These tools will no longer be maintained as of December 31, 2024. Archived website can be found here. PubMed4Hh GitHub repository can be found here. Contact NLM Customer Service if you have questions.
324 related articles for article (PubMed ID: 25191843)
1. Transcriptome profiling of spinal muscular atrophy motor neurons derived from mouse embryonic stem cells. Maeda M; Harris AW; Kingham BF; Lumpkin CJ; Opdenaker LM; McCahan SM; Wang W; Butchbach ME PLoS One; 2014; 9(9):e106818. PubMed ID: 25191843 [TBL] [Abstract][Full Text] [Related]
2. The human centromeric survival motor neuron gene (SMN2) rescues embryonic lethality in Smn(-/-) mice and results in a mouse with spinal muscular atrophy. Monani UR; Sendtner M; Coovert DD; Parsons DW; Andreassi C; Le TT; Jablonka S; Schrank B; Rossoll W; Prior TW; Morris GE; Burghes AH Hum Mol Genet; 2000 Feb; 9(3):333-9. PubMed ID: 10655541 [TBL] [Abstract][Full Text] [Related]
3. Development and characterization of an SMN2-based intermediate mouse model of Spinal Muscular Atrophy. Cobb MS; Rose FF; Rindt H; Glascock JJ; Shababi M; Miller MR; Osman EY; Yen PF; Garcia ML; Martin BR; Wetz MJ; Mazzasette C; Feng Z; Ko CP; Lorson CL Hum Mol Genet; 2013 May; 22(9):1843-55. PubMed ID: 23390132 [TBL] [Abstract][Full Text] [Related]
4. A Perturbed MicroRNA Expression Pattern Characterizes Embryonic Neural Stem Cells Derived from a Severe Mouse Model of Spinal Muscular Atrophy (SMA). Luchetti A; Ciafrè SA; Murdocca M; Malgieri A; Masotti A; Sanchez M; Farace MG; Novelli G; Sangiuolo F Int J Mol Sci; 2015 Aug; 16(8):18312-27. PubMed ID: 26258776 [TBL] [Abstract][Full Text] [Related]
5. Spinal motor neuron loss occurs through a p53-and-p21-independent mechanism in the Smn Reedich EJ; Kalski M; Armijo N; Cox GA; DiDonato CJ Exp Neurol; 2021 Mar; 337():113587. PubMed ID: 33382987 [TBL] [Abstract][Full Text] [Related]
6. Modeling the differential phenotypes of spinal muscular atrophy with high-yield generation of motor neurons from human induced pluripotent stem cells. Lin X; Li JJ; Qian WJ; Zhang QJ; Wang ZF; Lu YQ; Dong EL; He J; Wang N; Ma LX; Chen WJ Oncotarget; 2017 Jun; 8(26):42030-42042. PubMed ID: 28159932 [TBL] [Abstract][Full Text] [Related]
7. A SMN2 Splicing Modifier Rescues the Disease Phenotypes in an In Vitro Human Spinal Muscular Atrophy Model. Son YS; Choi K; Lee H; Kwon O; Jung KB; Cho S; Baek J; Son B; Kang SM; Kang M; Yoon J; Shen H; Lee S; Oh JH; Lee HA; Lee MO; Cho HS; Jung CR; Kim J; Cho S; Son MY Stem Cells Dev; 2019 Apr; 28(7):438-453. PubMed ID: 30667343 [TBL] [Abstract][Full Text] [Related]
8. Established Stem Cell Model of Spinal Muscular Atrophy Is Applicable in the Evaluation of the Efficacy of Thyrotropin-Releasing Hormone Analog. Ohuchi K; Funato M; Kato Z; Seki J; Kawase C; Tamai Y; Ono Y; Nagahara Y; Noda Y; Kameyama T; Ando S; Tsuruma K; Shimazawa M; Hara H; Kaneko H Stem Cells Transl Med; 2016 Feb; 5(2):152-63. PubMed ID: 26683872 [TBL] [Abstract][Full Text] [Related]
9. Peripheral SMN restoration is essential for long-term rescue of a severe spinal muscular atrophy mouse model. Hua Y; Sahashi K; Rigo F; Hung G; Horev G; Bennett CF; Krainer AR Nature; 2011 Oct; 478(7367):123-6. PubMed ID: 21979052 [TBL] [Abstract][Full Text] [Related]
10. Reduced survival of motor neuron (SMN) protein in motor neuronal progenitors functions cell autonomously to cause spinal muscular atrophy in model mice expressing the human centromeric (SMN2) gene. Park GH; Maeno-Hikichi Y; Awano T; Landmesser LT; Monani UR J Neurosci; 2010 Sep; 30(36):12005-19. PubMed ID: 20826664 [TBL] [Abstract][Full Text] [Related]
11. ZPR1 prevents R-loop accumulation, upregulates SMN2 expression and rescues spinal muscular atrophy. Kannan A; Jiang X; He L; Ahmad S; Gangwani L Brain; 2020 Jan; 143(1):69-93. PubMed ID: 31828288 [TBL] [Abstract][Full Text] [Related]
12. SMN deficiency alters Nrxn2 expression and splicing in zebrafish and mouse models of spinal muscular atrophy. See K; Yadav P; Giegerich M; Cheong PS; Graf M; Vyas H; Lee SG; Mathavan S; Fischer U; Sendtner M; Winkler C Hum Mol Genet; 2014 Apr; 23(7):1754-70. PubMed ID: 24218366 [TBL] [Abstract][Full Text] [Related]
14. SAHA ameliorates the SMA phenotype in two mouse models for spinal muscular atrophy. Riessland M; Ackermann B; Förster A; Jakubik M; Hauke J; Garbes L; Fritzsche I; Mende Y; Blumcke I; Hahnen E; Wirth B Hum Mol Genet; 2010 Apr; 19(8):1492-506. PubMed ID: 20097677 [TBL] [Abstract][Full Text] [Related]
15. Neuronal SMN expression corrects spinal muscular atrophy in severe SMA mice while muscle-specific SMN expression has no phenotypic effect. Gavrilina TO; McGovern VL; Workman E; Crawford TO; Gogliotti RG; DiDonato CJ; Monani UR; Morris GE; Burghes AH Hum Mol Genet; 2008 Apr; 17(8):1063-75. PubMed ID: 18178576 [TBL] [Abstract][Full Text] [Related]
16. Therapeutics development for spinal muscular atrophy. Sumner CJ NeuroRx; 2006 Apr; 3(2):235-45. PubMed ID: 16554261 [TBL] [Abstract][Full Text] [Related]
17. Neurocalcin Delta Suppression Protects against Spinal Muscular Atrophy in Humans and across Species by Restoring Impaired Endocytosis. Riessland M; Kaczmarek A; Schneider S; Swoboda KJ; Löhr H; Bradler C; Grysko V; Dimitriadi M; Hosseinibarkooie S; Torres-Benito L; Peters M; Upadhyay A; Biglari N; Kröber S; Hölker I; Garbes L; Gilissen C; Hoischen A; Nürnberg G; Nürnberg P; Walter M; Rigo F; Bennett CF; Kye MJ; Hart AC; Hammerschmidt M; Kloppenburg P; Wirth B Am J Hum Genet; 2017 Feb; 100(2):297-315. PubMed ID: 28132687 [TBL] [Abstract][Full Text] [Related]
18. hnRNP M facilitates exon 7 inclusion of SMN2 pre-mRNA in spinal muscular atrophy by targeting an enhancer on exon 7. Cho S; Moon H; Loh TJ; Oh HK; Cho S; Choy HE; Song WK; Chun JS; Zheng X; Shen H Biochim Biophys Acta; 2014; 1839(4):306-15. PubMed ID: 24533984 [TBL] [Abstract][Full Text] [Related]
19. Normalization of Patient-Identified Plasma Biomarkers in SMNΔ7 Mice following Postnatal SMN Restoration. Arnold WD; Duque S; Iyer CC; Zaworski P; McGovern VL; Taylor SJ; von Herrmann KM; Kobayashi DT; Chen KS; Kolb SJ; Paushkin SV; Burghes AH PLoS One; 2016; 11(12):e0167077. PubMed ID: 27907033 [TBL] [Abstract][Full Text] [Related]
20. Calpain Inhibition Increases SMN Protein in Spinal Cord Motoneurons and Ameliorates the Spinal Muscular Atrophy Phenotype in Mice. de la Fuente S; Sansa A; Periyakaruppiah A; Garcera A; Soler RM Mol Neurobiol; 2019 Jun; 56(6):4414-4427. PubMed ID: 30327977 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]