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4. Corrector therapies (with or without potentiators) for people with cystic fibrosis with class II CFTR gene variants (most commonly F508del). Heneghan M; Southern KW; Murphy J; Sinha IP; Nevitt SJ Cochrane Database Syst Rev; 2023 Nov; 11(11):CD010966. PubMed ID: 37983082 [TBL] [Abstract][Full Text] [Related]
5. Long-Term Safety and Efficacy of Elexacaftor/Tezacaftor/Ivacaftor in Children Aged ⩾6 Years with Cystic Fibrosis and at Least One Wainwright C; McColley SA; McNally P; Powers M; Ratjen F; Rayment JH; Retsch-Bogart G; Roesch E; Ahluwalia N; Chin A; Chu C; Lu M; Menon P; Waltz D; Weinstock T; Zelazoski L; Davies JC Am J Respir Crit Care Med; 2023 Jul; 208(1):68-78. PubMed ID: 37154609 [No Abstract] [Full Text] [Related]
6. Lumacaftor/Ivacaftor in Patients Aged 6-11 Years with Cystic Fibrosis and Homozygous for F508del-CFTR. Milla CE; Ratjen F; Marigowda G; Liu F; Waltz D; Rosenfeld M; Am J Respir Crit Care Med; 2017 Apr; 195(7):912-920. PubMed ID: 27805836 [TBL] [Abstract][Full Text] [Related]
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12. Cystic Fibrosis: A Review. Ong T; Ramsey BW JAMA; 2023 Jun; 329(21):1859-1871. PubMed ID: 37278811 [TBL] [Abstract][Full Text] [Related]
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20. Correlation between Ivacaftor-induced CFTR Activation in Airway Epithelial Cells and Improved Lung Function: A Proof-of-Concept Study. Debley JS; Barrow KA; Rich LM; Singh P; McKone EF; Nichols DP Ann Am Thorac Soc; 2020 Aug; 17(8):1024-1027. PubMed ID: 32421352 [No Abstract] [Full Text] [Related] [Next] [New Search]