114 related articles for article (PubMed ID: 25541102)
1. Shotgun proteomics reveals possible mechanisms for cognitive impairment in Mucopolysaccharidosis I mice.
Baldo G; Lorenzini DM; Santos DS; Mayer FQ; Vitry S; Bigou S; Heard JM; Matte U; Giugliani R
Mol Genet Metab; 2015 Feb; 114(2):138-45. PubMed ID: 25541102
[TBL] [Abstract][Full Text] [Related]
2. Proteomic analysis of mucopolysaccharidosis I mouse brain with two-dimensional polyacrylamide gel electrophoresis.
Ou L; Przybilla MJ; Whitley CB
Mol Genet Metab; 2017; 120(1-2):101-110. PubMed ID: 27742266
[TBL] [Abstract][Full Text] [Related]
3. Cathepsin B-associated Activation of Amyloidogenic Pathway in Murine Mucopolysaccharidosis Type I Brain Cortex.
Viana GM; Gonzalez EA; Alvarez MMP; Cavalheiro RP; do Nascimento CC; Baldo G; D'Almeida V; de Lima MA; Pshezhetsky AV; Nader HB
Int J Mol Sci; 2020 Feb; 21(4):. PubMed ID: 32093427
[TBL] [Abstract][Full Text] [Related]
4. Evidence of a progressive motor dysfunction in Mucopolysaccharidosis type I mice.
Baldo G; Mayer FQ; Martinelli B; Dilda A; Meyer F; Ponder KP; Giugliani R; Matte U
Behav Brain Res; 2012 Jul; 233(1):169-75. PubMed ID: 22580166
[TBL] [Abstract][Full Text] [Related]
5. Progressive heart disease in mucopolysaccharidosis type I mice may be mediated by increased cathepsin B activity.
Baldo G; Tavares AM; Gonzalez E; Poletto E; Mayer FQ; Matte UD; Giugliani R
Cardiovasc Pathol; 2017; 27():45-50. PubMed ID: 28104572
[TBL] [Abstract][Full Text] [Related]
6. Alterations of membrane lipids and in gene expression of ganglioside metabolism in different brain structures in a mouse model of mucopolysaccharidosis type I (MPS I).
Kreutz F; dos Santos Petry F; Camassola M; Schein V; Guma FC; Nardi NB; Trindade VM
Gene; 2013 Sep; 527(1):109-14. PubMed ID: 23774686
[TBL] [Abstract][Full Text] [Related]
7. Intracerebroventricular transplantation of human bone marrow-derived multipotent progenitor cells in an immunodeficient mouse model of mucopolysaccharidosis type I (MPS-I).
Nan Z; Shekels L; Ryabinin O; Evavold C; Nelson MS; Khan SA; Deans RJ; Mays RW; Low WC; Gupta P
Cell Transplant; 2012; 21(7):1577-93. PubMed ID: 22472595
[TBL] [Abstract][Full Text] [Related]
8. High-dose enzyme replacement therapy in murine Hurler syndrome.
Ou L; Herzog T; Koniar BL; Gunther R; Whitley CB
Mol Genet Metab; 2014 Feb; 111(2):116-22. PubMed ID: 24100243
[TBL] [Abstract][Full Text] [Related]
9. Enzyme replacement therapy started at birth improves outcome in difficult-to-treat organs in mucopolysaccharidosis I mice.
Baldo G; Mayer FQ; Martinelli BZ; de Carvalho TG; Meyer FS; de Oliveira PG; Meurer L; Tavares A; Matte U; Giugliani R
Mol Genet Metab; 2013 May; 109(1):33-40. PubMed ID: 23562162
[TBL] [Abstract][Full Text] [Related]
10. Residual α-L-iduronidase activity in fibroblasts of mild to severe Mucopolysaccharidosis type I patients.
Oussoren E; Keulemans J; van Diggelen OP; Oemardien LF; Timmermans RG; van der Ploeg AT; Ruijter GJ
Mol Genet Metab; 2013 Aug; 109(4):377-81. PubMed ID: 23786846
[TBL] [Abstract][Full Text] [Related]
11. Progression of multiple behavioral deficits with various ages of onset in a murine model of Hurler syndrome.
Pan D; Sciascia A; Vorhees CV; Williams MT
Brain Res; 2008 Jan; 1188():241-53. PubMed ID: 18022143
[TBL] [Abstract][Full Text] [Related]
12. Glial fibrillary acidic protein-expressing neural progenitors give rise to immature neurons via early intermediate progenitors expressing both glial fibrillary acidic protein and neuronal markers in the adult hippocampus.
Liu Y; Namba T; Liu J; Suzuki R; Shioda S; Seki T
Neuroscience; 2010 Mar; 166(1):241-51. PubMed ID: 20026190
[TBL] [Abstract][Full Text] [Related]
13. [The development of cognitive functions in children with Hurler phenotype mucopolysaccharidosis type I on enzyme replacement therapy with laronidase].
Biernacka M; Jakubowska-Winecka A; Tylki-Szymańska A
Pediatr Endocrinol Diabetes Metab; 2010; 16(4):249-54. PubMed ID: 21447265
[TBL] [Abstract][Full Text] [Related]
14. Neonatal gene therapy of MPS I mice by intravenous injection of a lentiviral vector.
Kobayashi H; Carbonaro D; Pepper K; Petersen D; Ge S; Jackson H; Shimada H; Moats R; Kohn DB
Mol Ther; 2005 May; 11(5):776-89. PubMed ID: 15851016
[TBL] [Abstract][Full Text] [Related]
15. Evidence that glycosaminoglycan storage and collagen deposition in the cauda epididymidis does not impair sperm viability in the Mucopolysaccharidosis type I mouse model.
do Nascimento CC; Aguiar O; Viana GM; D Almeida V
Reprod Fertil Dev; 2020 Feb; 32(3):304-312. PubMed ID: 31679559
[TBL] [Abstract][Full Text] [Related]
16. Mucopolysaccharidosis type I.
Wraith JE; Jones S
Pediatr Endocrinol Rev; 2014 Sep; 12 Suppl 1():102-6. PubMed ID: 25345091
[TBL] [Abstract][Full Text] [Related]
17. Mucopolysaccharidosis type V. (Scheie syndrome). A postmortem study by multidisciplinary techniques with emphasis on the brain.
Dekaban AS; Constantopoulos G; Herman MM; Steusing JK
Arch Pathol Lab Med; 1976 May; 100(5):237-45. PubMed ID: 817693
[TBL] [Abstract][Full Text] [Related]
18. Lipid composition of whole brain and cerebellum in Hurler syndrome (MPS IH) mice.
Heinecke KA; Peacock BN; Blazar BR; Tolar J; Seyfried TN
Neurochem Res; 2011 Sep; 36(9):1669-76. PubMed ID: 21253856
[TBL] [Abstract][Full Text] [Related]
19. Glycosaminoglycan fragments as a measure of disease burden in the mucopolysaccharidosis type I mouse.
Saville JT; McDermott BK; Fuller M
Mol Genet Metab; 2018 Feb; 123(2):112-117. PubMed ID: 29273385
[TBL] [Abstract][Full Text] [Related]
20. Attenuated plasticity in neurons and astrocytes in the mouse model of Sanfilippo syndrome type B.
Li HH; Zhao HZ; Neufeld EF; Cai Y; Gómez-Pinilla F
J Neurosci Res; 2002 Jul; 69(1):30-8. PubMed ID: 12111813
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]