These tools will no longer be maintained as of December 31, 2024. Archived website can be found here. PubMed4Hh GitHub repository can be found here. Contact NLM Customer Service if you have questions.
2. Identification and allele-specific silencing of the mutant huntingtin allele in Huntington's disease patient-derived fibroblasts. van Bilsen PH; Jaspers L; Lombardi MS; Odekerken JC; Burright EN; Kaemmerer WF Hum Gene Ther; 2008 Jul; 19(7):710-9. PubMed ID: 18549309 [TBL] [Abstract][Full Text] [Related]
3. Parent-of-origin differences of mutant HTT CAG repeat instability in Huntington's disease. Aziz NA; van Belzen MJ; Coops ID; Belfroid RD; Roos RA Eur J Med Genet; 2011; 54(4):e413-8. PubMed ID: 21540131 [TBL] [Abstract][Full Text] [Related]
4. Novel allele-specific quantification methods reveal no effects of adult onset CAG repeats on HTT mRNA and protein levels. Shin A; Shin B; Shin JW; Kim KH; Atwal RS; Hope JM; Gillis T; Leszyk JD; Shaffer SA; Lee R; Kwak S; MacDonald ME; Gusella JF; Seong IS; Lee JM Hum Mol Genet; 2017 Apr; 26(7):1258-1267. PubMed ID: 28165127 [TBL] [Abstract][Full Text] [Related]
5. Making (anti-) sense out of huntingtin levels in Huntington disease. Evers MM; Schut MH; Pepers BA; Atalar M; van Belzen MJ; Faull RL; Roos RA; van Roon-Mom WM Mol Neurodegener; 2015 Apr; 10():21. PubMed ID: 25928884 [TBL] [Abstract][Full Text] [Related]
6. Is There Convincing Evidence that Intermediate Repeats in the HTT Gene Cause Huntington's Disease? Oosterloo M; Van Belzen MJ; Bijlsma EK; Roos RA J Huntingtons Dis; 2015; 4(2):141-8. PubMed ID: 26397895 [TBL] [Abstract][Full Text] [Related]
7. The number of CAG repeats within the normal allele does not influence the age of onset in Huntington's disease. Klempíř J; Zidovská J; Stochl J; Ing VK; Uhrová T; Roth J Mov Disord; 2011 Jan; 26(1):125-9. PubMed ID: 21322024 [TBL] [Abstract][Full Text] [Related]
9. Allele-specific quantitation of ATXN3 and HTT transcripts in polyQ disease models. Joachimiak P; Ciesiołka A; Kozłowska E; Świtoński PM; Figura G; Ciołak A; Adamek G; Surdyka M; Kalinowska-Pośka Ż; Figiel M; Caron NS; Hayden MR; Fiszer A BMC Biol; 2023 Feb; 21(1):17. PubMed ID: 36726088 [TBL] [Abstract][Full Text] [Related]
10. Does the Mutant CAG Expansion in Huntingtin mRNA Interfere with Exonucleolytic Cleavage of its First Exon? Liu W; Pfister EL; Kennington LA; Chase KO; Mueller C; DiFiglia M; Aronin N J Huntingtons Dis; 2016; 5(1):33-8. PubMed ID: 27003665 [TBL] [Abstract][Full Text] [Related]
11. Lack of huntingtin promotes neural stem cells differentiation into glial cells while neurons expressing huntingtin with expanded polyglutamine tracts undergo cell death. Conforti P; Camnasio S; Mutti C; Valenza M; Thompson M; Fossale E; Zeitlin S; MacDonald ME; Zuccato C; Cattaneo E Neurobiol Dis; 2013 Feb; 50():160-70. PubMed ID: 23089356 [TBL] [Abstract][Full Text] [Related]
12. Olesoxime suppresses calpain activation and mutant huntingtin fragmentation in the BACHD rat. Clemens LE; Weber JJ; Wlodkowski TT; Yu-Taeger L; Michaud M; Calaminus C; Eckert SH; Gaca J; Weiss A; Magg JC; Jansson EK; Eckert GP; Pichler BJ; Bordet T; Pruss RM; Riess O; Nguyen HP Brain; 2015 Dec; 138(Pt 12):3632-53. PubMed ID: 26490331 [TBL] [Abstract][Full Text] [Related]
14. Evidence for a predisposing background for CAG expansion leading to HTT mutation in a Chinese population. Ma M; Yang Y; Shang H; Su D; Zhang H; Ma Y; Liu Y; Tao D; Zhang S J Neurol Sci; 2010 Nov; 298(1-2):57-60. PubMed ID: 20864123 [TBL] [Abstract][Full Text] [Related]
15. A series of N-terminal epitope tagged Hdh knock-in alleles expressing normal and mutant huntingtin: their application to understanding the effect of increasing the length of normal Huntingtin's polyglutamine stretch on CAG140 mouse model pathogenesis. Zheng S; Ghitani N; Blackburn JS; Liu JP; Zeitlin SO Mol Brain; 2012 Aug; 5():28. PubMed ID: 22892315 [TBL] [Abstract][Full Text] [Related]
16. Preventing formation of toxic N-terminal huntingtin fragments through antisense oligonucleotide-mediated protein modification. Evers MM; Tran HD; Zalachoras I; Meijer OC; den Dunnen JT; van Ommen GJ; Aartsma-Rus A; van Roon-Mom WM Nucleic Acid Ther; 2014 Feb; 24(1):4-12. PubMed ID: 24380395 [TBL] [Abstract][Full Text] [Related]
17. Huntingtin gene CAG repeat size affects autism risk: Family-based and case-control association study. Piras IS; Picinelli C; Iennaco R; Baccarin M; Castronovo P; Tomaiuolo P; Cucinotta F; Ricciardello A; Turriziani L; Nanetti L; Mariotti C; Gellera C; Lintas C; Sacco R; Zuccato C; Cattaneo E; Persico AM Am J Med Genet B Neuropsychiatr Genet; 2020 Sep; 183(6):341-351. PubMed ID: 32652810 [TBL] [Abstract][Full Text] [Related]
18. Haplotype analysis of the CAG and CCG repeats in 21 Brazilian families with Huntington's disease. Agostinho Lde A; Rocha CF; Medina-Acosta E; Barboza HN; da Silva AF; Pereira SP; da Silva Idos S; Paradela ER; Figueiredo AL; Nogueira Ede M; Alvarenga RM; Hernan Cabello P; dos Santos SR; Paiva CL J Hum Genet; 2012 Dec; 57(12):796-803. PubMed ID: 23051704 [TBL] [Abstract][Full Text] [Related]
19. A pathogenic mechanism in Huntington's disease involves small CAG-repeated RNAs with neurotoxic activity. Bañez-Coronel M; Porta S; Kagerbauer B; Mateu-Huertas E; Pantano L; Ferrer I; Guzmán M; Estivill X; Martí E PLoS Genet; 2012; 8(2):e1002481. PubMed ID: 22383888 [TBL] [Abstract][Full Text] [Related]
20. Msh2 acts in medium-spiny striatal neurons as an enhancer of CAG instability and mutant huntingtin phenotypes in Huntington's disease knock-in mice. Kovalenko M; Dragileva E; St Claire J; Gillis T; Guide JR; New J; Dong H; Kucherlapati R; Kucherlapati MH; Ehrlich ME; Lee JM; Wheeler VC PLoS One; 2012; 7(9):e44273. PubMed ID: 22970194 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]