nagata T; Miura A; Kamata S; Ishii I
Biol Pharm Bull; 2019; 42(6):1054-1057. PubMed ID: 31155583
[TBL] [Abstract][Full Text] [Related]
3. Cystathionine gamma-Lyase-deficient mice require dietary cysteine to protect against acute lethal myopathy and oxidative injury.
Ishii I; Akahoshi N; Yamada H; Nakano S; Izumi T; Suematsu M
J Biol Chem; 2010 Aug; 285(34):26358-68. PubMed ID: 20566639
[TBL] [Abstract][Full Text] [Related]
4. Genetic background conversion ameliorates semi-lethality and permits behavioral analyses in cystathionine beta-synthase-deficient mice, an animal model for hyperhomocysteinemia.
Akahoshi N; Kobayashi C; Ishizaki Y; Izumi T; Himi T; Suematsu M; Ishii I
Hum Mol Genet; 2008 Jul; 17(13):1994-2005. PubMed ID: 18364386
[TBL] [Abstract][Full Text] [Related]
5. Enzyme replacement with PEGylated cystathionine β-synthase ameliorates homocystinuria in murine model.
Bublil EM; Majtan T; Park I; Carrillo RS; Hůlková H; Krijt J; Kožich V; Kraus JP
J Clin Invest; 2016 Jun; 126(6):2372-84. PubMed ID: 27183385
[TBL] [Abstract][Full Text] [Related]
6. The effect of dietary modulation of sulfur amino acids on cystathionine β synthase-deficient mice.
Kruger WD; Gupta S
Ann N Y Acad Sci; 2016 Jan; 1363(1):80-90. PubMed ID: 26599618
[TBL] [Abstract][Full Text] [Related]
7. Methionine excess in diet induces acute lethal hepatitis in mice lacking cystathionine γ-lyase, an animal model of cystathioninuria.
Yamada H; Akahoshi N; Kamata S; Hagiya Y; Hishiki T; Nagahata Y; Matsuura T; Takano N; Mori M; Ishizaki Y; Izumi T; Kumagai Y; Kasahara T; Suematsu M; Ishii I
Free Radic Biol Med; 2012 May; 52(9):1716-26. PubMed ID: 22387178
[TBL] [Abstract][Full Text] [Related]
8. Hemizygosity of transsulfuration genes confers increased vulnerability against acetaminophen-induced hepatotoxicity in mice.
Hagiya Y; Kamata S; Mitsuoka S; Okada N; Yoshida S; Yamamoto J; Ohkubo R; Abiko Y; Yamada H; Akahoshi N; Kasahara T; Kumagai Y; Ishii I
Toxicol Appl Pharmacol; 2015 Jan; 282(2):195-206. PubMed ID: 25499718
[TBL] [Abstract][Full Text] [Related]
9. Hyperhomocysteinemia due to cystathionine beta synthase deficiency induces dysregulation of genes involved in hepatic lipid homeostasis in mice.
Hamelet J; Demuth K; Paul JL; Delabar JM; Janel N
J Hepatol; 2007 Jan; 46(1):151-9. PubMed ID: 17030070
[TBL] [Abstract][Full Text] [Related]
10. Effect of endotoxemia in mice genetically deficient in cystathionine-γ-lyase, cystathionine-β-synthase or 3-mercaptopyruvate sulfurtransferase.
Ahmad A; Gerö D; Olah G; Szabo C
Int J Mol Med; 2016 Dec; 38(6):1683-1692. PubMed ID: 27748832
[TBL] [Abstract][Full Text] [Related]
11. Taurine-deficient diet up-regulated cystathionine beta-synthase monoallele in hemizygous cystathionine beta-synthase knockout mice.
Chao WH; Reynolds RD
Nutr Res; 2009 Nov; 29(11):794-801. PubMed ID: 19932868
[TBL] [Abstract][Full Text] [Related]
12. Thioethers as markers of hydrogen sulfide production in homocystinurias.
Kožich V; Krijt J; Sokolová J; Melenovská P; Ješina P; Vozdek R; Majtán T; Kraus JP
Biochimie; 2016 Jul; 126():14-20. PubMed ID: 26791043
[TBL] [Abstract][Full Text] [Related]
13. Expression of mutant human cystathionine beta-synthase rescues neonatal lethality but not homocystinuria in a mouse model.
Wang L; Chen X; Tang B; Hua X; Klein-Szanto A; Kruger WD
Hum Mol Genet; 2005 Aug; 14(15):2201-8. PubMed ID: 15972722
[TBL] [Abstract][Full Text] [Related]
14. Hyperhomocysteinemia abrogates fasting-induced cardioprotection against ischemia/reperfusion by limiting bioavailability of hydrogen sulfide anions.
Nakano S; Ishii I; Shinmura K; Tamaki K; Hishiki T; Akahoshi N; Ida T; Nakanishi T; Kamata S; Kumagai Y; Akaike T; Fukuda K; Sano M; Suematsu M
J Mol Med (Berl); 2015 Aug; 93(8):879-89. PubMed ID: 25740079
[TBL] [Abstract][Full Text] [Related]
15. Mice deficient in cystathionine beta synthase display altered homocysteine remethylation pathway.
Alberto JM; Hamelet J; Noll C; Blaise S; Bronowicki JP; Guéant JL; Delabar JM; Janel N
Mol Genet Metab; 2007 Aug; 91(4):396-8. PubMed ID: 17562377
[TBL] [Abstract][Full Text] [Related]
16. DNA methylation status is not impaired in treated cystathionine beta-synthase (CBS) deficient patients.
Heil SG; Riksen NP; Boers GH; Smulders Y; Blom HJ
Mol Genet Metab; 2007 May; 91(1):55-60. PubMed ID: 17336565
[TBL] [Abstract][Full Text] [Related]
17. E2β stimulates ovine uterine artery endothelial cell H2S production in vitro by estrogen receptor-dependent upregulation of cystathionine β-synthase and cystathionine γ-lyase expression†.
Lechuga TJ; Qi QR; Kim T; Magness RR; Chen DB
Biol Reprod; 2019 Feb; 100(2):514-522. PubMed ID: 30277497
[TBL] [Abstract][Full Text] [Related]
18. The H2S-generating enzymes cystathionine β-synthase and cystathionine γ-lyase play a role in vascular development during normal lung alveolarization.
Madurga A; Golec A; Pozarska A; Ishii I; Mižíková I; Nardiello C; Vadász I; Herold S; Mayer K; Reichenberger F; Fehrenbach H; Seeger W; Morty RE
Am J Physiol Lung Cell Mol Physiol; 2015 Oct; 309(7):L710-24. PubMed ID: 26232299
[TBL] [Abstract][Full Text] [Related]
19. Triacylglycerol/phospholipid molecular species profiling of fatty livers and regenerated non-fatty livers in cystathionine beta-synthase-deficient mice, an animal model for homocysteinemia/homocystinuria.
Ikeda K; Kubo A; Akahoshi N; Yamada H; Miura N; Hishiki T; Nagahata Y; Matsuura T; Suematsu M; Taguchi R; Ishii I
Anal Bioanal Chem; 2011 Jun; 400(7):1853-63. PubMed ID: 21301820
[TBL] [Abstract][Full Text] [Related]
20. Cystathionine β-synthase deficiency: Of mice and men.
Kruger WD
Mol Genet Metab; 2017 Jul; 121(3):199-205. PubMed ID: 28583326
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]