These tools will no longer be maintained as of December 31, 2024. Archived website can be found here. PubMed4Hh GitHub repository can be found here. Contact NLM Customer Service if you have questions.
3. Partial external biliary diversion in bile salt export pump deficiency: Association between outcome and mutation. Ellinger P; Stindt J; Dröge C; Sattler K; Stross C; Kluge S; Herebian D; Smits SHJ; Burdelski M; Schulz-Jürgensen S; Ballauff A; Schulte Am Esch J; Mayatepek E; Häussinger D; Kubitz R; Schmitt L World J Gastroenterol; 2017 Aug; 23(29):5295-5303. PubMed ID: 28839429 [TBL] [Abstract][Full Text] [Related]
4. ATP8B1 and ABCB11 analysis in 62 children with normal gamma-glutamyl transferase progressive familial intrahepatic cholestasis (PFIC): phenotypic differences between PFIC1 and PFIC2 and natural history. Davit-Spraul A; Fabre M; Branchereau S; Baussan C; Gonzales E; Stieger B; Bernard O; Jacquemin E Hepatology; 2010 May; 51(5):1645-55. PubMed ID: 20232290 [TBL] [Abstract][Full Text] [Related]
5. Targeted pharmacotherapy in progressive familial intrahepatic cholestasis type 2: Evidence for improvement of cholestasis with 4-phenylbutyrate. Gonzales E; Grosse B; Schuller B; Davit-Spraul A; Conti F; Guettier C; Cassio D; Jacquemin E Hepatology; 2015 Aug; 62(2):558-66. PubMed ID: 25716872 [TBL] [Abstract][Full Text] [Related]
6. Successful mutation-specific chaperone therapy with 4-phenylbutyrate in a child with progressive familial intrahepatic cholestasis type 2. Gonzales E; Grosse B; Cassio D; Davit-Spraul A; Fabre M; Jacquemin E J Hepatol; 2012 Sep; 57(3):695-8. PubMed ID: 22609309 [TBL] [Abstract][Full Text] [Related]
7. Hepatocanalicular bile salt export pump deficiency in patients with progressive familial intrahepatic cholestasis. Jansen PL; Strautnieks SS; Jacquemin E; Hadchouel M; Sokal EM; Hooiveld GJ; Koning JH; De Jager-Krikken A; Kuipers F; Stellaard F; Bijleveld CM; Gouw A; Van Goor H; Thompson RJ; Müller M Gastroenterology; 1999 Dec; 117(6):1370-9. PubMed ID: 10579978 [TBL] [Abstract][Full Text] [Related]
8. 4-phenylbutyrate enhances the cell surface expression and the transport capacity of wild-type and mutated bile salt export pumps. Hayashi H; Sugiyama Y Hepatology; 2007 Jun; 45(6):1506-16. PubMed ID: 17538928 [TBL] [Abstract][Full Text] [Related]
9. The mechanism of increased biliary lipid secretion in mice with genetic inactivation of bile salt export pump. Gooijert KE; Havinga R; Wolters H; Wang R; Ling V; Tazuma S; Verkade HJ Am J Physiol Gastrointest Liver Physiol; 2015 Mar; 308(5):G450-7. PubMed ID: 25552583 [TBL] [Abstract][Full Text] [Related]
10. A novel mutation within a transmembrane helix of the bile salt export pump (BSEP, ABCB11) with delayed development of cirrhosis. Stindt J; Ellinger P; Weissenberger K; Dröge C; Herebian D; Mayatepek E; Homey B; Braun S; Schulte am Esch J; Horacek M; Canbay A; Schmitt L; Häussinger D; Kubitz R Liver Int; 2013 Nov; 33(10):1527-35. PubMed ID: 23758865 [TBL] [Abstract][Full Text] [Related]
11. BSEP: function and role in progressive familial intrahepatic cholestasis. Thompson R; Strautnieks S Semin Liver Dis; 2001 Nov; 21(4):545-50. PubMed ID: 11745042 [TBL] [Abstract][Full Text] [Related]
12. Cross-Sectional Analysis of Progressive Familial Intrahepatic Cholestasis in Puerto Rican Children. Soler DM; Del Valle AI; Fernandez-Lube D; Shneider BL P R Health Sci J; 2016 Dec; 35(4):220-223. PubMed ID: 27898169 [TBL] [Abstract][Full Text] [Related]
13. De novo bile salt transporter antibodies as a possible cause of recurrent graft failure after liver transplantation: a novel mechanism of cholestasis. Keitel V; Burdelski M; Vojnisek Z; Schmitt L; Häussinger D; Kubitz R Hepatology; 2009 Aug; 50(2):510-7. PubMed ID: 19642168 [TBL] [Abstract][Full Text] [Related]
14. Relapsing features of bile salt export pump deficiency after liver transplantation in two patients with progressive familial intrahepatic cholestasis type 2. Maggiore G; Gonzales E; Sciveres M; Redon MJ; Grosse B; Stieger B; Davit-Spraul A; Fabre M; Jacquemin E J Hepatol; 2010 Nov; 53(5):981-6. PubMed ID: 20800306 [TBL] [Abstract][Full Text] [Related]
15. Combined mutations of canalicular transporter proteins cause severe intrahepatic cholestasis of pregnancy. Keitel V; Vogt C; Häussinger D; Kubitz R Gastroenterology; 2006 Aug; 131(2):624-9. PubMed ID: 16890614 [TBL] [Abstract][Full Text] [Related]
16. Geniposidic acid protected against ANIT-induced hepatotoxity and acute intrahepatic cholestasis, due to Fxr-mediated regulation of Bsep and Mrp2. Chen H; Huang X; Min J; Li W; Zhang R; Zhao W; Liu C; Yi L; Mi S; Wang N; Wang Q; Zhu C J Ethnopharmacol; 2016 Feb; 179():197-207. PubMed ID: 26723467 [TBL] [Abstract][Full Text] [Related]
17. Novel ATP8B1 mutation in an adult male with progressive familial intrahepatic cholestasis. Deng BC; Lv S; Cui W; Zhao R; Lu X; Wu J; Liu P World J Gastroenterol; 2012 Nov; 18(44):6504-9. PubMed ID: 23197899 [TBL] [Abstract][Full Text] [Related]
18. Hepatocellular carcinoma in ten children under five years of age with bile salt export pump deficiency. Knisely AS; Strautnieks SS; Meier Y; Stieger B; Byrne JA; Portmann BC; Bull LN; Pawlikowska L; Bilezikçi B; Ozçay F; László A; Tiszlavicz L; Moore L; Raftos J; Arnell H; Fischler B; Németh A; Papadogiannakis N; Cielecka-Kuszyk J; Jankowska I; Pawłowska J; Melín-Aldana H; Emerick KM; Whitington PF; Mieli-Vergani G; Thompson RJ Hepatology; 2006 Aug; 44(2):478-86. PubMed ID: 16871584 [TBL] [Abstract][Full Text] [Related]
19. Short-chain ubiquitination is associated with the degradation rate of a cell-surface-resident bile salt export pump (BSEP/ABCB11). Hayashi H; Sugiyama Y Mol Pharmacol; 2009 Jan; 75(1):143-50. PubMed ID: 18829893 [TBL] [Abstract][Full Text] [Related]