324 related articles for article (PubMed ID: 25801282)
1. Perinatal Gjb2 gene transfer rescues hearing in a mouse model of hereditary deafness.
Iizuka T; Kamiya K; Gotoh S; Sugitani Y; Suzuki M; Noda T; Minowa O; Ikeda K
Hum Mol Genet; 2015 Jul; 24(13):3651-61. PubMed ID: 25801282
[TBL] [Abstract][Full Text] [Related]
2. Virally expressed connexin26 restores gap junction function in the cochlea of conditional Gjb2 knockout mice.
Yu Q; Wang Y; Chang Q; Wang J; Gong S; Li H; Lin X
Gene Ther; 2014 Jan; 21(1):71-80. PubMed ID: 24225640
[TBL] [Abstract][Full Text] [Related]
3. BAAV mediated GJB2 gene transfer restores gap junction coupling in cochlear organotypic cultures from deaf Cx26Sox10Cre mice.
Crispino G; Di Pasquale G; Scimemi P; Rodriguez L; Galindo Ramirez F; De Siati RD; Santarelli RM; Arslan E; Bortolozzi M; Chiorini JA; Mammano F
PLoS One; 2011; 6(8):e23279. PubMed ID: 21876744
[TBL] [Abstract][Full Text] [Related]
4. A deafness mechanism of digenic Cx26 (GJB2) and Cx30 (GJB6) mutations: Reduction of endocochlear potential by impairment of heterogeneous gap junctional function in the cochlear lateral wall.
Mei L; Chen J; Zong L; Zhu Y; Liang C; Jones RO; Zhao HB
Neurobiol Dis; 2017 Dec; 108():195-203. PubMed ID: 28823936
[TBL] [Abstract][Full Text] [Related]
5. Deafness induced by Connexin 26 (GJB2) deficiency is not determined by endocochlear potential (EP) reduction but is associated with cochlear developmental disorders.
Chen J; Chen J; Zhu Y; Liang C; Zhao HB
Biochem Biophys Res Commun; 2014 May; 448(1):28-32. PubMed ID: 24732355
[TBL] [Abstract][Full Text] [Related]
6. The protective effects of systemic dexamethasone on sensory epithelial damage and hearing loss in targeted Cx26-null mice.
Xu K; Chen S; Xie L; Qiu Y; Liu XZ; Bai X; Jin Y; Wang XH; Sun Y
Cell Death Dis; 2022 Jun; 13(6):545. PubMed ID: 35688810
[TBL] [Abstract][Full Text] [Related]
7. Mice with conditional deletion of Cx26 exhibit no vestibular phenotype despite secondary loss of Cx30 in the vestibular end organs.
Lee MY; Takada T; Takada Y; Kappy MD; Beyer LA; Swiderski DL; Godin AL; Brewer S; King WM; Raphael Y
Hear Res; 2015 Oct; 328():102-12. PubMed ID: 26232528
[TBL] [Abstract][Full Text] [Related]
8. Assembly of the cochlear gap junction macromolecular complex requires connexin 26.
Kamiya K; Yum SW; Kurebayashi N; Muraki M; Ogawa K; Karasawa K; Miwa A; Guo X; Gotoh S; Sugitani Y; Yamanaka H; Ito-Kawashima S; Iizuka T; Sakurai T; Noda T; Minowa O; Ikeda K
J Clin Invest; 2014 Apr; 124(4):1598-607. PubMed ID: 24590285
[TBL] [Abstract][Full Text] [Related]
9. Timed conditional null of connexin26 in mice reveals temporary requirements of connexin26 in key cochlear developmental events before the onset of hearing.
Chang Q; Tang W; Kim Y; Lin X
Neurobiol Dis; 2015 Jan; 73():418-27. PubMed ID: 25251605
[TBL] [Abstract][Full Text] [Related]
10. The pathogenesis of common Gjb2 mutations associated with human hereditary deafness in mice.
Li Q; Cui C; Liao R; Yin X; Wang D; Cheng Y; Huang B; Wang L; Yan M; Zhou J; Zhao J; Tang W; Wang Y; Wang X; Lv J; Li J; Li H; Shu Y
Cell Mol Life Sci; 2023 May; 80(6):148. PubMed ID: 37178259
[TBL] [Abstract][Full Text] [Related]
11. Cell degeneration is not a primary causer for Connexin26 (GJB2) deficiency associated hearing loss.
Liang C; Zhu Y; Zong L; Lu GJ; Zhao HB
Neurosci Lett; 2012 Oct; 528(1):36-41. PubMed ID: 22975134
[TBL] [Abstract][Full Text] [Related]
12. Connexin 26 null mice exhibit spiral ganglion degeneration that can be blocked by BDNF gene therapy.
Takada Y; Beyer LA; Swiderski DL; O'Neal AL; Prieskorn DM; Shivatzki S; Avraham KB; Raphael Y
Hear Res; 2014 Mar; 309():124-35. PubMed ID: 24333301
[TBL] [Abstract][Full Text] [Related]
13. Restoration of connexin26 protein level in the cochlea completely rescues hearing in a mouse model of human connexin30-linked deafness.
Ahmad S; Tang W; Chang Q; Qu Y; Hibshman J; Li Y; Söhl G; Willecke K; Chen P; Lin X
Proc Natl Acad Sci U S A; 2007 Jan; 104(4):1337-41. PubMed ID: 17227867
[TBL] [Abstract][Full Text] [Related]
14. Digenic inheritance of non-syndromic deafness caused by mutations at the gap junction proteins Cx26 and Cx31.
Liu XZ; Yuan Y; Yan D; Ding EH; Ouyang XM; Fei Y; Tang W; Yuan H; Chang Q; Du LL; Zhang X; Wang G; Ahmad S; Kang DY; Lin X; Dai P
Hum Genet; 2009 Feb; 125(1):53-62. PubMed ID: 19050930
[TBL] [Abstract][Full Text] [Related]
15. The human deafness-associated connexin 30 T5M mutation causes mild hearing loss and reduces biochemical coupling among cochlear non-sensory cells in knock-in mice.
Schütz M; Scimemi P; Majumder P; De Siati RD; Crispino G; Rodriguez L; Bortolozzi M; Santarelli R; Seydel A; Sonntag S; Ingham N; Steel KP; Willecke K; Mammano F
Hum Mol Genet; 2010 Dec; 19(24):4759-73. PubMed ID: 20858605
[TBL] [Abstract][Full Text] [Related]
16. Connexins, hearing and deafness: clinical aspects of mutations in the connexin 26 gene.
Lefebvre PP; Van De Water TR
Brain Res Brain Res Rev; 2000 Apr; 32(1):159-62. PubMed ID: 10928803
[TBL] [Abstract][Full Text] [Related]
17. Modeling gap junction beta 2 gene-related deafness with human iPSC.
Fukunaga I; Oe Y; Danzaki K; Ohta S; Chen C; Shirai K; Kawano A; Ikeda K; Kamiya K
Hum Mol Genet; 2021 Jul; 30(15):1429-1442. PubMed ID: 33997905
[TBL] [Abstract][Full Text] [Related]
18. Connexin32 can restore hearing in connexin26 deficient mice.
Degen J; Schütz M; Dicke N; Strenzke N; Jokwitz M; Moser T; Willecke K
Eur J Cell Biol; 2011 Oct; 90(10):817-24. PubMed ID: 21813206
[TBL] [Abstract][Full Text] [Related]
19. Actin-independent trafficking of cochlear connexin 26 to non-lipid raft gap junction plaques.
Defourny J; Thelen N; Thiry M
Hear Res; 2019 Mar; 374():69-75. PubMed ID: 30732922
[TBL] [Abstract][Full Text] [Related]
20. Degradation of cochlear Connexin26 accelerate the development of age-related hearing loss.
Xu K; Chen S; Bai X; Xie L; Qiu Y; Liu XZ; Wang XH; Kong WJ; Sun Y
Aging Cell; 2023 Nov; 22(11):e13973. PubMed ID: 37681746
[TBL] [Abstract][Full Text] [Related]
[Next] [New Search]
