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3. Pyruvate dehydrogenase deficiency caused by deletion of a 7-bp repeat sequence in the E1 alpha gene. Dahl HH; Maragos C; Brown RM; Hansen LL; Brown GK Am J Hum Genet; 1990 Aug; 47(2):286-93. PubMed ID: 2378353 [TBL] [Abstract][Full Text] [Related]
4. Mutation of the E1 alpha subunit of the pyruvate dehydrogenase complex, in relation to heterogeneity. Kitano A; Endo F; Matsuda I; Miyabayashi S; Dahl HH J Inherit Metab Dis; 1989; 12(2):97-107. PubMed ID: 2502681 [TBL] [Abstract][Full Text] [Related]
5. Mutation of E1 alpha gene in a female patient with pyruvate dehydrogenase deficiency due to rapid degradation of E1 protein. Ito M; Huq AH; Naito E; Saijo T; Takeda E; Kuroda Y J Inherit Metab Dis; 1992; 15(6):848-56. PubMed ID: 1338114 [TBL] [Abstract][Full Text] [Related]
6. Detection of a homozygous four base pair deletion in the protein X gene in a case of pyruvate dehydrogenase complex deficiency. Ling M; McEachern G; Seyda A; MacKay N; Scherer SW; Bratinova S; Beatty B; Giovannucci-Uzielli ML; Robinson BH Hum Mol Genet; 1998 Mar; 7(3):501-5. PubMed ID: 9467010 [TBL] [Abstract][Full Text] [Related]
7. Mutations in the X-linked E1 alpha subunit of pyruvate dehydrogenase leading to deficiency of the pyruvate dehydrogenase complex. Chun K; MacKay N; Petrova-Benedict R; Robinson BH Hum Mol Genet; 1993 Apr; 2(4):449-54. PubMed ID: 8504306 [TBL] [Abstract][Full Text] [Related]
8. Pyruvate dehydrogenase deficiency in a male caused by a point mutation (F205L) in the E1 alpha subunit. Dahl HH; Brown GK Hum Mutat; 1994; 3(2):152-5. PubMed ID: 8199595 [No Abstract] [Full Text] [Related]
9. Pyruvate dehydrogenase deficiency caused by a four-nucleotide insertion in the E1 alpha subunit gene. Naito E; Ito M; Yokota I; Matsuda J; Yara A; Kuroda Y Hum Mol Genet; 1994 Jul; 3(7):1193-4. PubMed ID: 7981697 [No Abstract] [Full Text] [Related]
10. Pyruvate dehydrogenase deficiency caused by a 33 base pair duplication in the PDH E1 alpha subunit. Hansen LL; Horn N; Dahl HH; Kruse TA Hum Mol Genet; 1994 Jun; 3(6):1021-2. PubMed ID: 7545958 [No Abstract] [Full Text] [Related]
11. A mutation in the E1 alpha subunit of pyruvate dehydrogenase associated with variable expression of pyruvate dehydrogenase complex deficiency. Wexler ID; Hemalatha SG; Liu TC; Berry SA; Kerr DS; Patel MS Pediatr Res; 1992 Aug; 32(2):169-74. PubMed ID: 1508605 [TBL] [Abstract][Full Text] [Related]
12. Mutations in the X-linked E1 alpha subunit of pyruvate dehydrogenase: exon skipping, insertion of duplicate sequence, and missense mutations leading to the deficiency of the pyruvate dehydrogenase complex. Chun K; MacKay N; Petrova-Benedict R; Federico A; Fois A; Cole DE; Robertson E; Robinson BH Am J Hum Genet; 1995 Mar; 56(3):558-69. PubMed ID: 7887409 [TBL] [Abstract][Full Text] [Related]
13. Pyruvate dehydrogenase deficiency in a female due to a 4 base pair deletion in exon 10 of the E1 alpha gene. Lissens W; Desguerre I; Benelli C; Marsac C; Fouque F; Haenggeli C; Ponsot G; Seneca S; Liebaers I; De Meirleir L Hum Mol Genet; 1995 Feb; 4(2):307-8. PubMed ID: 7757085 [No Abstract] [Full Text] [Related]
14. Mutations and polymorphisms in the pyruvate dehydrogenase E1 alpha gene. Dahl HH; Brown GK; Brown RM; Hansen LL; Kerr DS; Wexler ID; Patel MS; De Meirleir L; Lissens W; Chun K Hum Mutat; 1992; 1(2):97-102. PubMed ID: 1301207 [TBL] [Abstract][Full Text] [Related]
15. Defective gene in lactic acidosis: abnormal pyruvate dehydrogenase E1 alpha-subunit caused by a frame shift. Endo H; Hasegawa K; Narisawa K; Tada K; Kagawa Y; Ohta S Am J Hum Genet; 1989 Mar; 44(3):358-64. PubMed ID: 2537010 [TBL] [Abstract][Full Text] [Related]
16. Characterization of the mutations in three patients with pyruvate dehydrogenase E1 alpha deficiency. Hansen LL; Brown GK; Kirby DM; Dahl HH J Inherit Metab Dis; 1991; 14(2):140-51. PubMed ID: 1909401 [TBL] [Abstract][Full Text] [Related]
17. Mutations in the X-linked pyruvate dehydrogenase (E1) alpha subunit gene (PDHA1) in patients with a pyruvate dehydrogenase complex deficiency. Lissens W; De Meirleir L; Seneca S; Liebaers I; Brown GK; Brown RM; Ito M; Naito E; Kuroda Y; Kerr DS; Wexler ID; Patel MS; Robinson BH; Seyda A Hum Mutat; 2000; 15(3):209-19. PubMed ID: 10679936 [TBL] [Abstract][Full Text] [Related]
18. An amino acid substitution in the pyruvate dehydrogenase E1 alpha gene, affecting mitochondrial import of the precursor protein. Takakubo F; Cartwright P; Hoogenraad N; Thorburn DR; Collins F; Lithgow T; Dahl HH Am J Hum Genet; 1995 Oct; 57(4):772-80. PubMed ID: 7573035 [TBL] [Abstract][Full Text] [Related]
19. Pyruvate dehydrogenase deficiency due to a 20-bp deletion in exon II of the pyruvate dehydrogenase (PDH) E1 alpha gene. Chun K; MacKay N; Petrova-Benedict R; Robinson BH Am J Hum Genet; 1991 Aug; 49(2):414-20. PubMed ID: 1907799 [TBL] [Abstract][Full Text] [Related]
20. Mutation analysis of the pyruvate dehydrogenase E1 alpha gene in eight patients with a pyruvate dehydrogenase complex deficiency. Lissens W; De Meirleir L; Seneca S; Benelli C; Marsac C; Poll-The BT; Briones P; Ruitenbeek W; van Diggelen O; Chaigne D; Ramaekers V; Liebaers I Hum Mutat; 1996; 7(1):46-51. PubMed ID: 8664900 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]