These tools will no longer be maintained as of December 31, 2024. Archived website can be found here. PubMed4Hh GitHub repository can be found here. Contact NLM Customer Service if you have questions.
269 related articles for article (PubMed ID: 25065395)
1. Roscovitine is a proteostasis regulator that corrects the trafficking defect of F508del-CFTR by a CDK-independent mechanism. Norez C; Vandebrouck C; Bertrand J; Noel S; Durieu E; Oumata N; Galons H; Antigny F; Chatelier A; Bois P; Meijer L; Becq F Br J Pharmacol; 2014 Nov; 171(21):4831-49. PubMed ID: 25065395 [TBL] [Abstract][Full Text] [Related]
2. The anion transporter SLC26A9 localizes to tight junctions and is degraded by the proteasome when co-expressed with F508del-CFTR. Sato Y; Thomas DY; Hanrahan JW J Biol Chem; 2019 Nov; 294(48):18269-18284. PubMed ID: 31645438 [TBL] [Abstract][Full Text] [Related]
3. Proteasome-dependent pharmacological rescue of cystic fibrosis transmembrane conductance regulator revealed by mutation of glycine 622. Norez C; Bilan F; Kitzis A; Mettey Y; Becq F J Pharmacol Exp Ther; 2008 Apr; 325(1):89-99. PubMed ID: 18230692 [TBL] [Abstract][Full Text] [Related]
4. Maintaining low Ca2+ level in the endoplasmic reticulum restores abnormal endogenous F508del-CFTR trafficking in airway epithelial cells. Norez C; Antigny F; Becq F; Vandebrouck C Traffic; 2006 May; 7(5):562-73. PubMed ID: 16643279 [TBL] [Abstract][Full Text] [Related]
5. Calumenin contributes to ER-Ca Philippe R; Antigny F; Buscaglia P; Norez C; Huguet F; Castelbou C; Trouvé P; Becq F; Frieden M; Férec C; Mignen O Cell Calcium; 2017 Mar; 62():47-59. PubMed ID: 28189267 [TBL] [Abstract][Full Text] [Related]
7. Augmentation of Cystic Fibrosis Transmembrane Conductance Regulator Function in Human Bronchial Epithelial Cells via SLC6A14-Dependent Amino Acid Uptake. Implications for Treatment of Cystic Fibrosis. Ahmadi S; Wu YS; Li M; Ip W; Lloyd-Kuzik A; Di Paola M; Du K; Xia S; Lew A; Bozoky Z; Forman-Kay J; Bear CE; Gonska T Am J Respir Cell Mol Biol; 2019 Dec; 61(6):755-764. PubMed ID: 31189070 [TBL] [Abstract][Full Text] [Related]
8. Trimethylangelicin promotes the functional rescue of mutant F508del CFTR protein in cystic fibrosis airway cells. Favia M; Mancini MT; Bezzerri V; Guerra L; Laselva O; Abbattiscianni AC; Debellis L; Reshkin SJ; Gambari R; Cabrini G; Casavola V Am J Physiol Lung Cell Mol Physiol; 2014 Jul; 307(1):L48-61. PubMed ID: 24816489 [TBL] [Abstract][Full Text] [Related]
10. Probing conformational rescue induced by a chemical corrector of F508del-cystic fibrosis transmembrane conductance regulator (CFTR) mutant. Yu W; Kim Chiaw P; Bear CE J Biol Chem; 2011 Jul; 286(28):24714-25. PubMed ID: 21602569 [TBL] [Abstract][Full Text] [Related]
11. Impact of the F508del mutation on ovine CFTR, a Cl- channel with enhanced conductance and ATP-dependent gating. Cai Z; Palmai-Pallag T; Khuituan P; Mutolo MJ; Boinot C; Liu B; Scott-Ward TS; Callebaut I; Harris A; Sheppard DN J Physiol; 2015 Jun; 593(11):2427-46. PubMed ID: 25763566 [TBL] [Abstract][Full Text] [Related]
12. Unravelling the Regions of Mutant F508del-CFTR More Susceptible to the Action of Four Cystic Fibrosis Correctors. Amico G; Brandas C; Moran O; Baroni D Int J Mol Sci; 2019 Nov; 20(21):. PubMed ID: 31683989 [TBL] [Abstract][Full Text] [Related]
13. Rescue of F508del-CFTR by RXR motif inactivation triggers proteome modulation associated with the unfolded protein response. Gomes-Alves P; Couto F; Pesquita C; Coelho AV; Penque D Biochim Biophys Acta; 2010 Apr; 1804(4):856-65. PubMed ID: 20044041 [TBL] [Abstract][Full Text] [Related]
14. Regulation of CFTR Biogenesis by the Proteostatic Network and Pharmacological Modulators. Estabrooks S; Brodsky JL Int J Mol Sci; 2020 Jan; 21(2):. PubMed ID: 31936842 [TBL] [Abstract][Full Text] [Related]
15. Phosphorylation of the Chaperone-Like HspB5 Rescues Trafficking and Function of F508del-CFTR. Degrugillier F; Aissat A; Prulière-Escabasse V; Bizard L; Simonneau B; Decrouy X; Jiang C; Rotin D; Fanen P; Simon S Int J Mol Sci; 2020 Jul; 21(14):. PubMed ID: 32650630 [TBL] [Abstract][Full Text] [Related]
16. Pharmacological Correction of Cystic Fibrosis: Molecular Mechanisms at the Plasma Membrane to Augment Mutant CFTR Function. Arora K; Naren AP Curr Drug Targets; 2016; 17(11):1275-81. PubMed ID: 26648081 [TBL] [Abstract][Full Text] [Related]
17. Restoration of R117H CFTR folding and function in human airway cells through combination treatment with VX-809 and VX-770. Gentzsch M; Ren HY; Houck SA; Quinney NL; Cholon DM; Sopha P; Chaudhry IG; Das J; Dokholyan NV; Randell SH; Cyr DM Am J Physiol Lung Cell Mol Physiol; 2016 Sep; 311(3):L550-9. PubMed ID: 27402691 [TBL] [Abstract][Full Text] [Related]
18. Identification of a NBD1-binding pharmacological chaperone that corrects the trafficking defect of F508del-CFTR. Sampson HM; Robert R; Liao J; Matthes E; Carlile GW; Hanrahan JW; Thomas DY Chem Biol; 2011 Feb; 18(2):231-42. PubMed ID: 21338920 [TBL] [Abstract][Full Text] [Related]
19. Partial rescue of F508del-cystic fibrosis transmembrane conductance regulator channel gating with modest improvement of protein processing, but not stability, by a dual-acting small molecule. Liu J; Bihler H; Farinha CM; Awatade NT; Romão AM; Mercadante D; Cheng Y; Musisi I; Jantarajit W; Wang Y; Cai Z; Amaral MD; Mense M; Sheppard DN Br J Pharmacol; 2018 Apr; 175(7):1017-1038. PubMed ID: 29318594 [TBL] [Abstract][Full Text] [Related]
20. Unravelling druggable signalling networks that control F508del-CFTR proteostasis. Hegde RN; Parashuraman S; Iorio F; Ciciriello F; Capuani F; Carissimo A; Carrella D; Belcastro V; Subramanian A; Bounti L; Persico M; Carlile G; Galietta L; Thomas DY; Di Bernardo D; Luini A Elife; 2015 Dec; 4():. PubMed ID: 26701908 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]