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9. Are astrocytes the missing link between lack of brain aspartoacylase activity and the spongiform leukodystrophy in Canavan disease? Baslow MH; Guilfoyle DN Neurochem Res; 2009 Sep; 34(9):1523-34. PubMed ID: 19319678 [TBL] [Abstract][Full Text] [Related]
11. Upregulation of N-acetylaspartic acid resulting nitric oxide toxicity induces aspartoacylase mutations and protein interaction to cause pathophysiology seen in Canavan disease. Surendran S Med Hypotheses; 2010 Dec; 75(6):533-4. PubMed ID: 20673702 [TBL] [Abstract][Full Text] [Related]
12. A mutation of aspartoacylase gene in a Turkish patient with Canavan disease. Eke GH; Iscan A; Cece H; Calik M Genet Couns; 2012; 23(1):9-12. PubMed ID: 22611636 [TBL] [Abstract][Full Text] [Related]
13. Restoration of aspartoacylase activity in CNS neurons does not ameliorate motor deficits and demyelination in a model of Canavan disease. Klugmann M; Leichtlein CB; Symes CW; Serikawa T; Young D; During MJ Mol Ther; 2005 May; 11(5):745-53. PubMed ID: 15851013 [TBL] [Abstract][Full Text] [Related]
14. Suppressing N-Acetyl-l-Aspartate Synthesis Prevents Loss of Neurons in a Murine Model of Canavan Leukodystrophy. Sohn J; Bannerman P; Guo F; Burns T; Miers L; Croteau C; Singhal NK; McDonough JA; Pleasure D J Neurosci; 2017 Jan; 37(2):413-421. PubMed ID: 28077719 [TBL] [Abstract][Full Text] [Related]
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16. New T530C mutation in the aspartoacylase gene caused Canavan disease with no correlation between severity and N-acetylaspartate excretion. Di Pietro V; Cavallari U; Amorini AM; Lazzarino G; Longo S; Poggiani C; Cavalli P; Tavazzi B Clin Biochem; 2013 Dec; 46(18):1902-4. PubMed ID: 24036223 [TBL] [Abstract][Full Text] [Related]
17. Novel mutation in an Egyptian patient with infantile Canavan disease. Zaki OK; El Abd HS; Mohamed SA; Zayed H Metab Brain Dis; 2016 Jun; 31(3):573-7. PubMed ID: 26613958 [TBL] [Abstract][Full Text] [Related]
18. Brain Nat8l Knockdown Suppresses Spongiform Leukodystrophy in an Aspartoacylase-Deficient Canavan Disease Mouse Model. Bannerman P; Guo F; Chechneva O; Burns T; Zhu X; Wang Y; Kim B; Singhal NK; McDonough JA; Pleasure D Mol Ther; 2018 Mar; 26(3):793-800. PubMed ID: 29456021 [TBL] [Abstract][Full Text] [Related]
19. Nur7 is a nonsense mutation in the mouse aspartoacylase gene that causes spongy degeneration of the CNS. Traka M; Wollmann RL; Cerda SR; Dugas J; Barres BA; Popko B J Neurosci; 2008 Nov; 28(45):11537-49. PubMed ID: 18987190 [TBL] [Abstract][Full Text] [Related]
20. Canavan disease: from spongy degeneration to molecular analysis. Matalon R; Michals K; Kaul R J Pediatr; 1995 Oct; 127(4):511-7. PubMed ID: 7562269 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]