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2. Perrault syndrome with neurological features in a compound heterozygote for two TWNK mutations: overlap of TWNK-related recessive disorders. Domínguez-Ruiz M; García-Martínez A; Corral-Juan M; Pérez-Álvarez ÁI; Plasencia AM; Villamar M; Moreno-Pelayo MA; Matilla-Dueñas A; Menéndez-González M; Del Castillo I J Transl Med; 2019 Aug; 17(1):290. PubMed ID: 31455392 [TBL] [Abstract][Full Text] [Related]
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4. Perrault syndrome with Marfanoid habitus in two siblings. Jacob JJ; Paul TV; Mathews SS; Thomas N J Pediatr Adolesc Gynecol; 2007 Oct; 20(5):305-8. PubMed ID: 17868898 [TBL] [Abstract][Full Text] [Related]
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6. Perrault syndrome with amenorrhea, infertility, Tarlov cyst, and degenerative disc. Al-Jaroudi D; Enabi S; AlThagafi MS Gynecol Endocrinol; 2019 Dec; 35(12):1037-1039. PubMed ID: 31274036 [TBL] [Abstract][Full Text] [Related]
7. Genotype and phenotype heterogeneity in perrault syndrome. Kim MJ; Kim SJ; Kim J; Chae H; Kim M; Kim Y J Pediatr Adolesc Gynecol; 2013 Feb; 26(1):e25-7. PubMed ID: 23332201 [TBL] [Abstract][Full Text] [Related]
8. Marfanoid habitus is a nonspecific feature of Perrault syndrome. Zerkaoui M; Demain LAM; Cherkaoui Jaouad I; Ratbi I; Amjoud K; Urquhart JE; O'Sullivan J; Newman WG; Sefiani A Clin Dysmorphol; 2017 Oct; 26(4):200-204. PubMed ID: 28832386 [TBL] [Abstract][Full Text] [Related]
9. Perrault syndrome: further evidence for genetic heterogeneity. Jenkinson EM; Clayton-Smith J; Mehta S; Bennett C; Reardon W; Green A; Pearce SH; De Michele G; Conway GS; Cilliers D; Moreton N; Davis JR; Trump D; Newman WG J Neurol; 2012 May; 259(5):974-6. PubMed ID: 22037954 [No Abstract] [Full Text] [Related]
10. A known pathogenic variant in the essential mitochondrial translation gene RMND1 causes a Perrault-like syndrome with renal defects. Demain LAM; Antunes D; O'Sullivan J; Bhaskhar SS; O'Keefe RT; Newman WG Clin Genet; 2018 Aug; 94(2):276-277. PubMed ID: 29671881 [No Abstract] [Full Text] [Related]
11. New insights into Perrault syndrome, a clinically and genetically heterogeneous disorder. Faridi R; Rea A; Fenollar-Ferrer C; O'Keefe RT; Gu S; Munir Z; Khan AA; Riazuddin S; Hoa M; Naz S; Newman WG; Friedman TB Hum Genet; 2022 Apr; 141(3-4):805-819. PubMed ID: 34338890 [TBL] [Abstract][Full Text] [Related]
12. A homozygous missense variant in HSD17B4 identified in a consanguineous Chinese Han family with type II Perrault syndrome. Chen K; Yang K; Luo SS; Chen C; Wang Y; Wang YX; Li DK; Yang YJ; Tang YL; Liu FT; Wang J; Wu JJ; Sun YM BMC Med Genet; 2017 Aug; 18(1):91. PubMed ID: 28830375 [TBL] [Abstract][Full Text] [Related]
13. LARS2-Perrault syndrome: a new case report and literature review. Carminho-Rodrigues MT; Klee P; Laurent S; Guipponi M; Abramowicz M; Cao-van H; Guinand N; Paoloni-Giacobino A BMC Med Genet; 2020 May; 21(1):109. PubMed ID: 32423379 [TBL] [Abstract][Full Text] [Related]
14. Serendipity or prepared mind? Recollections of the KOP translocation (1967) and of one form of Perrault syndrome. Opitz JM Am J Med Genet C Semin Med Genet; 2014 Dec; 166C(4):387-96. PubMed ID: 25424868 [TBL] [Abstract][Full Text] [Related]
15. Genomic sequencing highlights the diverse molecular causes of Perrault syndrome: a peroxisomal disorder (PEX6), metabolic disorders (CLPP, GGPS1), and mtDNA maintenance/translation disorders (LARS2, TFAM). Tucker EJ; Rius R; Jaillard S; Bell K; Lamont PJ; Travessa A; Dupont J; Sampaio L; Dulon J; Vuillaumier-Barrot S; Whalen S; Isapof A; Stojkovic T; Quijano-Roy S; Robevska G; van den Bergen J; Hanna C; Simpson A; Ayers K; Thorburn DR; Christodoulou J; Touraine P; Sinclair AH Hum Genet; 2020 Oct; 139(10):1325-1343. PubMed ID: 32399598 [TBL] [Abstract][Full Text] [Related]
16. Expanding the genotypic spectrum of Perrault syndrome. Demain LA; Urquhart JE; O'Sullivan J; Williams SG; Bhaskar SS; Jenkinson EM; Lourenco CM; Heiberg A; Pearce SH; Shalev SA; Yue WW; Mackinnon S; Munro KJ; Newbury-Ecob R; Becker K; Kim MJ; O' Keefe RT; Newman WG Clin Genet; 2017 Feb; 91(2):302-312. PubMed ID: 26970254 [TBL] [Abstract][Full Text] [Related]
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18. An Application of NGS for Molecular Investigations in Perrault Syndrome: Study of 14 Families and Review of the Literature. Lerat J; Jonard L; Loundon N; Christin-Maitre S; Lacombe D; Goizet C; Rouzier C; Van Maldergem L; Gherbi S; Garabedian EN; Bonnefont JP; Touraine P; Mosnier I; Munnich A; Denoyelle F; Marlin S Hum Mutat; 2016 Dec; 37(12):1354-1362. PubMed ID: 27650058 [TBL] [Abstract][Full Text] [Related]
19. A novel mutation of Twinkle in Perrault syndrome: A not rare diagnosis? Gotta F; Lamp M; Geroldi A; Trevisan L; Origone P; Fugazza G; Fabbri S; Nesti C; Rubegni A; Morani F; Santorelli FM; Bellone E; Mandich P Ann Hum Genet; 2020 Sep; 84(5):417-422. PubMed ID: 32281099 [TBL] [Abstract][Full Text] [Related]
20. Broadening the phenotype of the TWNK gene associated Perrault syndrome. Fekete B; Pentelényi K; Rudas G; Gál A; Grosz Z; Illés A; Idris J; Csukly G; Domonkos A; Molnar MJ BMC Med Genet; 2019 Dec; 20(1):198. PubMed ID: 31852434 [TBL] [Abstract][Full Text] [Related] [Next] [New Search]