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2. Transgenic mice recapitulate the phenotypic heterogeneity of genetic prion diseases without developing prion infectivity: Role of intracellular PrP retention in neurotoxicity. Chiesa R; Restelli E; Comerio L; Del Gallo F; Imeri L Prion; 2016 Mar; 10(2):93-102. PubMed ID: 26864450 [TBL] [Abstract][Full Text] [Related]
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19. Recombinant human prion protein mutants huPrP D178N/M129 (FFI) and huPrP+9OR (fCJD) reveal proteinase K resistance. Gauczynski S; Krasemann S; Bodemer W; Weiss S J Cell Sci; 2002 Nov; 115(Pt 21):4025-36. PubMed ID: 12356908 [TBL] [Abstract][Full Text] [Related]
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